• Title/Summary/Keyword: 혈관성 기형

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A Modified Technique in Surgical Correction of Ebstein Anomaly (Ebstein 기형 교정의 변형 술식)

  • 윤석원;윤태진;박정준;서동민
    • Journal of Chest Surgery
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    • v.35 no.11
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    • pp.817-821
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    • 2002
  • There are various surgical techniques in repairing Ebstein anomaly, but residual tricuspid regurgitation and compromized right heart function may ensue in some cases. We report our clinical experience of Ebstein anomaly and atrial flutter in a 19-year-old male patient who underwent simple modified tricuspid annuloplasty, hi-directional cavopulmonary shunt and cryoablation of cavotricuspid isthmus.

Cone Reconstruction for Tricuspid Valve Repair in a Patient with Ebstein's Anomaly - A case report - (Cone 재건술을 이용한 엡스타인 기형의 삼첨판막 성형술 - 1예 보고 -)

  • Lee, Cheul;Kwak, Jae-Gun;Lee, Chang-Ha
    • Journal of Chest Surgery
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    • v.42 no.4
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    • pp.509-512
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    • 2009
  • Ebstein's anomaly is a complex congenital defect of the tricuspid valve and right ventricle. Various surgical methods to repair the regurgitant tricuspid valve have been reported, and most of them depend on monocuspidalization with using the anterior leaflet. We report here on our first experience with Ebstein's anomaly in a 31-year-old female patient who underwent cone reconstruction of the tricuspid valve with using three leaflets.

Congenital Cardiac Anomaly Combined with the VATER Association - A case report - (VATER 증후군에 동반된 선천성 심장기형 치험 1례)

  • Ban, Dong-Gyu;Kim, Hyuck;Jee, Heng-Ok;Chung, Won-Sang;Kang, Jung-Ho;Kim, Young-Hak;Lee, Chul-Bum;Ham, Shi-Young;Kim, Nam-Su
    • Journal of Chest Surgery
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    • v.34 no.11
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    • pp.858-860
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    • 2001
  • VATER is a complex anomaly of multiple organs and often combined with cardiac anomalies. However, it can be cured with active surgical intervention. We achieved successful result with aggressive surgery in the patient with VATER and report it with references.

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Animal Experiments of Heart Transplantation for Complicated Congenital Heart Disease in Neonate (신생아의 복잡심장기형에서 심장이식을 위한 동물실험)

  • 박영환;윤치순;정원석;김명옥;조범구
    • Journal of Chest Surgery
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    • v.32 no.6
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    • pp.504-509
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    • 1999
  • Background: Heart transplantation is considerated for a selected certain group of complicated congenital heart disease in neonates because corrective surgery is very difficult and has high mortality. Precise planning of transplantation is necessary to adequately fit the donor heart to the recipient. Material and Method: We have performed 4 neonatal pig heart transplantations to test the technical feasibility. Experiment 1: The transplantation was performed using the same technique as the adult heart transplantation. Experiment 2: The transplantation for hypoplastic left heart syndrome was simulated as we reconstructed the whole aortic arch with donor aorta. Experiment 3: The heart transplantation was done with radical pulmonary artery reconstruction. Experiment 4: The experiment was performed for a long term survival. Result: Preoperative planning was very important for adequate fitting. All animals could be weaned from cardiopulmonary bypass, however, two animals died due to bleeding at pulmonary artery and left atrium. Conclusion: We concluded that the neonatal heart transplantation can be applied in some complicated Further using animal model is mandatory.

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Pictorial Essay: Understanding of Persistent Left Superior Vena Cava and Its Differential Diagnosis (임상화보: 지속성 좌측상대정맥의 이해와 감별 진단)

  • Eo Ram Jeong;Eun-Ju Kang;Joo Hee Jeun
    • Journal of the Korean Society of Radiology
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    • v.83 no.4
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    • pp.846-860
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    • 2022
  • Persistent left superior vena cava (PLSVC) is a rare congenital, thoracic, and vascular anomaly. Although PLSVCs generally do not have a hemodynamic effect, several types of PLSVC and some cardiac anomalies may manifest with clinical symptoms. The presence of PLSVC can render catheterization via left subclavian access difficult when placing a pacemaker or central venous catheter. As such, recognizing a PLSVC that is typically incidentally discovered can prevent complications such as vascular injury. Differentiating vessels found in a similar location as PLSVC is necessary when performing thoracic vascular procedures. This pictorial essay explains the multi-detector CT findings of a PLSVC, and provides a summary of other blood vessels that require differentiation during thoracic vascular procedures.

Congenital Cystic Adenomatoid Malformation Associated with Extralobar Pulmonary Sequestration - A case report - (외엽형 폐격리증을 동반한 선천성 낭종성 신종양 기형 - 1례 보고 -)

  • Lee, Jae-Kwang;Kweon, Jong-Bum;Park, Kuhn;Kwack, Moon-Sub;Sim, Sung-Bo
    • Journal of Chest Surgery
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    • v.33 no.7
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    • pp.594-596
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    • 2000
  • Congenital cystic adenomatoid malformation and Extralobar Pulmonary sequestration are very rare congenital anomalies. We experienced a 4 year-old female patient who had Congenital cystic adenomatoid malformation in her lower lobe of left lung. We accidently found extralobar pulmonary sequestration associated with Congenital cystic adenomatoid malformation at operation field. The resection of the left lower lobe and the extralobar pulmonary sequestration were performed. The arterial supply of the extralobar pulmonary sequestration was one anomalous artery arised from the thoracic aorta. The Venous drainage of expralobar pulmonary sequestration was intercostal vein into the azygous vein. The patient was discharged without any problem.

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Benign Mediastinal Cystic Teratoma Complicated by Cardiac Tamponade due to Trauma (외상에 의하여 심장눌림증을 유발한 종격동 양성낭기형종)

  • Choe Ju-Won;Kim Yong-In
    • Journal of Chest Surgery
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    • v.39 no.9 s.266
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    • pp.729-732
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    • 2006
  • Mediastinal teratoma is one of the most common lesions found in the anterior mediastinum, accounting for $8\sim13%$ of all mediastinal tumors. This tumor is incidentally detected by routine chest roentgengography, but pericardial perforation or pleural effusion occurs rarely. In our patient cardiac tamponade was developed due to anterior chest wall contusion, we confirmed the anterior mediastinal tumor. Vital signs were stabilized after the pericardiocentesis, and the patient underwent the tumor resection in the anterior mediastinum for a definite treatment. On histologic examination, the tumor revealed cystic structures composed of mature squamous epithelium, pilosebaceous glands, mature fat tissue, gastrointestinal mucosa, respiratory epithelium, and pancreatic tissues.

Esophageal Plexiform Schwannoma -A case report- (식도 얼기형 신경집종 -1예 보고-)

  • Jang, Jae-Seok;Park, Ki-Sung
    • Journal of Chest Surgery
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    • v.39 no.11 s.268
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    • pp.875-878
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    • 2006
  • A 39-year-old man presented with a esophageal submucosal tumor on regular check up examination. Preoperative exams showed the typical submucosal tumor as leiomyoma and operative procedure was enucleation for complete resection. Postoperative pathologic diagnosis including histologic and immunohistochemical study was compatible with plexiform schwannoma. Plexiform schwannoma is one of the least common variant of schwannoma that typically shows a plexiform or multinodular pattern. To our knowledge, there is rare case report of plexiform schwannoma originating in the esophagus and we report ore case with related literature.

Experimental Study for the Teratogenic Effect of Gamma-ray on the Heart of Chick Embryo (계태에서 감마선 조사에 의한 심장기형 발생에 관한 실험적 연구)

  • Jo, Yong Whan;Kim, Nam Su;Moon, Sung Yup;Yum, Myeng Gul;Kim, Sung Hoon;Chun, Ha Chung;Kim, Yong Joo;Lee, Hahng
    • Clinical and Experimental Pediatrics
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    • v.46 no.6
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    • pp.554-560
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    • 2003
  • Purpose : To investigate the teratogenic effect of gamma-ray on the heart of chick embryo. Methods : 50 rad, 100 rad, 150 rad, 200 rad, 250 rad, and 300 rad of gamma-ray were used to irradiate three days old chick embryos. The control group was not irradiated. After three weeks, the embryos were sacrificed and examined for cardiovascular malformation. Results : The survival rate of the gamma-ray irradiated group was significantly lower than that of the control group(33.3-63.3% vs 76.4%, P=0.001). The cardiac malformation rate of the experimental group was 11.0%. In the control group, no congenital cardiac malformations were observed. The experimental groups had a significantly higher malformation rate(P=0.001). The types of malformation were ventricular septal defect, tricuspid atresia, Ebstein anomaly and aortic arch anomaly. In the gamma-ray irradiated group, the cardiac malformations were : 14 small ventricular septal defects (VSDs), five large VSDs, two tricuspid atresias, and one Ebstein anomaly. The higher the dose of radiation applied, the higher the incidence of cardiac malformation was noted. Conclusion : Gamma-ray irradiation of 3 days old chick embryos increased the rate of death and the rate of cardiac malformation significantly.