• 제목/요약/키워드: Low grade fibromyxoid sarcoma

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흉벽에 발생한 저등급의 섬유점액성 육종 -1 례 보고- (Low Grade Fibromyxoid Sarcoma in Chest Wall -One case report-)

  • 이기복;홍기우;박희철;이원진;김건일;최광민;박혜림;장기택
    • Journal of Chest Surgery
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    • 제35권8호
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    • pp.638-641
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    • 2002
  • 저등급의 섬유점액성 육종은 최근에야 진단적 분류가 이루어진, 드문 연부 조직 종양이다. 젊은 성인의 심부연부 조직에서 발생하는 경향이 있으며, 국소 재발이나 원격 전이가 가능하다. 진단적 범주가 확실히 정립되어 있지 않고 특정한 질환명으로 구분되고 있지 않다. 조직학적으로, 주로 소용돌이 양상으로 자라는 방추상세포와 점액성이나 섬유성 기질이 번갈아 관찰되는 것이 특징이다. 형태학적이나 면역조직학적 특징에 대한 세심한 고려가 상기 질환의 진단에 도움이 되며, 다른 양성이나 악성 연부 조직 종양과의 감별에 도움이 된다. 흉백에 발생한 저등급의 섬유점액성 육종을 경험하였기에, 문헌 고찰과 함께 보고하는 바이다.

견갑부에서 저등급 섬유점액성 육종 - 1례 보고- (Low grade fibromyxoid sarcoma in shoulder -One case report-)

  • 이상선;송철;선두훈;문명상
    • 대한골관절종양학회지
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    • 제10권2호
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    • pp.130-133
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    • 2004
  • 저등급의 섬유점액성 육종은 매우 드문 연부 종양이다. 젊은 성인에서 발생하는 경향이 있으며, 국소 재발이나 원격 전이가 가능하다. 이들 종양 대부분은 하지 연부 조직에 발생하는 것으로 알려졌다. 조직학적으로 방추상 세포와 점액성 기질과 섬유성 기질이 혼재된 양상으로 관찰되는 것이 특징이며, 면역 조직학적 검사상 다른 양성 종양이나 악성 연부 조직과의 감별에 도움이 된다. 견갑부의 저등급의 섬유점액성 육종을 경험하였기에 문헌 고찰과 함께 보고하는 바이다.

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Primary Paravertebral Low-Grade Fibromyxoid Sarcoma

  • Lee, Woo-Jin;Park, Chong-Oon;Yoon, Seung-Hwan;Chu, Young-Chae
    • Journal of Korean Neurosurgical Society
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    • 제48권5호
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    • pp.461-464
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    • 2010
  • The authors report a 58-year-old woman with low-grade fibromyxoid sarcoma primarily located in the right paravertebral area with extension to L4 neural foramen. The patient complained lower back pain with radiating pain along the posterolateral aspect of the right lower leg. She underwent subtotal surgical removal and Cyber Knife therapy. Diagnosis was made by strikingly characteristic microscopic appearance of a bland spindle cell sarcoma which contained numerous giant collagen rosettes and was also supported by immunohistological findings. The diagnostic image findings and literatures are reviewed and discussed.

후비강에서 발생한 저등급의 섬유점액성 육종: 증례 보고 및 문헌 고찰 (Low-Grade Fibromyxoid Sarcoma Arising in Posterior Nasal Cavity: Case Report and Review of the Literature)

  • 손정협;이기진;조경래
    • Korean Journal of Otorhinolaryngology-Head and Neck Surgery
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    • 제61권11호
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    • pp.624-629
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    • 2018
  • Low-grade fibromyxoid sarcoma (LGFMS), a soft tissue tumor that has high recurrence and metastasizing potential, rarely occurs in the head and neck region. Therefore, the treatment for LGFMS in the facial area is challenging in terms of cosmetic and functional maintenance. The authors report a case of LGFMS in the posterior nasal cavity. It was completely removed in parallel with the nasal endoscopic and oral approach, but the lower margin was closed by preserving the soft palate. The patient is well without any recurrence or metastasis after 5 years of follow-up.

저등급 섬유점액육종의 세포소견 -1예 보고- (Cytological Features of Low Grade Fibromyxoid Sarcoma -Report of a Case with a Review of the Literature-)

  • 권미선
    • 대한세포병리학회지
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    • 제17권2호
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    • pp.153-158
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    • 2006
  • Low-grade fibromyxoid sarcoma (LGFMS) is a rare soft tissue tumor. There have been only a few prior fine-needle aspiration (FNA) cytological reports. Recognition of this tumor is important because of its potential for metastasis despite its indolent nature and its deceptively bland cytologic appearance. A 60-year-old male presented with a slowly growing mass in the left calf detected 10 years ago. The patient underwent surgical excision. FNA cytology was performed directly on the mass. The smears showed low cellularity composed of hypercellular tissue fragments, hypocellular loose aggregates, and stripped nuclei. The cytoplasm was seen as either collagenous material or very thin fibrillary collagen strands. Tumor cells had spindle, ovoid, or irregular nuclei, fine chromatin, and small nucleoli. Focally slight degree of nuclear pleomorphism is noted. There were no mitotic figures. Blood vessels were frequently seen. Immunocytochemically, tumor cells were negative for S-100 protein, desmin, smooth muscle actin, and CD34. The diagnosis of LGFMS is rarely possible by cytology alone; however, LGFMS should be included in the differential diagnosis of spindle-cell tumors consisting of hypercellular and hypocellular components with some capillary-sized vessels arising in the deep soft tissue of the lower extremities, particularly the thigh. The immunocytochemical findings are of help in the differential diagnosis.

장측 늑막에서 발생한 저등급 섬유점액성 육종 - 1예 보고 - (Low Grade Fibromyxoid Sarcoma of the Visceral Pleura - A case report -)

  • 김연수;장선희;이성순;류지윤;박경택;장우익;김창영;조성준
    • Journal of Chest Surgery
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    • 제41권1호
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    • pp.141-144
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    • 2008
  • 저등급 섬유점액성 육종은 드문 심연부 조직의 악성 종양이다. 비록 조직학적으로는 양성 소견을 보이지만 임상적으로는 악성 경과를 보인다. 일반적으로 하지나 체벽에서 발생하는 종양이며, 장측 늑막에서 발생된 보고는 극히 드물다. 저자들은 37세의 남자에서 장측 늑막에서 기원한 저등급 섬유점액성 육종의 증례를 보고한다. 수술 33개월째 국소재발이나 원격전이 없이 추적 관찰 중이다.

The Magnetic Resonance (MR) Imaging Features of Myxoid Liposarcoma Arising from the Mesentery: a Case Report

  • Ahn, Taehoon;Lee, Young Hwan;Lee, Guy Mok;Kim, Youe Ree;Yoon, Kwon-Ha
    • Investigative Magnetic Resonance Imaging
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    • 제21권4호
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    • pp.252-258
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    • 2017
  • Primary mesenteric liposarcoma is rare. It is difficult to make an accurate preoperative diagnosis of the myxoid type of liposarcoma by using imaging such as ultrasound or computed tomography (CT) due to the very small amount of fat that is located in the tumor. We report a case of primary myxoid liposarcoma of the mesentery which was difficult to differentiate from other solid mesenteric tumors with a myxoid component such as low grade fibromyxoid sarcoma, myxoid leiomyosarcoma or myxoma. Use of chemical shift magnetic resonance (MR) imaging to detect small fat components and its cystic appearance with solid components on the MR images can be useful to differentiate myxoid liposarcoma from the other mesenteric tumors with a myxoid component.