Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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Cone Repair in Adult Patients with Ebstein Anomaly

  • Lee, Chang-Ha (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital) ;
  • Lim, Jae Hong (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital) ;
  • Kim, Eung Rae (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital) ;
  • Kim, Yong Jin (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital)
  • Received : 2020.09.01
  • Accepted : 2020.09.02
  • Published : 2020.10.30
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Abstract

Ebstein anomaly is a rare congenital heart malformation typically involving the tricuspid valve and the right ventricle that has a wide range of anatomical and pathophysiological presentations. Various surgical repair techniques for Ebstein anomaly have been reported because of its near-infinite anatomical variability. Cone repair for Ebstein anomaly can achieve nearly anatomical reconstruction of the tricuspid valve with promising outcomes. In this article, the surgical techniques for cone repair in adult patients with Ebstein anomaly are described in detail, and clinical experiences and technically challenging cases are presented.

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References

  1. Attenhofer Jost CH, Connolly HM, Dearani JA, Edwards WD, Danielson GK. Ebstein's anomaly. Circulation 2007;115:277-85. https://doi.org/10.1161/CIRCULATIONAHA.106.619338
  2. Dearani JA, Mora BN, Nelson TJ, Haile DT, O'Leary PW. Ebstein anomaly review: what's now, what's next? Expert Rev Cardiovasc Ther 2015;13:1101-9. https://doi.org/10.1586/14779072.2015.1087849
  3. Danielson GK, Fuster V. Surgical repair of Ebstein's anomaly. Ann Surg 1982;196:499-504. https://doi.org/10.1097/00000658-198210000-00014
  4. Carpentier A, Chauvaud S, Mace L, et al. A new reconstructive operation for Ebstein's anomaly of the tricuspid valve. J Thorac Cardiovasc Surg 1988;96:92-101. https://doi.org/10.1016/S0022-5223(19)35302-4
  5. Hetzer R, Nagdyman N, Ewert P, et al. A modified repair technique for tricuspid incompetence in Ebstein's anomaly. J Thorac Cardiovasc Surg 1998;115:857-68. https://doi.org/10.1016/S0022-5223(98)70367-8
  6. Da Silva JP, Baumgratz JF, da Fonseca L, et al. The cone reconstruction of the tricuspid valve in Ebstein's anomaly: the operation: early and midterm results. J Thorac Cardiovasc Surg 2007;133:215-23. https://doi.org/10.1016/j.jtcvs.2006.09.018
  7. Da Silva JP, da Silva Lda F. Ebstein's anomaly of the tricuspid valve: the cone repair. Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2012;15:38-45. https://doi.org/10.1053/j.pcsu.2012.01.008
  8. Ibrahim M, Tsang VT, Caruana M, et al. Cone reconstruction for Ebstein's anomaly: patient outcomes, biventricular function, and cardiopulmonary exercise capacity. J Thorac Cardiovasc Surg 2015;149:1144-50. https://doi.org/10.1016/j.jtcvs.2014.12.074
  9. Lange R, Burri M, Eschenbach LK, et al. Da Silva's cone repair for Ebstein's anomaly: effect on right ventricular size and function. Eur J Cardiothorac Surg 2015;48:316-21. https://doi.org/10.1093/ejcts/ezu472
  10. Belli E, Rabot M, Petit J, Gouton M. Ebstein's anomaly in adults: modified cone reconstruction of the tricuspid valve is associated with promising outcomes. Arch Cardiovasc Dis 2017;110:325-33. https://doi.org/10.1016/j.acvd.2017.03.003
  11. Holst KA, Dearani JA, Said S, et al. Improving results of surgery for Ebstein Anomaly: where are we after 235 cone repairs? Ann Thorac Surg 2018;105:160-8. https://doi.org/10.1016/j.athoracsur.2017.09.058
  12. Schreiber C, Cook A, Ho SY, Augustin N, Anderson RH. Morphologic spectrum of Ebstein's malformation: revisitation relative to surgical repair. J Thorac Cardiovasc Surg 1999;117:148-55. https://doi.org/10.1016/S0022-5223(99)70480-0
  13. Hetzer R, Hacke P, Javier M, et al. The long-term impact of various techniques for tricuspid repair in Ebstein's anomaly. J Thorac Cardiovasc Surg 2015;150:1212-9. https://doi.org/10.1016/j.jtcvs.2015.08.036
  14. Dearani JA, Said SM, O'Leary PW, Burkhart HM, Barnes RD, Cetta F. Anatomic repair of Ebstein's malformation: lessons learned with cone reconstruction. Ann Thorac Surg 2013;95:220-8. https://doi.org/10.1016/j.athoracsur.2012.04.146