• Journal of The Korean Society of Inherited Metabolic disease
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• v.15 no.3
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• pp.118-126
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• 2015

Background and objectives: A deficiency of BH4 (tetrahydrobiopterin) not only causes the classical phenylketonuric phenotype, but also is the source of neurological signs and symptoms due to impaired syntheses of L-Dopa and serotonin. The treatment of BH4 deficiency usually consists of replacement with BH4 and the neurotransmitters. We performed this study to finding out long-term follow-up clinical symptoms and prognosis of BH4 deficiency. Methods: Clinical and biochemical, genetic analysis were done retrospectively from January 1999 to July 2015 in Soonchunhyang University Hospital. Results: In our study, total 207 patients were confirmed to hyperphenylalaninemia. Among them, 10 patients were BH4 deficiency. 9 patients were 6-pyruvoyl-tetrahydropterin (PTPS) deficiency and one patient was dihydropteridine reductase (DHPR) deficiency. The patients who received delayed treatment, most of our patients suffered from severe psychomotor retardation, hypotonia and seizure. c.259C>T mutation was identified most commonly in PTPS gene analysis. A patient with DHPR deficiency had a mental retardation, dystonia, seizure. His seizure semiology was dialeptic feature. His EEG showed generalized spike wave patterns. All patients had treated with tolerate L-Dopa, BH4 and 5-hydroxytryptophan. Most of the early treated patients have a good tolerance for drugs well. But some patients had neurologic symptoms, despite early detection and treatment. Conclusion: BH4 deficiency patients who had delayed treatment tend to have severe psychomotor problem and neurologic deficits.

• Journal of the Korean Society of Fisheries and Ocean Technology
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• v.53 no.4
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• pp.446-455
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• 2017

The improvement of resistance performance for the 4.99 ton class fishing boats was shown. The 4.99 ton fishing boats are the most commonly used one in the Korean coastal region. The evaluation of resistance performance was estimated by the Computational Fluid Dynamics (CFD) analysis. The CFD simulation was performed by the validation for various types of bow shapes on the hull. The optimized hull form from the simulation was selected and showed the best resistance performance. This hull type was tested on the towing tank in the National Institute of Fisheries Science (NIFS). The effective horsepower (EHP) was estimated by the resistance test on the towing tank with the bare hull condition. The drag force on the three service speed conditions was obtained for the resistance analysis to power prediction. The measured drag forces are compared with the results from the CFD simulation with one another. As results of the model tests, it was confirmed that the shape of the bow is an important factor in the resistance performance. The effective horsepower decreased about 30% in comparison with the conventional hull form. Also, the resistance performance improved the reduction of required horsepower, which especially contributed to the energy-saving for the fisheries industry. In the CFD analysis, the resistance performance improved slightly. In this case, the ratio of the residual resistance ($C_R$) in the total resistance ($C_T$) was high. Therefore, the CFD analysis was not enough to satisfy with reflection for the free surface and wave form in the CFD procedure. Both model test and CFD calculation in this study can be applied to the initial design process for the coastal fishing vessel.

• Journal of Korean Society of Coastal and Ocean Engineers
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• v.2 no.4
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• pp.208-222
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• 1990

The nonlinear hydrodynamic pressure force and moment on hinged wavemakers of variable-draft are presented. A closed-form solution (correct to second-order) for the nonlinear wavemaker boundary value problem has been obtained by employing the Stokes perturbation expansion scheme. The physical significance of the second-order contributions to the hydrodynamic pressure moment are examined in detail. Design curves are presented which demonstrate both the magnitude of the second-order nonlinearities and the effects of the variable-draft hinge height. The second-order contributions to the total hydrodynamic force and moment consist of a time-dependent and a steady part. The sum of the first and second-order pressure force and moment show a significant increase over those predicted by linear wavemaker theory. The second-order effects are shown to vary with both relative water depth and wave amplitude. The second-order dynamic effects are relatively more important for hinged wavemakers with shallower drafts.

• Journal of the Korean Society of Fisheries and Ocean Technology
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• v.33 no.4
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• pp.285-289
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• 1997

A Held experiment was carried out to confirm the effect of underwater sound on the luring of fish school of rudder fish in a set net at the coast of Cheju Island. The effects of the acoustic emission on the luring of fish school were observed at a cage around a set net fishing ground using a manufactured underwater speaker. Underwater sounds that were emitted for the luring of fish school were the pure sounds of which frequency were 300Hz and 400Hz, engine noise and swimming sound. The results of the observation are as follows : 1. The input and output wave forms of a manufactured underwater speaker in water tank were similar to those in measurement frequencies. The result of the observation indicated that it could be used for the purpose of the sound emission in measurement frequencies. 2. The effect of the emitted pure sound of 300Hz, 400Hz was remarkable for the luring of fish school in 2 minutes after the sound emission. The reaction of fish school was more sensitive to the pure sound of 400Hz than 300Hz. 3. The effect of the emitted engine noise was more remarkable than that of the pure sound for 3 minute continuously. On the feeding sound, fish formed a shoal and swimmed, but didn't gather around the underwater speaker. 4. The feeding and swimming sound spectra on rudder Hsh showed similar sound pressure distribution each other, they appeared low sound pressure in frequencies of 200-600Hz.

• Journal of the Korean Society of Clothing and Textiles
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• v.36 no.7
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• pp.714-726
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• 2012

The Korean wave 'Hallyu' has proliferated in China and the trend is remarkable especially in wedding photography. Korean style wedding photography has gained wide popularity among newly married Chinese couples because it is regarded as fresh and trendy. Accordingly, there is an urgent need to develop and supply dress designs for Chinese brides who want Korean style wedding photography. This study outlined the current status of Hallyu and wedding photography in China in order to analyze dresses for wedding photography. Chinese brides were analyzed to outline the features of preferred designs. The dresses preferred by Chinese brides for wedding photography included wedding dresses, evening dresses, and casuals (respectively), and partly featured traditional dresses. The preferred design elements for wedding dresses and evening dresses were ball gown silhouettes, strapless necklines, and gather detail. As for the casuals preferred by Chinese brides, the romantic style was most preferred and the skirts, dresses, T-shirts and blouse items were preferred for the romantic style. Through the analysis, dress designs for Chinese brides who want Korean style wedding photography were developed to reflect Hallyu content as well as 2012 S/S fashion trends for wedding dresses, evening dresses, and casuals. Currently Korean style wedding photography is gaining popularity in China and Hallyu content is considered a fresh and competitive item that may strongly appeal to Chinese consumers. This study focused on the development of designs for wedding photography dresses with Hallyu related content and is to be used as a reference for the development of Hallyu related wedding products as well as the proliferation of Hallyu.

• Journal of the Society of Naval Architects of Korea
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• v.33 no.3
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• pp.66-80
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• 1996

Recently, HT steel has been widely used in structure, and this enables to reduce the plate thickness. To use the HT steel effectively for a ship hull, the plate thickness becomes thin so that plate buckling may take place. Therefore, precise assessment of the behaviour of plat above primary buckling load is important. The plate under the load, that is called, secondary buckling load may undergo abrupt changes in wave form after primary buckling. This is very important when the collapse strength of the whole structures is considered. From this point of view, this paper discusses secondary buckling behaviour of thin plate under inplane compressive loading. A elastic large deflection analysis of plates with initial imperfection is performed assuming uniaxial compression, respectively, and the influence of secondary buckling is investigated. It is known that square plate is not influenced by non-symmetrical deflection coefficient but influenced by symmetrical deflection coefficient. Also, it has been found that rectangular plate($\alpha$=a/b) is influenced by all deflection coefficient, and the reduction of inplane stiffness of the plate after primary buckling is continued.

• Journal of the Society of Naval Architects of Korea
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• v.57 no.4
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• pp.213-220
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• 2020

In the present paper, implosion responses of two adjacent cylindrical tubes under external hydrostatic pressure were experimentally investigated. The cylinder models were fabricated of aluminium alloy 6061-T6 commercial tubes. In the experiment, a pair of two-cylinders were placed inside of a support frame in a medium-size pressure chamber, whose design pressure was 6.0MPa. The distance between the two-cylinders was 30 millimeter measured from outer shell at the mid-length. The implosion tests were performed with water and compressed nitrogen gas as the pressurizing media. The ambient static pressure of the chamber and local dynamic pressure near the two-imploded models were measured simultaneously. It was found that the energy released during an implosion from the first, weaker cylinder triggered the instability of the second, stronger cylinders. In other words, the resulting shock wave of the first implosive impact from the weaker cylinder could cause the premature failure of the neighboring stronger cylinders. The non-contact implosion phenomena from the two-cylindrical tube were clearly observed.

• Korean Journal of Human Ecology
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• v.16 no.5
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• pp.1051-1059
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• 2007

This study intends to find out possible variations in physical properties and color of hair depending on dye type(acidic and alkalic) and permanent treatment/hair dyeing procedure. To meet the goals, healthy hair samples were taken from 5 women's hair speciment in 20's without experiencing in any harmful substance via long-term medications. and beauty care using chemicals. To get possible findings depending upon hair dye type and treatment procedure, both acidic and alkalic hair dye were applied on some specimens after permanent treatment, while on other specimens before permanent treatment. In order to determine scale damage, this study used SEM(Hitachi S-2500C) both hair thickness and tensile strength were measured with optical microscope(Nikon, MM-60/L3T) and Instron (4482-standard). Wave configuration was measured transverse and longitudinal round diameter. The chromaticity of each specimen was measured using a spectrocolorimeter(Color Techno System, JP/JX-777) with visual $C/2^{\circ}$ (at $2^{\circ}$ with C light source) monitor fixed to determine Lab and CMYK values. As a result, it was found that hair specimens were more significantly damaged with alkalic hair dye treatment than with acidic hair dye treatment, while hair specimens were more effectively dyed with the former hair dye type than with the latter one. For possible results depending on treatment procedure, it was found that hair specimens were less damaged but more effectively dyed with permanent treatment followed by hair dyeing than vice versa. Therefore, it was concluded that permanent treatment followed by acidic hair dyeing would be more effective in reducing hair damages.

• The Journal of The Korea Institute of Intelligent Transport Systems
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• v.7 no.1
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• pp.1-9
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• 2008

According to the ubiquitous trend, the needs for the context based application service have been increased. These services take on Location Based Service which is based on the current location of users. It is widely used that localization techniques use GPS or ground wave and more efficient and accurate methods have been studied. Recently, not only services which targeted outdoor but also services which targeted indoor, for example home services and facility guidance of the building come into the spotlight. In case of the outdoor positioning area, COTH (Commercial Off-The-Shelf) has been released and used but relatively it doesn't produce an outcome in the indoor positioning area. Therefore, this paper Proposes the indoor positioning technique using wireless LAN (Local Area Network) which is one of the widely used wireless communication technique. It analyzes the typical WLAN location positioning methodology has been studied and their advantage and disadvantage also suggests how to design and implement the specific WLAN positioning system. In addition, it suggests new methods that progress the accuracy of the existing systems and improve the efficient computation.

• Journal of the Institute of Electronics Engineers of Korea SD
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• v.38 no.6
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• pp.383-389
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• 2001

We report on the design, fabrication, and characterization of 0.35${\mu}{\textrm}{m}$-gate AIGaAs/InGaAs PHEMTs for millimeter-wane applications. The epi-wafer structures were designed using ATLAS for optimum DC and AC characteristics, 0.351m-gate AIGaAs/rnGaAs PHEMTs having different gate widths and number of fingers were fabricated using electron beam lithography Dependence of RF characteristics of PHEMT on gate finger with and number of gate fingers have been investigated. PHEMT haying two 0.35$\times$60${\mu}{\textrm}{m}$$^2$ gate fingers showed the knee voltage, pinch-off voltage, drain saturation current density, and maximum transconductance of 1.2V, -1.5V, 275㎃/mm, and 260.17㎳/mm, respectively. The PHEMT showed fT(equation omitted)(current gain cut-off frequency) of 45㎓ and fmax(maximum oscillation frequency) of 100㎓. S$_{21}$ and MAG of the PHEMT were 3.6dB and 11.15dB, respectively, at 35㎓