비장경색이 동반된 베체트병 1예

A Case of Behcet's Disease with Splenic Infarction

  • 정장한 (건양대학교 의과대학 류마티스내과학교실) ;
  • 강민규 (건양대학교 의과대학 류마티스내과학교실) ;
  • 이한나 (건양대학교 의과대학 류마티스내과학교실) ;
  • 권미혜 (건양대학교 의과대학 류마티스내과학교실) ;
  • 정청일 (건양대학교 의과대학 류마티스내과학교실)
  • Jung, Jang-Han (Division of Rheumatology, Department of Internal Medicine, Konyang University College of Medicine) ;
  • Kang, Min-Kyu (Division of Rheumatology, Department of Internal Medicine, Konyang University College of Medicine) ;
  • Lee, Han-Na (Division of Rheumatology, Department of Internal Medicine, Konyang University College of Medicine) ;
  • Kwon, Mi-Hye (Division of Rheumatology, Department of Internal Medicine, Konyang University College of Medicine) ;
  • Joung, Chung-Il (Division of Rheumatology, Department of Internal Medicine, Konyang University College of Medicine)
  • 발행 : 2011.07.01

초록

베체트병을 진단 받았거나, 의심되는 환자에서 왼쪽 옆구리 통증이 동반될 경우, 혈전성 혈관염에 동반된 비장 경색을 감별해야 하겠다.

Behcet's disease is a multisystem autoimmune disease with vasculitic features, and major vascular involvement occurs in 7.7-60% of patients. Venous lesions are more common than arterial lesions and arterial thrombotic events are relatively rare. We report a patient with Behcet's disease who developed a splenic infarct associated with splenic thrombotic arteritis. A 44-year-old man who had been diagnosed with Behcet's disease 5 years earlier presented with left flank pain lasting for 5 days. Laboratory tests revealed an elevated erythrocyte sedimentation rate (ESR) and C-reactive protein (CRP). Computed tomography (CT) and three-dimensional CT showed a wedge-shaped splenic infarct and thrombus in the splenic artery. We treated him with low-molecular-weight heparin and prednisolone. The symptoms improved within 6 days of hospitalization, after which we stopped the heparin and added methotrexate and azathioprine. Splenic infarct should be ruled out if patients with Behcet's disease complain of new left-sided abdominal pain.

키워드

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