Journal of the Korean Society of Radiology (대한영상의학회지)

The Korean Society of Radiology (대한영상의학회)
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Role of Lymphatic Embolization in Chylothorax Associated with Gorham-Stout Disease: A Case Report

고함-스타우트병과 연관된 유미흉 치료에서 림프관 색전술의 역할: 증례 보고

  • Min-Hyuk Yu (Department of Radiology, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Dongho Hyun (Department of Radiology, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Sun-Hye Shin (Division of Pulmonary and Critical Care Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Sang-Yun Ha (Department of Pathology, Samsung Medical Center, Sungkyunkwan University School of Medicine)
  • 유민혁 (성균관대학교 의과대학 삼성서울병원 영상의학과) ;
  • 현동호 (성균관대학교 의과대학 삼성서울병원 영상의학과) ;
  • 신선혜 (성균관대학교 의과대학 삼성서울병원 호흡기내과) ;
  • 하상윤 (성균관대학교 의과대학 삼성서울병원 병리과)
  • Received : 2023.04.24
  • Accepted : 2023.08.18
  • Published : 2024.03.01
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Abstract

A 45-year-old male patient with spontaneous chylothorax and osteolysis in the right 1st and 2nd ribs was diagnosed with Gorham-Stout disease based on clinical manifestations and bone biopsy. The chylothorax temporarily decreased after a successful selective lymphatic embolization. The patient presented with recurrent chylothorax, mild chest discomfort, and progressive osteolysis (despite administering sirolimus) during the follow-up period of 15 months.

특이 외상력 없이 우측 1, 2번 갈비뼈 골용해와 자발성 유미흉을 주소로 내원한 45세 남환이 임상 양상과 골생검을 통해 고함-스타우트병으로 확진된 증례를 보고하고자 한다. 자발성 유미흉의 치료를 위해 림프관 색전술을 시행하였고 성공적인 시술 직후 유미흉은 호전되었다. 하지만 15개월간의 관찰 동안 시롤리무스(sirolimus) 투여에도 불구하고 유미흉이 재발되었고 흉부 불편감과 골용해는 진행되었다.

Keywords

References

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