The Korean Journal of Medicine

  • 제81권2호
  • /
  • Pages.273-278
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  • 2011
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  • 1738-9364(pISSN)
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  • 2289-0769(eISSN)
대한내과학회 (The Korean Association of Internal Medicine)
권호 표지

다발신경병증과 근위축을 동반한 쇼그렌 증후군 1예

A Case of Sensorimotor Polyneuropathy in a Patient with Sjogren's Syndrome

  • 김은정 (조선대학교 의과대학 내과학교실) ;
  • 이희정 (조선대학교 의과대학 내과학교실) ;
  • 정유진 (조선대학교 의과대학 내과학교실) ;
  • 홍수진 (조선대학교 의과대학 내과학교실) ;
  • 김윤성 (조선대학교 의과대학 내과학교실) ;
  • 김현숙 (조선대학교 의과대학 내과학교실)
  • Kim, Eun-Jeong (Department of Internal Medicine, College of Medicine, Chosun University) ;
  • Lee, Hee-Jeong (Department of Internal Medicine, College of Medicine, Chosun University) ;
  • Jeong, Yu-Jin (Department of Internal Medicine, College of Medicine, Chosun University) ;
  • Hong, Su-Jin (Department of Internal Medicine, College of Medicine, Chosun University) ;
  • Kim, Yun-Sung (Department of Internal Medicine, College of Medicine, Chosun University) ;
  • Kim, Hyun-Sook (Department of Internal Medicine, College of Medicine, Chosun University)
  • 발행 : 2011.08.01
⟨ 이전 논문 다음 논문 ⟩

초록

근력약화와 따끔거림을 주소로 내원한 환자에서 일차성 쇼그렌 증후군에서 병발한 다발신경병증을 진단하고 고용량 스테로이드 치료 및 면역억제제 치료하며 경과관찰 중 근위축까지 진행된 1예를 경험하였기에 문헌고찰과 함께 증례 보고하는 바이다.

Sjogren's syndrome is a chronic inflammatory disorder characterized by lymphocytic infiltration of the exocrine glands, especially the lacrimal and salivary glands. Although it is characterized primarily by a particular form of dry eyes (keratoconjunctivitis sicca) and a dry mouth (xerostomia), this condition may affect a wide variety of organ systems, including the skin, lungs, heart, and kidneys, and it may rarely have neurological manifestations. The peripheral neuropathy results from nerve damage due to vasculitis or nerve sheath demyelination, which adversely affects the ability of nerves to send messages. We report the case of a 71-year-old woman who presented with polyneuropathy of the lower limbs that was diagnosed as Sjogren's syndrome but progressed to muscle atrophy during her treatment.

키워드

참고문헌

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