The Korean Journal of Medicine

  • 제86권4호
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  • Pages.500-504
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  • 2014
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  • 1738-9364(pISSN)
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  • 2289-0769(eISSN)
대한내과학회 (The Korean Association of Internal Medicine)
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선천성 낭성 선종양 기형에서 발견된 악성 변화 1예

A Case of Malignant Transformation in a Congenital Cystic Adenomatoid Malformation

  • 최재우 (충남대학교 의학전문대학원 내과학교실) ;
  • 송승택 (충남대학교 의학전문대학원 내과학교실) ;
  • 박연희 (충남대학교 의학전문대학원 내과학교실) ;
  • 박동일 (충남대학교 의학전문대학원 내과학교실) ;
  • 정재욱 (충남대학교 의학전문대학원 내과학교실) ;
  • 이충식 (충남대학교 의학전문대학원 병리학교실) ;
  • 정성수 (충남대학교 의학전문대학원 내과학교실)
  • Choi, Jae Woo (Department of Internal Medicine, Chungnam National University School of Medicine) ;
  • Song, Seung Taek (Department of Internal Medicine, Chungnam National University School of Medicine) ;
  • Park, Yeon Hee (Department of Internal Medicine, Chungnam National University School of Medicine) ;
  • Park, Dong Il (Department of Internal Medicine, Chungnam National University School of Medicine) ;
  • Chung, Chae Uk (Department of Internal Medicine, Chungnam National University School of Medicine) ;
  • Lee, Choong Sik (Department of Pathology, Chungnam National University School of Medicine) ;
  • Jung, Sung Soo (Department of Internal Medicine, Chungnam National University School of Medicine)
  • 투고 : 2013.08.19
  • 심사 : 2013.10.16
  • 발행 : 2014.04.01
⟨ 이전 논문 다음 논문 ⟩

초록

폐에서 발생한 CCAM은 전형적으로 신생아에서 나타나는 드문 선천성 기형이다. 성인에서는 type I CCAM이 다른 호흡기 이상들과 관련하여 극히 드물게 보고되고 있다. 하지만 만성 기침과 같이 서서히 발생하는 증상들이 있거나 영상의학검사에서 낭종 병터가 있는 경우에는 악성 변형 가능성이 있는 선천성 이상 병터일 수 있기 때문에 추가적인 검사가 필요하다. 이러한 병터의 진단과 치료를 위해서 전산화 단층촬영과 수술적 생검이 고려되어야 한다. 저자들은 수술적 절제한 CCAM에서 국내 처음으로 악성 변형을 관찰하였기에 문헌고찰과 함께 보고하는 바이다.

Congenital cystic adenomatoid malformation (CCAM) of the lung is a rare condition with the potential for malignant transformation. Several cases that presented with malignant changes have been reported worldwide. However, no report about a malignant transformation case in a CCAM in Korea has been published. We report the first patient who had a malignant change in a CCAM. A 32-year-old female underwent a bilobectomy for a cystic lung lesion that was a type 1 CCAM associated with malignant transformation. A biopsy specimen from the resected cystic lesion showed foci of adenocarcinoma.

키워드

참고문헌

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