• Annals of Clinical Neurophysiology
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• v.24 no.2
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• pp.90-92
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• 2022

AGel amyloidosis is an autosomal dominantly inherited disease caused by a GSN mutation, and affected patients typically present with the clinical triad of corneal lattice dystrophy, progressive cranial neuropathy, and cutis laxa. We report a Korean family with AGel amyloidosis with predominant manifestations of facial and bulbar muscle weakness. Whole-exome sequencing revealed a common missense mutation (p.Asp214Tyr) in GSN. This case strongly suggests that AGel amyloidosis should be considered when a patient presents with progressive facial and bulbar palsies.

• Korea journal of population studies
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• v.22 no.2
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• pp.163-195
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• 1999

이 글은 '강력한 남성 부양자'국가로서 90년대 일본사회가 제시한 여성노동력에 대한 사회적 보호정책을 살펴보고 평가하는데 그 목적이 있다. 논의의 초점은 크게 3가지로 구분되는데 어머니로서는 보육정책을, 노동자로서는 노동정책을, 부인으로서는 사회보장 정책에 대한 논의가 그것이다. 보육정책의 경우 급격한 소자녀와 추세에 따라서 94년에 도입된 "엔젤 플랜"의 성격을 소개하였다. 노동정책은 99년 4월 실시된 개정 '노기법', 균등법', 휴업법' 내용을 다루었다. 정책내용에 담겨 있는 성이 여성의 규정방식을 평가하였다. 90년대 이후 지속되는 일본경제의 장기 불황 그리고 전세계적으로 도입되고 있는 신자유주의적 사조는, 90년대 이루어진 여성노동력에 대한 사회적 보호정책 개정의 효과를 반감시키는 요인으로 작용할 수 있다. 즉, 최근 개정된 일련의 여성노동력에 대한 사회적 보호정책의 기조는 '강력한 남성부양자' 국가인 일본사회의 남성 중심성을 수정 보완하기에는 역부족으로 보인다.

• Journal of the Korean Electrochemical Society
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• v.5 no.4
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• pp.212-215
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• 2002

A superoxide dismutase (SOD)-based superoxide ion $(O_2^-)$ sensor was fabricated by immobilizing SOD on a self-assembled monolayer (SAM) of 3-mercaptopropionic acid (MPA) which was prepared on a gold electrode. The SAM of MPA was found to function as an effective promoter for the electrode reaction of SOD. The amperometric response to $(O_2^-)$ was monitored at 300mV and -100mV vs. Ag/ Agel in 5mM phosphate buffer solution containing $KO_2$. The sensor was proved to have a high sensitivity, selectivity and short response time (<5 s) and negligible interference.

• Koreanishche Zeitschrift fur Deutsche Sprachwissenschaft
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• v.1
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• pp.91-118
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• 1999

Die vorliegende Arbeit behandelt ein zweidimensionales Valenzmodell. In diesem Modell wurde der Versuch unternommen, durch Beruck­sichtigung $valenzunabh\"{a}ngiger$ Faktoren die bisherige eindimensionale Valenzkonzeption zu $\"{u}berwinden\;und\;f\"{u}r\;Problemf\"{a}lle$ der Valenz­forschung angemessenere $Erkl\"{a}rungen$ zu bieten. Dabei wurde mit Agel (1994) davon ausgegangen, $da\ss$ man zwischen Valenzpotenz und Valenzrealisierung unterscheiden sollte. Zwischen den beiden Ebenen besteht keine Isomorphie. Auf der Ebene der Valenz­potenz spreche ich von valenzgebundenen und valenzfreien Gliedern, auf der Ebene der Valenzrealisierung dagegen von notwendigen und optional en Gliedern. Somit ergeben sich insgesamt vier $M\"{o}glichkeiten:$ 1. valenzgebunden und notwendig; 2. valenzgebunden und optional; 3. valenzfrei und notwendig; 4. valenzfrei und optional. Viele $Problemf\"{a}lle$ der bisherigen Valenzforschung $geh\"{o}ren$ zu dem zweiten und dem dritten Typ. Erst die Annahme des zweidimensionalen Valenzmodells bietet $daf\"{u}r\;systematische\;Erkl\"{a}rungen$. Anhand verschiedener Beispiele wurde gezeigt, $da\ss$ syntaktische, semantische, pragmatische und konzeptuelle Faktoren die Valenzrealisierung beeinflussen. Valenzrealisierung ist somit nicht als $blo{\ss}e$ Wiedergabe der im Lexikon immanenten Valenzpotenz anzusehen. $Schlie{\ss}lich$ wurde am Beispiel yon gehen das $Verh\"{a}ltnis$ zwischen Valenzpotenz, konzeptuellen Prozessen und Valenzrealisierung dargestellt: Die Realisierung der eigentlich valenzgebundenen lokalen Adverbial­bestimmung $h\"{a}ngt$ eng mit den konzeptuellen Prozessen ($Lokalisierungs-proze{\ss}\;vs.\;Delokalisierungsproze{\ss}$) zusammen. Falls $Lokalisierungs-proze{\ss}$ stattfindet, ist die Realisietung der lokalen Adverbialbestimmung notwendig, um die Direktionalisierung des Verweisobjekts im Hinblick auf das Bezugsobjekt zu bezeichnen. Bei $Delokalisierungsproze\ss$ ist die Realisierung der lokalen Adverbialbestimung dagegen optional.

• Journal of the Society of Disaster Information
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• v.9 no.4
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• pp.449-461
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• 2013

As the hydrofluoric acid leak in Gumi-si, Gyeongsangbuk-do or hydrochloric acid leak in Ulsan, Gyeongsangnam-do demonstrated, chemical related accidents are mostly caused by large amounts of volatile toxic substances leaking due to the damages of storage tank or pipe lines of transporter. Safety assessment is the most important concern because such toxic material accidents cause human and material damages to the environment and atmosphere of the surrounding area. Therefore, in this study, a hydrofluoric acid leaked from a storage tank was selected as the study example to simulate the leaked substance diffusing into the atmosphere and result analysis was performed through the numerical Analysis and diffusion simulation of ALOHA(Areal Location of Hazardous Atmospheres). the results of a qualitative evaluation of HAZOP (Hazard Operability)was looked at to find that the flange leak, operation delay due to leakage of the valve and the hose, and toxic gas leak were danger factors. Possibility of fire from temperature, pressure and corrosion, nitrogen supply overpressure and toxic leak from internal corrosion of tank or pipe joints were also found to be high. ALOHA resulting effects were a little different depending on the input data of Dense Gas Model, however, the wind direction and speed, rather than atmospheric stability, played bigger role. Higher wind speed affected the diffusion of contaminant. In term of the diffusion concentration, both liquid and gas leaks resulted in almost the same $LC_{50}$ and ALOHA AEGL-3(Acute Exposure Guidline Level) values. Each scenarios showed almost identical results in ALOHA model. Therefore, a buffer distance of toxic gas can be determined by comparing the numerical analysis and the diffusion concentration to the IDLH(Immediately Dangerous to Life and Health). Such study will help perform the risk assessment of toxic leak more efficiently and be utilized in establishing community emergency response system properly.