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베체트병 환자에서 질병 활성도 증가로 오인된 갈색세포종 1예

A Case of Pheochromocytoma Misdiagnosed as Activation of Behcet's Disease

  • 김용준 (동아대학교 의과대학 내과학교실 류마티스 내과) ;
  • 이상엽 (동아대학교 의과대학 내과학교실 류마티스 내과)
  • Kim, Yong Jun (Division of Rheumatology, Department of Internal Medicine, Dong-A University College of Medicine) ;
  • Lee, Sang Yeob (Division of Rheumatology, Department of Internal Medicine, Dong-A University College of Medicine)
  • 투고 : 2013.01.28
  • 심사 : 2013.05.10
  • 발행 : 2013.09.01

초록

저자들은 베체트병에 동반된 갈색세포종 1예를 경험하였고 국내에 베체트병과 갈색세포종이 동반된 예는 보고된 적이 없다. 특히 베체트병에서 동반되는 심-뇌혈관계 증상 활성화와 갈색세포종의 임상 증상이 유사하므로 이를 간과하여 치명적인 결과를 초래할 수 있다는 점에서 임상적 중요성이 있다고 생각한다.

A 30 year-old woman with a history of Behcet's disease was admitted to our clinic because of a paroxysmal attack of palpitations, headache, and ocular pain. Initially, we did not suspect a pheochromocytoma. We evaluated Behcet's disease activity because the cardiovascular and neurological symptoms mimicked those of Behcet's disease. Pheochromocytoma is often overlooked and can be fatal if not recognized and treated appropriately. In the present case, abdominal computerized tomography incidentally revealed a mass confirmed to be a pheochromocytoma in the left adrenal gland, and the tumor was successfully removed. This is the first Korean report of a pheochromocytoma in a patient with Behcet's disease. We suggest that pheochromocytoma should be included in the differential diagnosis of Behcet's disease if a patient presents with cardiovascular or neurological symptoms.

키워드

참고문헌

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피인용 문헌

  1. Rare association of aortoarteritis and pheochromocytoma: A case report vol.77, pp.None, 2013, https://doi.org/10.1016/j.ijscr.2020.10.048