Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
권호 표지

Low Grade Fibromyxoid Sarcoma of the Visceral Pleura - A case report -

장측 늑막에서 발생한 저등급 섬유점액성 육종 - 1예 보고 -

  • Kim, Yeon-Soo (Department of Thoracic and Cardiovascular Surgery, Ilsan Paik Hospital, College of Medicine, Inje University) ;
  • Chang, Sun-Hee (Department of Anatomical Pathology, Ilsan Paik Hospital, College of Medicine, Inje University) ;
  • Lee, Sung-Soon (Department of Internal Medicine, Ilsan Paik Hospital, College of Medicine, Inje University) ;
  • Ryoo, Ji-Yoon (Department of Thoracic and Cardiovascular Surgery, Ilsan Paik Hospital, College of Medicine, Inje University) ;
  • Park, Kyung-Taek (Department of Thoracic and Cardiovascular Surgery, Ilsan Paik Hospital, College of Medicine, Inje University) ;
  • Chang, Woo-Ik (Department of Thoracic and Cardiovascular Surgery, Ilsan Paik Hospital, College of Medicine, Inje University) ;
  • Kim, Chang-Young (Department of Thoracic and Cardiovascular Surgery, Ilsan Paik Hospital, College of Medicine, Inje University) ;
  • Cho, Seong-Joon (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Kangwon National University)
  • 김연수 (인제대학교 의과대학 일산백병원 흉부외과학교실) ;
  • 장선희 (인제대학교 의과대학 일산백병원 병리학교실) ;
  • 이성순 (인제대학교 의과대학 일산백병원 내과학교실) ;
  • 류지윤 (인제대학교 의과대학 일산백병원 흉부외과학교실) ;
  • 박경택 (인제대학교 의과대학 일산백병원 흉부외과학교실) ;
  • 장우익 (인제대학교 의과대학 일산백병원 흉부외과학교실) ;
  • 김창영 (인제대학교 의과대학 일산백병원 흉부외과학교실) ;
  • 조성준 (강원대학교 의과대학 흉부외과학교실)
  • Published : 2008.02.05
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Abstract

Low grade fibromyxoid sarcoma (LGFM) is a rare, deep soft-tissue malignant tumor. Although its histologic features are benign, the clinical course is malignant. The usual tumor locations are the lower extremity and chest wall. LGFM originating from the visceral pleura is extremely rare. We report here on a 37 year old man with a LGFM of the visceral pleura. Thirty three months after surgery, the patient is alive without any sign of local recurrence or distant metastasis.

저등급 섬유점액성 육종은 드문 심연부 조직의 악성 종양이다. 비록 조직학적으로는 양성 소견을 보이지만 임상적으로는 악성 경과를 보인다. 일반적으로 하지나 체벽에서 발생하는 종양이며, 장측 늑막에서 발생된 보고는 극히 드물다. 저자들은 37세의 남자에서 장측 늑막에서 기원한 저등급 섬유점액성 육종의 증례를 보고한다. 수술 33개월째 국소재발이나 원격전이 없이 추적 관찰 중이다.

Keywords

References

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