The Journal of Korea Assosiation for Disability and Oral Health (대한장애인치과학회지)

Korean Association for Disability and Oral Health (대한장애인치과학회)
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VITAMIN D-RESISTANT RICKETS : A CASE REPORT

비타민 D 저항성 구루병 환아의 치험례

  • Kim, So-Jung (Department of Pediatric Dentistry and Institute of Oral Biology, School of Dentistry, Kyung Hee University) ;
  • Park, Jae-Hong (Department of Pediatric Dentistry and Institute of Oral Biology, School of Dentistry, Kyung Hee University) ;
  • Kim, Kwang-Chul (Department of Pediatric Dentistry and Institute of Oral Biology, School of Dentistry, Kyung Hee University) ;
  • Choi, Sung-Chul (Department of Pediatric Dentistry and Institute of Oral Biology, School of Dentistry, Kyung Hee University)
  • 김소정 (경희대학교 소아치과학교실, 구강생물학 연구소) ;
  • 박재홍 (경희대학교 소아치과학교실, 구강생물학 연구소) ;
  • 김광철 (경희대학교 소아치과학교실, 구강생물학 연구소) ;
  • 최성철 (경희대학교 소아치과학교실, 구강생물학 연구소)
  • Received : 2010.05.26
  • Accepted : 2010.06.15
  • Published : 2010.06.30
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Abstract

Vitamin D-resistant rickets(VDRR) is hereditary disease manifesting marked hypophosphatemia caused by renal tubular loss of phosphate into urine and an associated decrease in the calcium and phosphorous ion product. VDRR is identified by clinical symptoms, such as in the limbs, gait disturbance, dwarfism, familial occurrence, bowlegs, and knock-knees, as well as by laboratory findings. Dental findings are enlarged chambers and extension of the pulp horns into the cusp tips in both the primary and the permanent dentition in contrast to the vitamin D-deficient rickets. The major oral manifestations are multiple spontaneous abscesses in a caries-free dentition. We reported the clinical features and treatment of a 6-year-old boy with vitamin D-resistant rickets referred to the department of pediatric dentistry in Kyung Hee University for multiple spontaneous periapical abscesses and gingival fistula without severe dental caries.

본 증례에서는 비타민 D 저항성 구루병으로 진단받았으며, 가족력이 있었고, 작은 키, 휜 다리 등의 전신적인 증상을 보이는 환아의 구강 증상과 치료를 보고하였다. 특징적으로 구강 내에 심한 우식이 없는 치아에 다발성 치은 농양이 관찰되었고, 방사선학적으로 유치와 영구치에서 상아법랑경계까지 길게 뻗은 치수각, 얇은 상아질 및 확장된 치수 강이 관찰되었다. 이러한 비타민 D 저항성 구루병 환아에게는 치수 절제술 및 기성 금관 수복뿐만 아니라 더욱 더 적극적인 예방치료와 주기적인 검사가 필요할 것으로 사료된다.

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