부신수질증식증이 동반된 알도스테론 분비 부신피질선종 1예

An Adrenal Cortical Adenoma with Adrenal Medullary Hyperplasia

  • 이향선 (연세대학교 원주의과대학 내분비내과학교실) ;
  • 김건우 (연세대학교 원주의과대학 내분비내과학교실) ;
  • 김재현 (연세대학교 원주의과대학 내분비내과학교실) ;
  • 이미영 (연세대학교 원주의과대학 내분비내과학교실) ;
  • 엄민섭 (연세대학교 원주의과대학 병리학교실) ;
  • 신영구 (연세대학교 원주의과대학 내분비내과학교실) ;
  • 정춘희 (연세대학교 원주의과대학 내분비내과학교실)
  • Lee, Hyang-Sun (Department of Internal Medicine, Yonsei University Wonju College of Medicine) ;
  • Kim, Gun-Woo (Department of Internal Medicine, Yonsei University Wonju College of Medicine) ;
  • Kim, Jae-Hyun (Department of Internal Medicine, Yonsei University Wonju College of Medicine) ;
  • Lee, Mi-Young (Department of Internal Medicine, Yonsei University Wonju College of Medicine) ;
  • Eum, Min-Sub (Department of Pathology, Yonsei University Wonju College of Medicine) ;
  • Shin, Young-Goo (Department of Internal Medicine, Yonsei University Wonju College of Medicine) ;
  • Chung, Choon-Hee (Department of Internal Medicine, Yonsei University Wonju College of Medicine)
  • 발행 : 2011.09.01

초록

부신피질과 수질은 서로 다른 기원과 기능을 가지고 있으나 드물게 혼합된 임상소견을 보이는 경우가 보고되고 있다. 저자 등은 갈색세포종의 증상을 보여 시행한 호르몬 검사상 알도스테론 분비 부신피질선종의 소견을 보인 환자에서 수술 후 병리 조직 소견상 부신피질선종과 부신수질증식증이 동반된 드문 경우가 있어 문헌고찰과 함께 국내에서 처음으로 보고하는 바이다.

The relationship between the adrenal cortex and medulla has been studied since the 1960s. Rarely, a patient with an adrenal cortical adenoma presents with the findings of pheochromocytoma. However, there has been no report of a case with the clinical features of pheochromocytoma showing the pathological features of an adrenal cortical adenoma with medullary hyperplasia on histological examination. We report a 59-year-old-man who was shown to have an adrenal cortical adenoma, with medullary hyperplasia, during a diagnostic work up for pheochromocytoma.

키워드

참고문헌

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