• 제목/요약/키워드: 선천적

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수막뇌류(髓膜腦瘤)를 수반(隨伴)한 선천성뇌수종(先天性腦水腫) 1례(例)의 초음파소견(超音波所見)에 관한 보험의학적(保險醫學的) 연구(硏究) (A Study of Ultrasonography in One Congenital Hydrocephalus Case Accompanied with Meningoencephalocele)

  • 한혜진;김강석
    • 보험의학회지
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    • 제2권1호
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    • pp.245-252
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    • 1985
  • Ultrasonographic examination in the obstetrics not only makes easy of the diagnosis of Hydrocephalus, placenta previa, anencephalus and ectopic pregnancy, etc, but also guaranteed its excellence in the diagnosis of women gynecology disease. Especially in case that it doesn't affect radiation hazard on the embryo, its efficiency keeps increasing and it is spotlighted to many clinic doctors. Even though in general hospital we often observe congenital hydrocephalus in Med. Dept. which entirly undergoes the medical examination to the insured, we don't observe even the women delivered with child and it is very difficult to find a rare congenital hydrocephlus throughout other present insurance companies. We inspected a congenital hydrocephalus, which other medical equipments of present insurance companies have many difficulties in the medical examination, accompanied by meningoencephalocele by ultrasonic diagnosis. We analyzed and compared the data by ultrasonic diagnosis with that of surgical diagnosis and the results are follows; 1) We could correctly describe meningoencephalocele by ultrasonic diagnosis. 2) It was able to be diagnosed in LMP 22 weeks. 3) BPD has about 10 mm higher than normal value in LMP 22 weeks. 4) Dilatation of lateral ventricle was observed in LMP 22 weeks. 5) As paralled with ultrasonic diagnosis in pregnancy medical examination, accepting declines including the risk rate can be restrained.

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신생아에서 맹장의 장 중복낭종에 의해 발생한 장 폐쇄 1예 (Intestinal obstruction caused by a duplication cyst of the cecum in a neonate)

  • 금승운;황민우;나종인;유승택;강동백;오연균
    • Clinical and Experimental Pediatrics
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    • 제52권2호
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    • pp.261-264
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    • 2009
  • 장 중복낭종은 드문 선천성 기형 질환으로 구강에서 항문까지 어느 곳에서나 발견할 수 있고 장관과 교통하기도 한다. 특히 맹장의 장 중복낭종은 더욱 드문 질환이다. 이들은 구토나 반복적인 복통과 위장관 출혈 및 변비 등의 증상으로 급성 장폐색을 발생시키며 생후 2년내 80%에서 발견된다. 저자들은 신생아에서 맹장의 장 중복낭종에 의해 발생한 장 폐색 1예를 경험하였기에 보고하고자 한다.

기관 식도루를 동반한 선천성 식도 폐쇄증의 외과적 치료 (Surgical treatent of esophageal atresia with tracheo-esophageal fistula)

  • 김동원
    • Journal of Chest Surgery
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    • 제27권7호
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    • pp.603-609
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    • 1994
  • Esophageal atresia is a rare congenital anomaly and it usually associated with tracheo-esophgeal fistula and other congenital anomalies. The first report of esophageal atresia with tracheo-esophageal fistula was done by Thomas Gibson in 1696. In 1941, Haight performed the first successful primary anastomosis for esophageal atresia. These accomplishments opened the gateway for clinical studies that have resulted in reinforcements and improvement in the care of infants born with this anomaly. From January 1986 to April 1994, 14 cases of esophgeal atresia with tracheo-esophgeal fistula were diagnosed in Kyung Hee Uinv. Hospital. There were 9 male and 5 female infants. 12 infants were Gross classification type C and 2 infants were type A. The average body weight was 2.7$\pm$0.4kg and Waterson Category A contained 4 infants, B contained 3 infants and C contained 7 infants. Among these infants, 9 infants were underwent anastomosis procedures. We performed retropleural approach in 6 infants, transpleural approach in 2 infants and 1 infant was performed colon interposition through substernal space.By the method of anastomosis, end-to-side anastomosis was performed in 5 infants, end-to-end anastomosis in 3 infants and esophagocologastrostomy in 1 infant.The former 8 infants were Gross classification type C and the latter was type A. Among the type C infants, 6 infants were anastomosed with one layer interrupted suture and 2 infants with 2 layer interrupted suture. Post- operative death was in 1 infant and 8 infants were discharged with good result and have been in good condition.

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선천성 횡경막 이상증의 임상적 경험 (Clinical Experiences of Congenital Diaphragmatic Anomaly)

  • 현명섭;임승균;정광진
    • Journal of Chest Surgery
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    • 제28권4호
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    • pp.381-386
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    • 1995
  • In our hospital we have seen 20 cases of congenital diaphragmatic anomalies from June 1984 until December 1993. These were classified into 10 cases of diaphragmatic eventration, 8 cases of Bochdalek hernia, 1 case of Morgagni hernia, and 1 case of esophageal hiatal hernia. Diaphragmatic eventration cases were composed of 8 males and 2 females with ages varing from 3 hour to 42 year. They were discovered by symptoms: 5 cases of respiratory insufficiency; 3 cases of frequent respiratory infection; and 2 cases by chance; 6 cases involved the left side, 4 cases involved right side. Emergency operations were done to 4 patients. Among the 10 patients, only one operative mortality occurred; 3 hour old female.Bochdalek hernia cases composed 6 females and 2 males, 5 patients were less than 6 hour old. All patients were operated on an emergency status and three of them expired due to the vicious cycle of pulmonary hypertension and pulmonary vasoconstriction, persistent fetal circulation, hypoxia, and metabolic acidosis. Morgagni hernia was seen in one 69 year old female patient, she had no complaint of symptoms and was incidentally detected. Hernia was repaired through right thoracotomy. She was discharged with healthy appearence. Esophageal hiatal hernia was seen in a 10 month old male patient, his symptoms were persistent vomiting and coughing since birth. Sliding type of esophageal hiatal hernia repair was completed through left thoracotomy.

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외과적 수술을 받은 선천성 구순 구개열자의 두개 안면 형태에 관한 연구 (A STUDY ON THE CRANIOFACIAL MORPHOLOGY OF OPERATED CONGENITAL CLEFT LIP & PALATE)

  • 도송희;손병화
    • 대한치과교정학회지
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    • 제23권4호
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    • pp.543-564
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    • 1993
  • A cephalometric study was undertaken to reveal significant differences of craniofacial morphology of operated congenital cleft lip and palate subjects and control subjects. The material for this study consisted of 73 subjects with operated congenital cleft lip and palate subjects(53 males, 20 females) and 110 control subjects (7 males, 34 females) ranging from 3 to 14 years old. Each group was divided into four age groups (3-5, 6-8, 9-11, 12-14 year) and analyzed by Cohen's method and Burstone's method. The following conclusions were obtained ; 1. In Wit's appraisal, there was no difference the cleft lip and palate subjects and the control subjects. 2. In the cleft lip and palate subjects, they had smaller and more retrusive maxilla than the control subjects in both sexes. 3. In the cleft lip and palate subjects, they had more retrusive mandible than the control subjects in both sexes. 4. In the cleft lip and palate subjects, they had more concave profile than the control subjects.

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선천성 수부 윤상 수축대 증후군에 대한 미세현미경을 이용한 수술적 교정 (Congenital Constriction Band Syndrome of Hand ; The Correction Under The Microscope)

  • 황호;김용규;황종익
    • Archives of Reconstructive Microsurgery
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    • 제14권1호
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    • pp.70-76
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    • 2005
  • The Z-plasty has been known as a most common surgical treatment of congenital circumferential constriction band syndrome of the hand. There were thirteen patients of congenital circumferential constriction band syndrome of the hand. All patients underwent Z-plasty under microscope. we did microsurgical dissection to minimize vascular, neural and lymphatic injury, and then considering secondary correction and scar contracture, tried to preserve as much subcutaneous fat and skin flap as possible without any excision. There were less skin necrosis and lymphedema as a result of vascular compromise. Using microscope offers several advantages. First, preventing vascular, neural and lymphatic injury. Second, getting an accurate suture approximation. finally, preserving as much subcutaneous fat and skin flap as possible without any excision. The outcome of digit growth and contour can be excellent than we expected. As a results, we believe that correction of congenital circumferential constriction band syndrome of the hand under the microscope have better results.

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강송의 기초적 재질에 관한 연구(제1보) (Studies on the Fundamental Properties of the Wood of Gumgangsong(Pinus densoflora for. erecta Uyeki) (Part 1))

  • 김정환;이원희;홍선천
    • 한국가구학회지
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    • 제10권2호
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    • pp.55-61
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    • 1999
  • This research was carried out to investigate the fundamental properties such as the structure of annual ring, density distribution, compressive strength with parallel to grain, relative crystallinity, and microfibril angle of Gumgangsong(Pinus densoflora for. erecta Uyeki). The wood specimens, Gumgangsong and Sonamu(Pinus densiflora S. et Z.), for this experiment were prepared at Ulijingoon Sokwangri and Kyungpook university's forest in Kyungpook province, respectively. Average annual ring width is $2.0mm{\pm}0.3$ in heartwood of Gumgangsong. The respectively of heart wood was over 60 percent in Gumgangsong and 20~50 percent in Sonamu. Heartwood density were ranged from 0.5 to $0.8{\;}g/cm^3$ in Gumgangsong and from 0.4 to $0.5{\;}g/cm^3$ in sonamu. Compressive strength in Gumgangsong and Sonamu was about $30{\pm}5MPa$ and $25{\pm}5MPa$, resepectively. But the relative crystallinity and microfibril angle of two species were not different clearly. From these results of Gumgangsong and Sonamu, therefore, it was considered the main difference factors for both species were annual ring width and heartwood percentage.

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성인 선천성 심장기형의 외과적 치료 (Surgical correction of congenital heart defects in adult)

  • 신현종
    • Journal of Chest Surgery
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    • 제22권1호
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    • pp.95-105
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    • 1989
  • The records of 248 patients over 16 years of age who had undergone a surgical correction of a congenital cardiovascular malformation during the period of 10 years from August, 1978 to July, 1988 were reviewed. During this period, the incidence of congenital cardiovascular malformation in adult was 18.2% of 1376 total heart disease operated on and 25.5% of 986 congenital heart defects. Among them, there were 200 patients in acyanotic group and 48 patients in cyanotic group. Male versus female ratio was 1:1.28. The oldest patient was 59 years old female who had atrial septal defect. The mean age was 24.4 years old. The distribution of the lesions showed a large preponderance of atrial septal defects [37.19o] followed in frequency by ventricular septal defects [918.1%], patent ductus arteriosus [17.3%], tetralogy of Fallot [16.1%], and a variety of other complex malformations[3.2%]. In the pediatric age group, relative frequency was different from that of this adult group, showing ventricular septal defects, tetralogy of Fallot, patent ductus arteriosus and atrial septal defects in order of incidence. The hospital mortality and late mortality were 6.0% and 1.7% respectively. The causes of hospital death were low cardiac output in 10 patients, arrhythmia in 2, air embolism in 1, sepsis in 1 and respiratory failure in l. Clinical improvement upto NYHA functional class I or II postoperatively has been achieved and sustained in all patients following repair except the patients of late death and receiving reoperation. This result confirms that congenital heart defects in the adults can be corrected with a good outcome and an aggressive operative approach seems justified.

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선천성 식도 폐쇄 환자에서 출생 후 위루관 삽입술과 계속적인 금식상태에서 근본수술 후 발생한 비후성 유문 협착증 - 1예 보고 - (Hypertrophic Pyloric Stenosis Occurring in Fasting State with Gastrostomy After Surgery for Esophageal Atresia with Tracheoesophageal Fistula)

  • 정은영;최순옥;박우현
    • Advances in pediatric surgery
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    • 제17권1호
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    • pp.88-92
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    • 2011
  • The onset of hypertrophic pyloric stenosis in the postoperative course of esophageal atresia with tracheoesophageal fistula is rarely reported. The diagnosis could be delayed due to its mimicking symptoms of other postoperative complications including gastroesophageal reflux or anastomotic stricture. We present an infant who had surgery for esophageal atresia with tracheoesophageal fistula. He had never fed since birth. The infant presented with an increased amount of orogastric tube drainage and consistently distended gastric air on simple abdominal X-ray. Abdominal ultrasonography showed hypertrophic thick pyloric muscle. The diagnosis of pyloric stenosis was confirmed d is rarely reported. The diagnosis could be delayed due to its mimicking symptoms of other postoperative complications including gastroesophageal reflux or anastomotic stricture. We present an infant who had surgery for esophageal atresia with tracheoesophageal fistula. He had never fed. The infant presented with uring surgery, After pyloromyotomy, the patient's condition improved.

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선천성 폐동맥협착증의 외과적 요법 (Surgical Treatment of the Pulmonary Stenosis: A Report of 17 Cases)

  • 김자억
    • Journal of Chest Surgery
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    • 제11권4호
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    • pp.481-487
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    • 1978
  • Seventeen patients of the congenital pulmenic stenosis were operated at the department of Thoracic Surgery, Seoul National University Hospital. There were thirteen male and four females, and ranging from six to thirty years of age. And it's incidence was 2.7% of congenital heart disease cases that were operated on. (Total 628) Seven case of trilogy of Fallot were excluded. Two cases of bacterial endocarditis were found. Right heart catheterization was done in all patients. Average right ventricular pressure was $121{\pm}35.8$mmHg, pulmonary artery $20{\pm}6.8$mmHg, and RV-PA pressure gradient $98{\pm}34.5$mmHg. The preoperative average time interval of A2-P2 which was checked at phonocardiography was $0.08{\pm}0.016$second, and was reduced to $0.03{\pm}0.009$second postoperatively. One was operated by Varco's procedure, another one was done by Brock's procedure, and fifteen patients were done by open heart surgery with heart-lung machine. Pure valvular stenosis was found in sixteen and infundibular stenosis in one case. And the combining anormalies were two patent ductus arteriosus, two patent foramen ovale, and one tricuspid valve hypoplasia. Two expired postoperatively at the begining stage of cardiac surgery in this Department. The remaining fifteen showed excellent operative results.

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