• Annals of Clinical Neurophysiology
• /
• 제3권2호
• /
• pp.160-163
• /
• 2001

Mirror movements in adult is usually accompanied with various clinical syndromes. But the pathogenesis of mirror movement is not clearly understood. A 20-year-old man visited with complaining of mirror movements in both hands, ophthalmoplegia and sensorineural hearing loss. He underwent through electromyography, transcranial magnetic stimulation, and functional magnetic resonance image. And we concluded that the mechanisms of his mirror movements were both ipsilateral innervated corticospinal tract and simultaneous activation of both motor cortex.

• 대한치과의사협회지
• /
• 제58권7호
• /
• pp.404-411
• /
• 2020

This study reports the unusual complications of 22-year-old male who presented with sudden hearing loss after the right mandibular third molar extraction under local anesthesia with 3.6 ml of 2 % lidocaine. Total 8.75 mg of oral dexamethasone for 1 week immediately after extraction was prescribed in department of oral and maxillofacial surgery but hearing did not improve after 1 week. As referral to otolaryngology, total 600 mg of oral methylon and hyperbaric oxygen therapies were operated for 2 weeks. The hearing of patient was improved at 6 weeks after extraction but tinnitus was persisted even after 12 months. The reason and treatment were discussed with literature review, searching with the keywords ['hearing loss' AND ('dental' OR 'tooth extraction'OR'teeth extraction')] in PubMed and Google scholar at October 2019. Total five cases were reported after tooth extraction with local anesthesia. The sudden hearing loss could be associated with local anesthesia containing vasoconstrictors. Early steroid (extensive medication and intra-tympanic injection) and hyperbaric oxygen therapies were recommended within 2 weeks. As a proper treatment, hearing could be improved but other additional symptoms, such as tinnitus, dizziness, might be remained.

• 재활복지
• /
• 제18권4호
• /
• pp.295-314
• /
• 2014

본 연구는 난청인이 오류를 보이는 음소들의 유형과 오류율을 확인하여 청능재활 현장에서 한국자음지각검사(KCPT)를 더욱 잘 활용할 수 있도록 기초자료를 제공하는데 목적이 있다. 30명의 감각신경성난청인을 대상으로, KCPT를 실시하여 오류유형, 화자에 따른 KCPT 점수의 변화 등을 알아보았다. 오류유형의 경우 30% 이상의 오류율을 보인 음소는 초성검사문항의 경우 /ㄷ/, /ㅂ/, /ㅃ/, /ㅉ/, /ㅌ/이었으며, /ㅊ/을 제외한 모든 음소에서 10% 이상의 오류율을 보였다. 종성검사문항에서 30% 이상의 오류율을 보인 음소는 /ㄱ/과 /ㄷ/ 이었다. 오류유형을 살펴보면 초성검사문항에서는 초성자음대치, 종성검사문항에서는 종성자음대치가 가장 많은 것으로 나타났으며, 각 검사문항이 초성 및 종성에 대한 검사에 적절한 도구임을 확인하였다. 또한 KCPT를 발화하는 화자가 남성 또는 여성으로 바뀌어도 점수에는 유의한 차이를 보이지 않는 것으로 나타나서 재활현장에서 화자의 성별에 관계없이 KCPT를 활용할 수 있음을 확인하였다.

• Journal of Audiology & Otology
• /
• 제25권4호
• /
• pp.209-216
• /
• 2021

Background and Objectives: We aimed to analyze treatment outcomes following different initial management approaches and confirm treatment regimens for acute low-tone sensorineural hearing loss (ALHL) that would yield the best results. Subjects and Methods: We retrospectively analyzed the medical records of 106 patients with ALHL who visited a university hospital's otology clinic from March 2013 to June 2019. Pure-tone averages at the initial visit and at 2 and 4 weeks after the initial visit were evaluated. Results: Forty-nine patients were enrolled in this study; of them, 41 (83.7%) exhibited complete recovery (CR) at 2 weeks and 43 (87.8%) exhibited CR at 1 month after the initial visit. Regression analysis revealed that CR at 2 weeks after the initial visit was associated with diuretic use [Exp(B): 10.309, 95% confidence interval (CI): 1.007-100]. An initial daily low-dose steroid use was marginally significant [Exp(B): 1.042, 95% CI: 0.997-1.092; p=0.066]. Isolated diuretic use [Exp(B): 25.641, 95% CI: 1.121-90.909; p=0.039] was an independent, good prognostic factor at 1 month after the initial visit. However, other treatment regimens did not affect the final results. Conclusions: A combination of initial daily administration of ≤30 mg prednisolone plus diuretics was sufficient as the first-line treatment for ALHL. High-dose steroids and salvage intratympanic steroid injections can be applied as a second choice; however, the predicted outcome would not be good in that case.

• 대한청각학회지
• /
• 제25권4호
• /
• pp.209-216
• /
• 2021

Background and Objectives: We aimed to analyze treatment outcomes following different initial management approaches and confirm treatment regimens for acute low-tone sensorineural hearing loss (ALHL) that would yield the best results. Subjects and Methods: We retrospectively analyzed the medical records of 106 patients with ALHL who visited a university hospital's otology clinic from March 2013 to June 2019. Pure-tone averages at the initial visit and at 2 and 4 weeks after the initial visit were evaluated. Results: Forty-nine patients were enrolled in this study; of them, 41 (83.7%) exhibited complete recovery (CR) at 2 weeks and 43 (87.8%) exhibited CR at 1 month after the initial visit. Regression analysis revealed that CR at 2 weeks after the initial visit was associated with diuretic use [Exp(B): 10.309, 95% confidence interval (CI): 1.007-100]. An initial daily low-dose steroid use was marginally significant [Exp(B): 1.042, 95% CI: 0.997-1.092; p=0.066]. Isolated diuretic use [Exp(B): 25.641, 95% CI: 1.121-90.909; p=0.039] was an independent, good prognostic factor at 1 month after the initial visit. However, other treatment regimens did not affect the final results. Conclusions: A combination of initial daily administration of ≤30 mg prednisolone plus diuretics was sufficient as the first-line treatment for ALHL. High-dose steroids and salvage intratympanic steroid injections can be applied as a second choice; however, the predicted outcome would not be good in that case.

• Childhood Kidney Diseases
• /
• 제24권2호
• /
• pp.91-97
• /
• 2020

Purpose: Alport syndrome (AS) is one of the most common inherited renal diseases caused due to mutations of genes encoding specific proteins of the type IV collagen family, and its major clinical manifestations include progressive renal failure, sensorineural deafness, and ocular abnormalities. We investigated the clinical characteristics and long-term prognosis of AS in Korean pediatric and adult populations. Methods: We conducted a retrospective review of medical records of 33 children and adults who had been diagnosed or treated with AS from 1985 to 2019. Results: The mean age of the 33 patients diagnosed with AS was 16.2±13.6 years, and the male-to-female ratio was 2:1. At the first visit, recurrent gross hematuria was the most common initial symptom. In 10 of 33 patients (30.3%), sensorineural hearing loss (SNHL) was diagnosed, but none had ophthalmic problems. Moreover, 11 of 33 patients (33.3%) had advanced to end-stage renal disease (ESRD), and a significant difference was observed in the age of the patients who progressed to ESRD based on the presence or absence of SNHL (P=0.035). Conclusion: SNHL in AS can be an important prognostic factor for long-term deterioration of renal function. Further investigation is required to confirm the clinical course and the genetic characteristics of AS in Korea through prospective national cohort studies.

• 대한기관식도과학회:학술대회논문집
• /
• 대한기관식도과학회 1978년도 제12차 학술대회연제 순서 및 초록
• /
• pp.8.2-8
• /
• 1978

언어는 청각을 통해서 발달하는 것으로서 난청이 있어서 듣지 못하는 경우 그 사람의 언어발달은 정지되어 농아자가 되는 경우가 많다. 따라서 언어발달에 미치는 영향 때문에 유아난청의 조기진단 및 치료는 대단히 중요하다고 하겠다. 이에 저자를은 유아난청의 원인을 조사함으로써 유아난청의 예방 및 치료에 도움을 주고자 1977년 1월부터 8월까지 8개월 동안에 본원 외래 난청실로 내방한 만5세 이하의 난청아 185명을 대상으로 하여 자세한 병력과 상세한 임상적 검사 및 Impedance audiometer(Madsen ZO 70)에 의한 청역검사를 실시하고 그 원인에 대한 통계적 고찰을 시도하여 다음과 같은 결과를 얻었다. 1. 유아난청 중 감각신경성난청의 가장 흔한 원인은 유아자신의 감염(123례중, 44례, 35.8%)이었으며 임신중의 모체의 상태(37례 30.1%), 분만시 외상 혹은 두부외상(18례, 14.7%)의 순이었다. 2. 유아난청 중 부음성난청의 가장 흔한 원인은 급성 혹은 만성중이질환이었으며(62례중 32례, 51.6%), 다음으로는 잦은 상기도감염(19례, 30.6%), 아데노이드 증식증(7례, 11.3%)의 순이었다. 3. 유아난청은 외인성원인이 185례중 179례(96.8%), 내인성원인이 6례(3.2%)로 대부분이 외인성 원인이었다.

• 대한의용생체공학회:의공학회지
• /
• 제32권3호
• /
• pp.218-229
• /
• 2011

Companding algorithms have been used to enhance speech recognition in noise for cochlea implant users. The efficiency of using companding for digital hearing aid users is not yet validated. The purpose of this study is to evaluate the performance of the companding for digital hearing aid users in the various hearing loss cases. Using HeLPS, a hearing loss simulator, two different sensorinerual hearing loss conditions were simulated; mild gently sloping hearing loss(HL1) and moderate to steeply sloping hearing loss(HL2). In addition, a non-linear compression was simulated to compensate for hearing loss using national acoustic laboratories-non-linear version 1(NAL-NL1) in HeLPS. In companding, the following four different companding strategies were used changing Q values(q1, q2) of pre-filter(F filter) and post filter(G filter). Firstly, five IEEE sentences which were presented with speech-shaped noise at different SNRs(0, 5, 10, 15 dB) were processed by the companding. Secondly, the processed signals were applied to HeLPS. For comparison, signals which were not processed by companding were also applied to HeLPS. For the processed signals, log-likelihood ratio(LLR) and cepstral distance(CEP) were measured for evaluation of speech quality. Also, fourteen normal hearing listeners performed speech reception threshold(SRT) test for evaluation of speech intelligibility. As a result of this study, the processed signals with the companding and NAL-NL1 have performed better than that with only NAL-NL1 in the sensorineural hearing loss conditions. Moreover, the higher ratio of Q values showed better scores in LLR and CEP. In the SRT test, the processed signals with companding(SRT = -13.33 dB SPL) showed significantly better speech perception in noise than those processed using only NAL-NL1(SRT = -11.56 dB SPL).

• 한국음향학회지
• /
• 제19권2호
• /
• pp.61-67
• /
• 2000

최근의 디지털 신호처리 기술과 집적 회로 설계 기술의 발달은 보청 시스템의 새로운 가능성을 제공하고 있다. 그러나, 배경 잡음은 여전히 많은 난청자가 호소하는 문제로 남아 있다. 본 논문에서는 임상 실험을 통하여 음성 대역 잡음 환경에서 감음신경성 난청자의 음성 인지 능력과 어음 변별력을 측정한 결과를 제시한다. 또한, 보다 향상된 보청 환경을 제공하기 위하여 보청 시스템의 전처리단으로써 음질 향상 기법을 이용하여 배경 잡음을 제거하였다. 음질 향상 기법은 DSP 보드를 이용하여 실시간 시스템으로 구현되었으며, 이를 이용하여 청력 검사를 실시하였다. 임상 실험을 실시한 결과, 음질 향상 기법은 배경 잡음을 제거함으로써 신호의 SNR을 개선시켜 보청 이득과 결합되어 감음신경성 난청자의 음성 변별력을 크게 향상시켰다.

• 대한두경부종양학회지
• /
• 제27권1호
• /
• pp.84-87
• /
• 2011

Branchio-otic syndrome(BOS) is a relatively uncommon genetic malformation associated with dysmorphogenesis of the first and second branchial arches and is characterized by branchial fistulae, congenital preauricular fistulae, and anomalies of the pinnae, external, middle, and inner ears, accompanied by hearing loss. Recently, we experienced a case of BOS in a 10 years old female patient and report this case with a review of literature. 10-year-old girl presented with hearing impairment, bilateral preauricular fistula and cervical fistula. The pure tone audiometry revealed that she had 60dB sensorineural hearing loss on right side and 90dB mixed hearing loss on left. Bilateral branchial fistula was found on the neck CT scan and bilateral ossicular and cochlear abnormality combined with enlarged internal auditory canal was noted on the temporal bone CT scan. To investigate the association with EYA1 gene, we performed DNA sequncing with peripheral white blood cell and found the point mutations on Exon 7, 12 and 16 of EYA1 gene. The preauricular fistula and branchial fistula was excised surgically and hearing aid was applied on her left side. There was no sign of fistula recurrence for seven years after the surgery.