• Journal of Chest Surgery
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• 제27권1호
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• pp.57-59
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• 1994

Ebstein`s anomaly, a rare congenital cardiac anomaly, is characterized by downward displacement of abnormal tricuspid valve. Indication for surgical repair and the optimal surgical approach are still controversy. Recently, we experience a case of Ebstein anomaly, which was treated by atrilized right ventricular plication and annuloplasty. The patient was discharged with good result on 17th post-operative day.

• Journal of Chest Surgery
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• 제25권8호
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• pp.826-831
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• 1992

Ebstein`s anomaly is characterized by a downward displacement of a malformed tricuspid valve, The ideal surgical management of Ebstein`s anomaly is not yet established. Recently we experience one case of Ebstein`s anomaly, which was treated sussessfully by partial artificial annulus formation, and tricuspid valve replacement with St. Jude Medical valve. We have achieved excellent results with mechanical valve replacement and partial artificial annulus formation using wessex pericardial patch. On follow up for 4 years, the patient is well and in functional class I.

• Journal of Chest Surgery
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• 제13권4호
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• pp.435-441
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• 1980

Ebstein`s anomaly had been amenable to reparative surgery since 1962. However, neither the role of surgery in Ebstein`s anomaly nor the surgical procedure of choice for its correction are clearly defined. Whether or not the atrialized right ventricle, which plays a major role in the functional abnormalities, should be obliterated in all cases remains unsolved. Four cases of Ebstein`s anomaly treated surgically at Seoul National University Hospital were reported. All had closure of the atrial septal defect, obliteration of the atrialized right ventricle by plication, and insertion of a tricuspid bioprosthesis and an epicardial ventricular pacemaker. One patient had a pulmonic valvotomy due to stenotic bicuspid pulmonic valve also. All but one had discharged with a good result.

• Journal of Chest Surgery
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• 제24권9호
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• pp.907-912
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• 1991

Isolated primary tricuspid insufficiency except Ebstein`s anomaly is rare disease. Recently we experienced two cases of isolated primary tricuspid insufficiency and treated successfully with annuloplasty or valve replacement. We could not classify our case as one of the classification of isolated tricuspid insufficiency, because the morphology and microscopic finding did not suggest any similar variety.

• Journal of Chest Surgery
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• 제42권4호
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• pp.509-512
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• 2009

엡스타인 기형은 다양한 형태의 삼첨판막 및 우심실의 이상을 나타내는 선천성 심기형이다. 동반되는 삼첨판막의 역류를 교정하기 위하여 다양한 성형술식들이 사용되고 있으나, 대부분은 전염만을 이용한 단일판막화 술식이다. 저자들은 엡스타인 기형을 가진 31세 여자 환자에게 세개의 판막엽들을 모두 이용하는 cone 재건술로 삼첨판막 성형술을 시행하여 좋은 결과를 얻었기에 보고하는 바이다.

• Journal of Chest Surgery
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• 제29권11호
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• pp.1202-1206
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• 1996

Ebstein기형은 삼첨판, 우심실 및 우심방의 특징적인 변형를 보이는 희귀한 선천성 심질환으로, 삼첨판의 후판막첨과 중격판막첨이 우심실로 나선형의 변형을 보이는 것이 특징적이다. 본 교실에서는 1988년 1월 1일부터 1995년 12월 31일까지 7년간 11명의 환자를 경험하였으며 평균연령은 29.6$\pm$11.1세, 성비는 남자 5명 여자 6명이었고, 주증상으로는 운동시 호흡곤란이었다. 모든례에서 삼첨판의 전형적인 변형을 보였으며 동반된 심기형으로는 개방성 난원창, 심방중격결손, 심실중격결손이 있었다. 9명은 Danielson씨 삼첨판성형술과 주름성형술을 시행하고 2명은 삼첨판막치환술과 주름성형술을 시행하였으며 동반된 심기형을 교정하였다. 수술후 5명의 환자에서 저심박출증, 부정맥, 창상감염 등의 합병증이 발생하였으며 수술사망례는 없었다. 술후 평균 33.3개월의 추적관찰 결과 모든 환자에서 술전보다 양호한 심기능을 보였다.

• Journal of Chest Surgery
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• 제18권3호
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• pp.391-397
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• 1985

Ebstein`s anomaly is a rare congenital cardiac malformation and characterized by downward displacement of an abnormal tricuspid valve cusps. But until now, the ideal surgical correction is still controversial. We present a case of Ebstein`s anomaly experienced lately. The patient was 13 year old girl with the complaints of dyspnea on exertion, fatigability and cyanosis. Echocardiography revealed downward displacement of septal leaflet of tricuspid valve and atrialized right ventricle. Cardiac catheterization and cineangiography revealed ASD and large right atrium. During operation, the atrialized right ventricle was plicated and tricuspid annuloplasty was done. And the two secundum type ASD`s were closed by direct suture closure. The patient`s postoperative course was uneventful and discharged on the 24th postoperative days.

• Journal of Chest Surgery
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• 제20권3호
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• pp.506-511
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• 1987

Increased clinical interest, stimulated by newer diagnostic techniques, has made it apparent that Ebstein`s anomaly represents a spectrum of right heart abnormalities. In the usual case, the septal and posterior leaflets of the tricuspid valve are not attached to the true annulus, but are displaced distally into the ventricle. Also the degree of malattachment and the structural deformities of the cusps may vary greatly. Recently we experienced 6 cases of Ebstein`s anomaly who underwent corrective operation in our hospital. Five patients were operated by plication and annuloplasty techniques based on the construction of a monocusp valve by the use of the anterior leaflet. Remained one was operated on by tricuspid valve replacement using No 31 mm C-E tissue valve. There was no operative mortality and the postoperative courses were relatively good with marked symptom improvement.

• Journal of Chest Surgery
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• 제18권3호
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• pp.436-439
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• 1985

A patient of Ebstein`s anomaly underwent surgical repair on Oct. 24th, 1984. Tricuspid valve was replaced by 31mm St. Jude mechanical valve without plication of atrialized right ventricle. The annulus has been placed below the coronary sinus, with care not to damage the conduction system. But postoperatively complete heart block developed. Permanent pacemaker was implanted on his 12th POD. Now he has been followed up for 9 months. There was no hemodynamic problems yet.

• Journal of Chest Surgery
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• 제23권1호
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• pp.205-212
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• 1990

A 17 year old female patient with Ebstein`s anomaly received surgical treatment for WPW syndrome and AV nodal reentrant supraventricular tachycardia[SVT] Electrophysiologic study revealed that an anomalous pathway was located in the right posterolateral portion and antegrade dual AV nodal pathway responsible for AV nodal reentrant tachycardia. The patient was underwent surgery on February 18, 1987. Intraoperative mapping was used to define the location of accessory pathway. The accessory pathway was cryoablated through the epicardium. Simultaneously discrete cryoablation around the perinodal area was performed to prevent AV nodal reentrant SVT. The atrialized right ventricle of Ebstein`s anomaly was plicated with 11 pledget mattress sutures under the cardiopulmonary bypass. Two and half years after surgery, the patient has no evidence of WPW syndrome or supraventricular tachycardia.