• Journal of Chest Surgery
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• 제36권4호
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• pp.277-279
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• 2003

15세 남아가 경도의 운동 시 호흡곤란, 우연히 발견된 심잡음을 주소로 내원하였다. 심초음파 소견에서 주로 심실중격을 침범한 종양에 의한 좌심실유출로 협착을 보였고, 심도자에서 측정한 좌심실유출로 평균 압력차는 20 mmHg였다. 체외순환하에 대동맥절개를 통해 종양의 부분절제를 시행하였고, 병리검사 결과 심근이형종으로 진단되었다. 병변은 중증비대를 보이는 성숙한 심근세포와 주변부 섬유화가 주를 이루었다. 술 후 5년간의 외래추적관찰에서 부정맥 발생이나 종양 재발의 증거는 관찰되지 않았다.

• 대한두경부종양학회지
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• 제24권2호
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• pp.207-210
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• 2008

The purpose of this paper is to review our experience with mucoepidermoid carcinoma(MEC), a rare tumour in minor salivary glands, in a paediatric patients. 15-year-old boy was noted to have a irregular round mass appearing atthe soft palate just to the right of the mid-line. A computed tomographic(CT) scan showed a palatal mass limited to soft palate with no bony erosion. The lesion was curetted and debulked. Pathology was reported as an intermediate-grade mucoepidermoid carcinoma, and the patient was considered to radiation therapy institution for further treatment. To date, patients remain free of disease. Wide local excision is the treatment of choice for low to intermediate grade MEC of the minor salivary glands in paediatric patients.

• Journal of the Korean Association of Oral and Maxillofacial Surgeons
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• 제37권2호
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• pp.127-132
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• 2011

Juvenile ossifying fibroma is an expansive intraosseous lesion of the bones. In most patients, the tumors are located in the facial bones. The main characteristics of juvenile ossifying fibroma are the early age of onset, localization of the tumor, radiological pattern and a tendency for recurrence. This article describes a case of expanded juvenile ossifying fibroma in the right maxilla in a 12-year old boy. The lesion was removed totally by surgery under general anesthesia. The patient showed no radiological signals of recurrence approximately two years after surgery.

• 대한가정학회지
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• 제18권3호
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• pp.29-34
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• 1980

The purpose of this study is to clarify the effects of mother's occupation on the personality of the child. for the purpose of this study, the Minnesota multiphastic Personality Inventory were administered to 33 boy students with employed mothers and another 33 whose mothers spened full time as house wife selected from two high schools located in Seoul. -test were employed for the statistical analysis of the data and the following are the findings: 1. In general working mother does not have any remarkable influence on personality of the child. 2. There is no significant difference between two groups except on scale, Sc scale, and Hs scale. 3. It may not be the mother's occupation but her attitude that influences the child's personality.

• 한국가정과교육학회지
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• 제14권2호
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• pp.79-95
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• 2002

The Purposes of this study are first to develop the teaching and learning plan for the dress part in high school's Home Economics by the application of the values clarification theory then to apply it to the classroom activities. and lastly to analyze its effects. We developed the master plan for teaching and learning, and developed the 12 hour sub plans including 7 activities and learning materials. The effects of the teaching are as followings: First, When the self-esteem was compared with the whole classes, there was no difference between the twos, but a boy and a girl who were observed as not making a value-oriented life marked higher score in answering the self-esteem. Second. It was found that values clarification theory made student's degree of participation and interest higher and helped them to choose their dresses in the real life.

• 가정과삶의질연구
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• 제17권3호
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• pp.33-46
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• 1999

The purpose of this stud was to investigate how the children's perceptions of interpersonal relations(parent, family and peers) and self are related to social preference. The subjects of this study were 625 children of 5th and 6th grade in 4 primary schools in Tajon. Social preference was highly correlated with perceptions of peer and of father. The direct path between boy's perceptions of parent/family and peer ratings of social preference was no longer significant whereas there was a significant path mediated by their perception of self. This suggests that boys and girls' peer representations were established for the role as mediators between parents/ family representations and peer ratings of social preference. In addition negative representations of self and others were found to be associated with increased social impairment and less positive status in the peer groups.

• Journal of Genetic Medicine
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• 제18권1호
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• pp.55-59
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• 2021

West syndrome (WS) presenting with infantile spasms, developmental delay, and hypsarrhythmia has genetic etiology in some patients. Movement disorders or visual impairment that share genetic underpinnings with infantile spasms can provide diagnostic clues for specific genetic mutations. Mutations of the GRIN1 gene encoding the glutamate receptor inotropic N-methyl-D-aspartate subunit can result in WS with hyperkinetic movements, cortical visual impairment, autistic features, and bilateral polymicrogyria. An 11-month-old boy with WS showed hyperkinetic movements and visual impairment. Brain magnetic resonance imaging and metabolic investigations revealed no abnormalities. Whole-exome sequencing revealed a novel likely pathogenic variant (c.1561_1563del; p.Asn521del) of GRIN1 (NM_007327.3). The proband was treated with vigabatrin and became seizure-free within one week. Notably, the cortical blindness improved within 3 months and the hyperkinetic movements resolved one year after the proband became seizure-free. To the best of our knowledge, this is the first report of GRIN1 encephalopathy in Koreans.

• 대한두개안면성형외과학회지
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• 제23권6호
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• pp.274-277
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• 2022

Fractures of the zygoma are rarely encountered in pediatric patients. This report presents a case of a 3-year-old child who presented with a vertically split fracture of the marginal tubercle of the zygoma. The marginal tubercle, a bony portion present on the posterior border of the frontal process, assists in attaching the temporalis fascia. This patient was treated surgically with bony fixation using tissue glue. To the best of our knowledge, no cases of fracture of the marginal tubercle of the zygoma have been reported in the literature. Fractures of the marginal tubercle of the zygoma in pediatric patients may be overlooked because of their anatomic location and the musculoskeletal characteristics of these patients. Here, we discuss the clinical features of marginal tubercle fractures of the zygoma.

• Journal of Chest Surgery
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• 제28권6호
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• pp.565-570
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• 1995

Seventy-three patients with isolated total anomalous pulmonary venous connection the patients associated with other major cardiac anomalies such as single ventricle, DORV[Double Outlet Right Ventricle and large VSD[Ventricular Septal Defect were excluded were underwent surgical repair from January 1980 through October 1993. There were 45 boys and 28 girls. The mean age at operation was 19.9 months[range 6 days to 24 years and mean body weight was 7.1kg[range 2.6kg to 45kg . The anomalous locations of connection were supracardiac in 38, cardiac in 21, infracardiac in 5, and mixed in 9. In 38 patients[52% , the venous drainage was obstructed. The obstruction ratios according to the connection type were as follows: 53%[28/38 in supracardiac, 52%[11/21 in cardiac, 100%[5/5 in infracardiac, 22%[2/9 in mixed type. The associated cardiac anomalies were persistent left SVC[2 , tricuspid valve regurgitation[3 , cor triatriatum[1 , and mitral cleft[1 . And associated noncardiac anomalies were imperforate anus[1 and Neil Weightman syndrome[1 . The operative mortality was 23%. The causes of death were pulmonary hypertensive crisis, perioperative myocardial failure, pneumonia with sepsis, arrhythmia and etc. The statistically significant factors in postoperative mortality were the pulmonary venous obstruction and age [p<0.01 . The operative mortality was high in groups of age under 1 month and pulmonary venous obstruction. The mean follow-up was 27.1 months. There were two late deaths. The first patient was three months old boy with supracardiac type and severe obstructive symptoms. The postoperative echocardiography was showed anastomotic stenosis and reoperations were performed twice but the patients expired due to pneumonia and sepsis. The second patient was three month old boy with supracardiac type and total correction was done and was doing well postoperatively. Eight years later, he expired suddenly due to arrhythmia. But all the other patients were in NYHA Fc I and received no medications. The 5-year survival rate excluding early expired patients is 97.1 $\pm$ 0.03 %. In conclusion, although the operative mortality of total anomalous pulmonary venous connection was relatively high compared to other major cardiac anomalies, we could expect excellent long-term results by early surgical correction.

• 아동학회지
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• 제33권6호
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• pp.21-34
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• 2012

This study examined the effects of physical activities using Korean dance upon the motor abilities of young children. The subjects of this study were divided into 2 groups. The first group was an experimental group (boy=12, girl=13) who participated in the Korean dance class and the other group was a comparative group (boy=11, girl=14). Experiments were performed during 18 sessions for 9 weeks. The study findings are as follows. First, physical activities using Korean dance had positive effects upon the development of basic motor abilities in young children. In terms of these basic motor abilities, movement motor ability and whole muscle operation motor ability showed significant differences between the pre-test and post-test stage in the experiment group and between the experimental and comparative groups in the post-test stage. On the other hand, in terms of non-movement motor abilities, there was a significant difference between the pre- and post-test stages for the experimental group, but no significant difference in the post-test stage for the experimental or comparative groups. Second, physical activities using Korean dance had positive effects upon the development of perceptive motor abilities in young children. In other words, in the sub-variables of perceptive motor abilities, there were significant differences between the pre- and post-test stages of the experimental group which experienced physical activities using Korean dance. In conclusion, the study findings showed that physical activities using Korean dance had positive effects upon the increase of both basic motor abilities and perceptive motor abilities in young children. Additionally, the experimental group exhibited more positive effects in the various areas of motor abilities than the comparative group.