• Journal of The Korean Society of Inherited Metabolic disease
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• v.16 no.2
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• pp.109-114
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• 2016

Carbamoyl phosphate synthetase 1 (CPS1) deficiency is an autosomal recessive urea cycle disorder which causes hyperammonemia. CPS1 is the first enzyme step in the urea cycle and almost patients present their symptoms during neonatal period. We report a case of CPS1 deficiency in a boy who developed symptoms including lethargy and seizure at 3 days of age. The ammonia level was up to $2,325{\mu}mol/L$, sodium benzoate (250 mg/kg/d) and high calories of both dextrose and lipid was promptly administered. Central access by experienced pediatric surgeon and emergent continuous hemodialysis by pediatric nephrologist was performed within 3 hours and ammonia was less than $100{\mu}mol/L$ at 5 days of age. Currently, he has showed excellent response to treatments including scavenging drugs and a low-protein diet. Despite of diffuse increasing signal intensity on cerebral white matters and basal ganglia on brain MRI, his development and weight gain were good at the last follow-up at 11 months of age. Molecular assay of the CPS1 gene demonstrated that patient had compound heterozygous for c.1529del ($p.Gly510Alafs^*5$) in exon 14 and c.3142-1G>C (IVS25(-1)G>C) in intron 25 and exon 26 boundary. The splicing mutation was novel mutation and inherited from patient's mother. Here, we report a neonatal lethal type CPS1 deficiency patient having novel mutation.

• 전기의세계
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• v.29 no.7
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• pp.455-459
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• 1980

The gain change of the photomultiplier which occurs as the count rate increased was examined. and simple feedback resistor series was introduced between 7th and 9th dynode for compensating the gain change. The effect of the feedback resistor series was considerably good to reduce the gain change. With the feedback resistor, the gain change was only 1.9%, when count rate was increased from 514 CPS (counts per second) to 1250 CPS. Without the feedback resister, the gain change was 6.9%, when the count rate was increased from 530 CPS to 1250 CPS.

• Journal of the Korean Data and Information Science Society
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• v.17 no.3
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• pp.851-859
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• 2006

The family income distributions of NLSY97 and CPS youth data are compared by using the generalized beta distribution of the second kind. The null hypothesis that the two data sets represent the same underlying population is rejected. The ML estimation suggests that NLSY97 data are oversampled in an income group of $11,308 or less, by about 15.7% compared to CPS data.

• Review of KIISC
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• v.29 no.2
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• pp.16-22
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• 2019

ICT 기술을 이용하여 업무 공정의 효율성을 높이기 위한 사이버물리시스템(CPS)은 구성요소 간 연결성 강화로 인한 사이버 공격 요인이 증가하고 있으며, 이에 따른 보안대책 수립이 CPS 구축 단계에서부터 고려되어야 한다. 본 논문에서는 CPS를 위한 보안대책의 온전한 수립을 위한 국제표준 동향을 ITU-T SG17의 표준화 활동을 중심을 살펴보고자 한다. ITU-T SG17에서 진행되고 있는 IoT 보안 표준, 스마트그리드 보안 표준, ITS 보안 표준 등 CPS 관련 보안 표준화 동향을 기술하고, 향후 표준화 추진 방향에 대해서도 다룬다.

• Proceedings of the Korea Information Processing Society Conference
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• 2009.11a
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• pp.185-186
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• 2009

오늘날 분산 컴퓨팅 환경은 유비쿼터스 컴퓨팅 기술을 요구하고 있다. 미국의 경우 최근 몇 년간 CPS에 대한 개념을 도입하여 차세대 임베디드 산업에 대한 새로운 패러다임을 제시하였고, 유비쿼터스 기술은 CPS 기술의 형태로 변화되기 시작하였다. 여기에 더해 실시간의 컴퓨팅 관리와 사용을 위해 자율 컴퓨팅 기술이 필요하며 기존과 달리 CPS 형 자율 컴퓨팅이 요구되고 있다. 본 논문은 기존의 분산 컴퓨팅과 CPS 컴퓨팅에서의 자율 컴퓨팅 요구를 소개하였다. 따라서 CPS 환경을 위해 주목해야 할 요소 기술들을 정리하였다.

• Journal of The Korean Society of Inherited Metabolic disease
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• v.18 no.1
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• pp.23-29
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• 2018

Carbamoyl phosphate synthetase 1 deficiency (CPS1D) is a rare autosomal recessive urea cycle disorder characterized by hyperammonemia. CPS1D is caused by mutations in the CPS1 gene on chromosome 2q35. Based on the age of onset, there are two phenotypes: the neonatal type and the delayed-onset type. The severity of clinical manifestation depends on the degree of CPS1 residual enzymatic activity, and can result in hyperammonemia and neurological dysfunction. We report a case of CPS1D in a neonate who developed vomiting, decreased consciousness and hyperammonemia at 25th day after birth. She showed excellent response to treatment including hydration, ammonia-lowering drugs and a low-protein diet without hemodialysis. Her growth, development and neurological outcomes were fair at the last follow-up at 17 months of age.

• Journal of IKEEE
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• v.12 no.3
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• pp.144-150
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• 2008

This paper describes the design of a coplanar-stripline(CPS) antenna without via hole in microstrip patch type for 910MHz RFID tags using the HFSS simulator. In order to obtain the simplified fabrication design of the antenna, we have used only an impedance matching network to match the impedance of a RFID-tag chip to that of the antenna, not using bandpass filter(BPF). In advance of the optimized antenna design, we have obtained and shown a good agreement compared with the published antenna for 5.8GHz in order to verify the simulation parameters in the HFSS. Based on the verified simulation parameters in the HFSS, we have designed and optimized the 910MHz-CPS-type microstrip patch antenna. The designed simulation results of the antenna show that the proposed antenna is very proper for RFID tags with the 910MHz center frequency without via hole in the microstrip patch antenna.

• The Journal of Korean Institute of Electromagnetic Engineering and Science
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• v.20 no.2
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• pp.208-214
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• 2009

A design and its experimental result of a wideband self-complementary spiral antenna for UWB USPR(Ultrashort-Pulse Radar) system applications is presented. By utilizing the planar-type ultra-wideband microstrip-to-CPS balun, ultra-wideband characteristics of the inherent spiral antenna are retrieved. Also, the design procedure of the spiral antenna is simplified by performing simple impedance matching between separately designed balun and antenna. The proposed spiral antenna is equiangular self-complementary spiral antenna. The implemented antenna demonstrates widebaad performance for frequency ranges from 2.9 to 12 GHz with the relatively flat antenna gain of 2.7 to 5.3 dB and broad beamwidth of more than $70^{\circ}$. From these result, the possibility of a spiral antenna using a ultra-wideband microstrip-CPS balun is verified.

• Journal of Korean Elementary Science Education
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• v.25 no.1
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• pp.27-38
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• 2006

The purpose of this study was to develop a test of a creative problem solving (CPS) for the selection of gifted science students in elementary school. For this, the methods and procedures of the selection of gifted science students was investigated through the internet homepages 23 gifted science education centers of universities and 16 city. province offices of education. The results of this study were as follows: Most of the gifted science students were selected through a multi-step examination process. They were selected on the basis of their records by recommendation of a principal or a classroom teacher in their school, by operation of standardized tests (ex. intelligence quotient score, achievements in science and mathematics, interest and attitude/aptitude for science as well as through other means), as well as through intensive observation of those gifted science students who are selected by interview and oral tests. The selection of gifted students was not evaluated through creativity testing; giftedness in city. province office of education. Testing of CPS was found to be especially lacking in these organizations. For the development of the test items of CPS in science, the five elements were extracted through the framework for the content analysis of the CPS: problem exploration, problem statement, solution thinking, experiment design, and assesment. In addition, suggestions were made regarding an appropriate scoring system for the test of the CPS. As the result of the developed test was applied to the 4th grade of the gifted and general student, we found that gifted students were superior to general students. In conclusion, it was that the CPS test developed in this study should be used to evaluate the CPS for the selection of gifted students.

• Journal of Veterinary Clinics
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• v.15 no.2
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• pp.370-377
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• 1998

본 연구는 황색포도상구균의 병원성 인자인 alpha-toxin, casular polysaccharides (CPS)와 fibronectin-binding protein (FnBP)을 이용해 실험동물인 토끼에서의 항체가 형성 능과 공격접종 후 방어능에 관한 연구를 위하여 수행되었으며 향후 젖소 유방염 아단위 항원 을 이용한 백신개발 가능성을 탐색하고자 수행되어졌다. 황색포도상구균의 alpha-toxin, capsu18r polysaccharides (CPS)91 fibronectin-binding protein (FnBP) 항원을 이통재 효소면 역측정법을 통한 혈중 IgG 항체가수준을 측정하였으며 alpha-toxin, capsular polysaccharides (CPS)와 fibronectin-binding protein (FnBP)으로 면역시킨 토끼에서 대조군의 토끼보다 혈 중 항체가 수준이 1차 면역 이후 유의성 있게 높았다 (p<0.05). 백신에 사용된 alpha-toxin, capsular polysaccharides (CPS)와 fibronectin-binding protein (FnBP) 항원중 capsular polysaccharides (CPS)가 다른 alpha toxin과 fibronectin-binding protein (FnBP)의 혈중항 체가 수준과 비교하여 볼 때 비교적 낮은 수준이었다. 세균을 혈중으로 공격접종한 후 대조군 과 백신접종군의 혈중내 세균제거율에 있어 대조군에 비해 백신접종군에서 유의성 있게 낮은 균수를 보였다 (p<0.05). 또한 장기내 균수측정실험결과 대조군의 장기보다 백신접종군에서 유의성 있게 세균수가 낮게 출현하였다 (p<0.05). 결론적으로 본 연구결과 황색포도상구균의 3가지 항훤 alpha-toxin, capsular polysaccharide와 재조합 fibronectin binding protein을 이 퐁한 실험동물에서 안단위 유방염 백신은 방어능이 있다고 생각된다.