• Journal of the korean academy of Pediatric Dentistry
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• v.45 no.1
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• pp.115-122
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• 2018

Noonan syndrome is characterized by distinctive facial features, short stature, and congenital heart disease. It is a congenital genetic disorder with a prevalence of between 1/1,000 and 1/2,500 in both genders. An 11-year-old boy with Noonan syndrome visited the hospital with an ectopically positioned tooth. A pulmonary stenosis was diagnosed and his growth and development were delayed. In many cases of this diseases there is obvious hemostasis, which he was not experiencing. His facial appearance showed characteristic features of Noonan syndrome. The patient showed a dental class II relationship, labioversion of the upper anterior teeth, and a shallow overbite. Radiographic examination revealed that the upper right canine was ectopically positioned, which led to root resorption of the upper right lateral incisor. A lateral cephalometric radiograph revealed a craniofacial pattern that was within normal limits. Surgical opening and button attachment on the impacted upper right canine were performed and traction was applied on the impacted tooth using a removable appliance. This patient was mildly affected by Noonan syndrome and showed some dental problems. However, few studies have reported the oral characteristics of Noonan syndrome despite its high incidence. Thus, this case report describes the oral features and management of Noonan syndrome.

• Journal of the korean academy of Pediatric Dentistry
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• v.26 no.2
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• pp.248-261
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• 1999

In order to define a current set of Korean children norm with mixed dentition, following study was done. The subjects were 102 healthy dentition contestants(48boys, 54girls). Standardized lateral head roentgenograms were taken, and Ricketts analysis was done. Results were as follows: 1. Length of anterior cranial base, posterior facial height, corpus length were longer in male than in female(p<0.05), and Porion was located posteriorly in male than in female(p<0.01). 2. Through facial depth, Pogonion of male was more forwardly positioned(p<0.05), mandible was significantly steeper in female, and maxillary anterior teeth were significantly tipped forward in male(p<0.05). 3. Variables such as length of anterior cranial base, upper molar position(p<0.01) and corpus length(p<0.05) were significantly changed by age. 4. Maxillary height, facial depth, mandibular plane angle, convexity were changed by age, but not significantly(p>0.05).

• Journal of the korean academy of Pediatric Dentistry
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• v.42 no.1
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• pp.75-79
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• 2015

Pulmonary arterial hypertension (PAH) is a common complication of Congenital heart defects (CHD) with left-to-right shunts, and PAH with increased pulmonary vascular resistance (PVR) is associated with considerable morbidity and mortality. General anesthesia (GA) can be life-threatening in patients with PAH, because the positive pressure ventilation during GA increases pulmonary arterial pressure and decreases pulmonary blood flow. This may also lead to hypoxia. Therefore, spontaneous ventilation may be safer than positive pressure ventilation in patients with PAH. A five-year-old male child, weighing 11 kg, with medical history showing a total correction of Tetralogy of Fallot (TOF) in 2009 and ongoing treatment with hypertension (HTN) medicine since 2007, visited the Dankook University Dental Hospital. He had multiple dental caries, and the treatment was completed under sevoflurane insufflation sedation via nasal cannula. The patient remained sedated throughout the operation while maintaining normal vital signs and spontaneous respiration. In conclusion, sevoflurane insufflation sedation may be a safer alternative to GA for the dental treatment of patients with PAH.

• Journal of the korean academy of Pediatric Dentistry
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• v.39 no.3
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• pp.306-313
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• 2012

Class III malocclusion or anterior crossbite is commonly seen in Asian. This problem is easily recognized by dentists and parents. During the primary dentition period, anterior crossbite with functional shift and deep overbite could develop to skeletal protrusive mandible. So, early and proper diagnosis of anterior crossbite which needs prompt treatment is important. These cases showed the early management of crossbite with functional shift in primary dentition using intraoral removable appliance resulting in improvement of intermaxillary relationship. And I analyzed the positional change and the dimensional change during treatment with lateral cephalometric x-ray analysis. Our patients showed vertical dimensional change of lower anterior facial height and clockwise rotation which results crossbite correction in 1 year of treatment period.

• Journal of Oral Medicine and Pain
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• v.35 no.1
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• pp.1-18
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• 2010

I'd like to introduce a teaching method to improve learning efficiency. Most students are likely to ignore what they don't understand in the class of a course. The subject of Occlusion is essential to understanding prosthodontic and orthodontic subjects. It is necessary to let students know and review what they don't understand among parts of a chapter in the course of Occlusion. Therefore I look over the examination papers after every examination and input the problems that each student didn't solve into the C-language computer program and print the list of the contents that each student must study particularly. I give the lists to students and let them review and present their own weak parts of a chapter in the course of Occlusion in the next class. This teaching method leads to improvement in learning and is helpful to students as well as lecturers.

• Journal of the korean academy of Pediatric Dentistry
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• v.28 no.1
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• pp.180-184
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• 2001

Cleidocranial Dysplasia(CCD) is an autosomal dominant human bone disease characterized by abnormal clavicles, patent sutures and fontanelles, and dental anomalies. Among dental anomalies, it is characterized that permanent dentition is severly disturbed due to multiple supernumerary teeth and abnormalities of tooth morphology. A eight-year-old female patient diagnosed as cleidocranial dysplasia visited in our hospital. Upon clinical oral exam, retained deciduous teeth, constriction of dental arch, anterior cross bite, and multiple dental caries were observed. In the dental panoramic radiograph, retained deciduous teeth and multiple supernumerary teeth in the maxilla and the mandible were found. In the cephalometric radiograph, open sutures and wormian bones were seen. In the chest P-A view absence of clavicles was observed. The cleidocranial dysplasia patients have eruption problems in permanent dentition both in regions with and without supernumerary teeth. The severely delayed or arrested eruption of permanent teeth has been ascribed to various factors : 1) The presence of multiple supernumerary teeth, 2) malformed roots with lack of cellular cementum, 3) the jaw bone being too dense, and 4) abnormal resorption of bone and primary teeth. Formation and maturation of primary teeth in cleidocranial dysplasia are normal, whereas the permanent dentition has various anomalies. Therefore, dentists should understand the development of dentition in cleidocranial dysplasia, and treat them in proper time.

• Journal of the korean academy of Pediatric Dentistry
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• v.35 no.3
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• pp.532-538
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• 2008

Lesch-Nyhan syndrome is a rare X-linked recessively inherited disorder, caused by complete absence or decrease in activity of hypoxanthine guanine phosphoribosyl transferase(HPRT), an enzyme involved in purine metabolism. This enzyme deficiency gives rise to nephropathy symptoms, such as hyperuricosuria and hyperuricemia by excessive uric acid production and neuropathy symptoms, such as mental retardation, choreoathetosis and self mutilation behavior. Patients with Lesch-Nyhan syndrome have tendency to bite their lip, tongue and finger. In severe cases, partial or even total amputation of tongue or finger occur. Self-inflicted bites are often complicated by secondary infection to the injured site as well as pain. Furthermore tissue loss by biting results in esthetic problems. The dental management of self mutilation includes treatment with appliances such as soft mouth guard or lip bumper, extraction of all the teeth, and orthognathic surgery. We report a case of a 13 year-old boy with Lesch-Nyhan syndrome, who severely injured himself on his tongue. At first, conservative treatment using soft mouth guard was considered, but it could not prevent trauma on his tongue. Therefore, extraction of the lower anterior and posterior teeth was carried out.

• Journal of the korean academy of Pediatric Dentistry
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• v.47 no.4
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• pp.377-388
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• 2020

The aim of this study was to evaluate the association between various predicting tools and Apnea-Hypopnea Index (AHI) to identify children with sleep disordered breathing (SDB). From 5 to 10 years old who came for orthodontic counseling, 61 children, whom had lateral cephalograms, pediatric sleep questionnaire (PSQ) records, and portable sleep monitoring results, were included in this study. A total of 17 measurements (11 distances and 6 angles) were made on lateral cephalograms. The measurements of lateral cephalograms, PSQ scales and portable sleep monitoring results were statistically analyzed. 49 of 61 (80%) patients showed AHI > 1, which suspected to have SDB and their mean AHI was 2.75. In this study, adenoid size (A/N ratio), position of the hyoid bone from mandibular plane, gonial angle, and PSQ scale were related to a higher risk of pediatric SDB. Also, oxygen desaturation index (ODI) and snoring time from sleep monitoring results were statistically significant in children with SDB using Mann-Whitney test (p < 0.05). In conclusion, evaluation of hyoid bone position, adenoidal hypertrophy, gonial angle in lateral cephalogram, and PSQ scale was important to screen out potential SDB, especially in children with frequent snoring.

• Journal of Technologic Dentistry
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• v.29 no.2
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• pp.197-211
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• 2007

With the development of orthodontics and increasing concerns on physical appearance, the number of patients has been steadily increasing. It is quite important not only to make effective cure plans and accurate diagnoses but also to have a thorough grasp of patients' malocclusion types and their occurrence frequency, in addition to patients' personality in order to cure the patients appropriately. This study is based on 946 malocclusion patients who had visited Chong-A Dental Hospital from 1999 to 2004 and investigated their aspects of malocclusion and characteristics of their gender, age and residence. The results are as follows. 1. The number of patients per year had been decreased until 2001, after which year the number had fluctuated. The number was the largest in 1999, 169 and the smallest in 2001, 140. Female occupied 68.0% of the total, twice as many as male, 32.0%) 2. Based on the Angle's classification, 19 or over year - old group was the largest of the total, 59.3% and 6 or younger year - old group, the smallest, 0.5%. The 19 or over year old group was less than a half of the total (47.4%) in 2003 and there were no patients who belonged to the 6 or younger year - old group in 2003 and 2004. 3. Distributions on the types of malocclusion have shown that 39.9 % of the total are in the Class I, the largest, 31.0% in the Class I and 29.2 in the Class II, the smallest. 1) The number of the ClassI was 73, the largest, that of the Class III being 35, the smallest in 1999. On the whole, the number of the Class I accounted for the largest part of the total. 2) The number of male patients in the Class II was the smallest, generally being the largest in the Class I. In case of female, that of the Class III was the smallest. 3) Based on the age, the Class I was the highest in between 7 and 13 age group, the Class III the lowest. The Class I occupied the largest around 40%. 4) In the shape of physiognomy, the meso occupied the largest part among all the Class, of which the Class II was the highest, 64.2%. The bracy was the largest in the Class I, and the dolicho in the Class III. 5) In the profile, the convex shape was the largest in the Class I and II, and especially in the Class II, over 3/4 of the total, 75.4%. In contrast, the direct shape was the largest in the Class III and the sunken shape occupied 33.3%, which was nearly ten times more than the case of the Class I and III. 6) In the asymmetry of physiognomy, the number of patients of the Class IIIwas the largest, 34.1% and that of the Class II, the smallest, 19.5%. It was found that about one fourth of the malocclusion patients were under the asymmetry of physiognomy. 4. In the distribution of patients' residence, 81.4% were from the Seoul Metropolis and 48.2% from Gangnam-Gu where Chong-A Dental Hospital is located and Seocho-Gu and Songpa-Gu which are adjacent to Gangnam-Gu.

• Journal of the korean academy of Pediatric Dentistry
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• v.36 no.4
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• pp.580-585
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• 2009

Pediatric dentists often meet children with abnormal in number of tooth. Presence of supernumerary teeth is frequent cause of malocclusion. Etiology for supernumerary teeth is not yet clearly defined, but it is thought to be caused by excessive proliferation of dental lamina by hereditary and environmental factors. Supernumerary teeth occur in the maxilla nine times more frequently than in the mandible. Most common supernumerary tooth is the mesiodens in the maxilla, and some are observed in the maxillary molar and mandibular premolar. It occurs rarely in the mandibular incisor region with the incidence of 1-2% among all supernumerary teeth. A six-year old boy visited the department of the pediatric dentistry, Yonsei University Dental Hospital, with the chief complaint of crowded supernumerary teeth on the mandibular incisor region. Clinical and radiographic examinations revealed six permanent mandibular incisors similar in size, shape, and length. Further investigation using computed tomography(CT) was proceeded on the mandible to measure and compare morphologic features and positions of the six incisors. Then, we decided to remove two incisors which were already erupted. Periodic check-up was followed to monitor the dental development and spontaneous positional enhancement of the remaining four incisors in the mandible.