Pediatric Gastroenterology, Hepatology & Nutrition

  • 제27권4호
  • /
  • Pages.197-205
  • /
  • 2024
  • /
  • 2234-8646(pISSN)
  • /
  • 2234-8840(eISSN)
대한소아소화기영양학회 (The Korean Society of Pediatric Gastroenterology, Hepatology and Nutrition)
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Time is Gut. Approaching Intestinal Leiomyositis: Case Presentation and Literature Review

  • Michail Aftzoglou (Department of Pediatric Surgery, Altona Children's Hospital) ;
  • Christina Heinrich (Department of Pediatric Gastroenterology, Altona Children's Hospital) ;
  • Till Sebastian Clauditz (Department of Pathology, University Medical Center Hamburg Eppendorf) ;
  • Thomas Menter (Department of Pathology, University Hospital Basel) ;
  • Deborah Dorth (Department of Pediatric Surgery, Altona Children's Hospital) ;
  • Konrad Reinshagen (Department of Pediatric Surgery, Altona Children's Hospital) ;
  • Ingo Konigs (Department of Pediatric Surgery, Altona Children's Hospital)
  • 투고 : 2023.12.31
  • 심사 : 2024.03.24
  • 발행 : 2024.07.15
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초록

T-lymphocytic intestinal leiomyositis is a rare cause of "pediatric intestinal pseudo-obstructions." Diagnosis may be difficult and requires full-thickness bowel biopsies during laparotomy or laparoscopy with possible enterostomy. Currently, immunosuppressive therapy is the only available treatment. A delay in diagnosis and therapy may negatively affect the prognosis because of ongoing fibrotic alterations; therefore, early diagnosis and consequent treatment are crucial. This review summarizes the available information on the nosology, diagnostic steps, and treatment modalities. Here, we report the youngest case of enteric leiomyositis reported in the last two decades and analyze its management by reviewing previous cases.

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참고문헌

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