• Maxillofacial Plastic and Reconstructive Surgery
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• 제30권6호
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• pp.572-576
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• 2008

Gorham-Stout 증후군은 조직학적으로 양성의 혈관 증식을 보이면서 광범위한 골 용해 현상을 나타내는 희귀한 병으로 알려져 있다. 병인론은 아직 명확히 밝혀져 있지 않으며 주로 남성과 젊은 성인에게서 호발하는 것으로 알려져 있다. 진단에는 컴퓨터 단층촬영, 자기공명영상, 핵의학검사, 혈관조영검사 등의 영상검사가 도움이 되며, 조직학적검사 역시 몇몇 특이 소견을 통해 진단에 도움을 줄 수 있다. 발생하는 부위에 따라서 그 예후는 매우 다르며, 특히 척추나 흉곽에 발생할 경우는 생명을 위협할 수 있다. 저자등은 우측 하악골의 병적 골절을 주소로 내원한 환자에서 임상검사, 방사선학적 검사, 조직병리학적 검사를 통해 Gorham-Stout 증후군으로 진단한 환자를 비골유리피판을 이용한 하악골 재건술을 통해 치료하였고 4년 동안 관찰 기간 중 재발 없이 양호한 치유 경과를 보였기에 문헌고찰과 함께 보고하는 바이다.

• 복식문화연구
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• 제23권3호
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• pp.512-522
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• 2015

The aim of this study was to investigate the change in women's somatotype with aging. The subjects were 1,123 women aged 40~69. Their anthropometric data were from the 6th Size Korea. The data were analyzed by factor analysis and cluster analysis. Seven factors were extracted: body mass, body length, back shoulder, arm length factor, front interscye factor, body rise factor, and shoulder angle. The upper body types of middle-aged and elderly women were classified into five types: skinny, short stout body type with forward posture, composite, tall & full body type, and short & skinny. The skinny and composite body type appeared more often than the short stout body type in the early 40s of Korean women. Starting in the mid-50s, composite body type was less often found. However, the number of women with short stout body type increased. In the 60s, the number of women with short stout and tall & full body types decreased. These results reveal that the body types of middle-aged and elderly women changed with some pattern with aging. And women in their early 40s, mid-50s, and 60s women had different body shapes and postures.

• Journal of Chest Surgery
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• 제52권1호
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• pp.44-46
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• 2019

Gorham-Stout disease (GSD) was first described by Gorham and colleagues in 1954, but its precise mechanism and cause remain to be elucidated. In this condition, voluminous and potentially fatal chylous effusions into the thorax can occur. Herein, we describe a case of GSD in which the patient presented with massive pleural effusions and mottled osteolytic bone lesions. We performed multiple operations, including thoracic duct ligation using video-assisted thoracoscopic surgery and thoracotomic decortication, but these procedures did not succeed in preventing recurrent pleural effusion and chest wall lymphedema. After administering sirolimus ($0.8mg/m^2$, twice a day) and propranolol (40 mg, twice a day), the process of GSD in this patient has been controlled for more than 2 years.

• 대한유전성대사질환학회지
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• 제17권1호
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• pp.24-30
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• 2017

Gorham-Stout disease (GSD)는 골용해와 함께 혈관 및 림프조직의 비정상적인 증식으로 골조직 파괴가 유발되는 매우 드문 질환이다. 아직까지 GSD의 정확한 병인 및 기전은 밝혀지지 않았다. 악성종양이나 신경병증, 감염과의 연관성은 불명확하며, 골조직이 있는 신체 어디에서든 기형적 혈관-림프관 증식이 발생할 수 있다. GSD 중 약 20%에서 유미흉을 동반하는데, 림프관 형성이상이나 가슴 림프관 손상에 의해 이차적으로 발생한다. 급격한 호흡부전으로 이어질 수 있어 불량한 예후인자로 알려져 있지만, 질환 자체의 희귀성 때문에 현재까지 확립된 표준치료법은 없다. 본 증례는 유미흉을 동반한 생명을 위협하는 GSD 환자에서 적극적인 외과적 중재술 후 mTOR inhibitor 및 beat-blocker 복합요법을 적용하여 치료에 성공한 보고이다. 환자는 가슴림프관 결찰술 및 흉막유착술을 시행 받았으나, 일시적 증상호전 이후로 유미흉 및 호흡곤란의 재악화 반복되었다. 양측 흉막유착제거 및 폐쇄 흉강삽관술과 함께, beta-blocker와 mTOR inbititor 경구투약을 시작했다. 약물투약 1개월 후 유미흉 재발없이 호흡 안정적으로 유지되어 산소 보조치료 없이 퇴원하였다. 현재 11개월째 지속적으로 약물 투약 중으로, 약물 부작용 및 추가적인 입원치료 없이 정상적인 일상생활을 유지하고 있다. 추후 유미흉을 동반한 GSD 환자의 치료에서, 적극적인 외과적 중재술과 함께 경구 mTOR inhibitor 및 beta-blocker 복합요법을 고려해 볼 수 있겠다.

• 한국의류학회지
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• 제33권2호
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• pp.230-243
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• 2009

The purpose of this study was to analyse the body sizes of $7{\sim}12$ years elementary school girls and also to categorize KS size dimensions by the detailed information of ages and body shapes. For the study, the data of SizeKorea(2004) was analysed. Height, bust, waist, hip, the ratio of waist to height and hip to height were significant between age groups, but the ratio of bust to height was not. Therefore, the increase of bust size was resulted in growth of bust circumference, instead of bust volume. In the same height group, over 11 year girls had smaller waist, while over 12 year girls had bigger hip. For Grouping girls by ages and body shapes, the ages were divided into 2 groups, under 10 years old and 11 to 12 years old. The body shapes classified into 3 groups 'Stout-shape', 'Middle-shape', and 'slim-shape', by the ratios of bust to height and hip to height. 'Stout-shape' was significantly big at the almost sizes, but 'Middle-shape' was significantly big at only circumferences, not lengths. In addition, drop(the difference between bust and hip) and lower-drop(the difference between waist and hip) were in inverse proportion to the ratios of bust to height and hip to height. It meant the increases of bust-ratio and hip-ratio of 'Stout-shape' were resulted in overweight, rather than female matureness. The distribution of sizes over 0.5% were grouped for grading system and the subtotal percentiles of each group were calculated for industrial data. The groups which covered more than 10% of consumers were 2 to 6 and the 1 or 2 groups for 'Stout-shape' were also observed, so that children's ready-to wear companies could use them efficiently for their own consumer target.

• 한국의류학회지
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• 제35권12호
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• pp.1454-1465
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• 2011

Menswear body types are often labeled on garments (to indicate how the garments are designed to fit) with indicators of a size category such as regular, portly, and stout, athletic, or big and tall. A drop (relationships between the chest and waist girths) is related to the fit of a tailored suit. However, current standards are not designed for various drops or body types. There is not enough information of categorizing men's body shapes for the apparel sizing systems. In this article, a set of men's data from SizeUSA sizing survey was analyzed to investigate men's body shapes and drops. Factor analysis and a cluster analysis method were used to categorize men's body shapes. In the results, twenty-five variables were selected through the factor analysis and found four factors: girth factor, height factor, torso girth factor, and slope degree factor. According to the factor and cluster analysis, various body shapes were found: Slim Shape (SS - tall ectomorphy), Heavy Shape (HS - athletic, big & tall, endomorphy and mesomorphy), Slant Inverted Triangle Shape (SITS - regular, slight ectomorphy and slight mesomorphy weight range from normal to slightly overweight), Short Round Top Shape (SRTS - portly and stout, endomorphy). Body shapes were related to fitting categories. SS and HS were related to big & tall fitting category. SITS was related to regular. SRTS was related to portly and stout. Shape 1 (31%) and Shape 2 (26%) were related to current big & tall category. Shape 3 (34%) were related to regular. Shape 4 (9%) were in portly and stout category. ASTM D 6240 standard was the only available standard that presented a regular fitting category. Various drops were found within a same chest size group; however, this study revealed great variances of drops by body shape.

• Journal of Chest Surgery
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• 제48권1호
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• pp.90-94
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• 2015

Gorham-Stout Syndrome (GSS) is a rare disease characterized by localized bone resorption. Any part of the skeleton may be affected; therefore, symptoms can vary depending on the site involved. Pathological analysis reveals lymphovascular proliferation and osteolysis in the affected lesion, but the etiology of the disease is poorly understood. When GSS occurs in the chest, chylothorax or respiratory failure may occur. Thus far, a standard treatment for GSS has not been established, and the prognosis remains unknown. The following case report describes a successfully treated case of GSS in a 16-year-old boy with an affected sternum and ribs.

• 대한영상의학회지
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• 제85권2호
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• pp.451-455
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• 2024

특이 외상력 없이 우측 1, 2번 갈비뼈 골용해와 자발성 유미흉을 주소로 내원한 45세 남환이 임상 양상과 골생검을 통해 고함-스타우트병으로 확진된 증례를 보고하고자 한다. 자발성 유미흉의 치료를 위해 림프관 색전술을 시행하였고 성공적인 시술 직후 유미흉은 호전되었다. 하지만 15개월간의 관찰 동안 시롤리무스(sirolimus) 투여에도 불구하고 유미흉이 재발되었고 흉부 불편감과 골용해는 진행되었다.

• 한국추진공학회:학술대회논문집
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• 한국추진공학회 2006년도 제27회 추계학술대회논문집
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• pp.113-115
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• 2006

Stout & Snell[1]이 수행했던 설계 과정을 기초로 하여 우주발사체 추진제 가압시스템 설계에 대한 기본적인 내용을 정리한다. 발사체 설계 초기 결정되어야 하는 가압시스템 요구 조건과 전반적인 시스템에 대한 물리적인 모델에 대한 내용을 소개하고, 온/오프 솔레노이드 밸브를 이용하는 가압 제어 시스템 설계에 대한 기본적인 내용 간략히 정리한다.

• Journal of Species Research
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• 제9권4호
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• pp.467-472
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• 2020

The crinoid specimens of the genus Anneissia were collected from Nokdong, Korea Strait, and Moseulpo, Jeju Island. The specimens were identified as Anneissia pinguis (A.H. Clark, 1909), which belongs to the family Comatulidae of the order Comatulida. Anneissia pinguis was first described by A.H. Clark in 1909 around southern Japan. This species can be distinguished from other Anneissia species by a longish and stout cirrus, much fewer arms, and short distal cirrus segments. The morphological features of Korean specimens are as follows: large disk (20-35 mm), 28-36 segments and 32-43 mm length cirrus, division series in all 4 (3+4), very stout and strong distal pinnule with 18-19 comb and 40 arms. In Korea fauna, only three species of genus Anneissia were recorded: A. intermedia, A. japonica, and A. solaster. In this study, we provide the morphological description and phylogenetic analysis based on cytochrome c oxidase subunit I.