Nuclear Medicine and Molecular Imaging

The Korean Society of Nuclear Medicine (대한핵의학회)
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A Giant Hepatic Hemangioma Complicated by Kasabach-Merritt Syndrome: Findings of Tc-99m RBC Scintigraphy and SPECT Including a Total Body Blood Pool Imaging Study

Kasabach-Merritt 증후군을 동반한 거대 간 혈관종: Tc-99m 적혈구 간 및 전신 혈액풀 신티그래피와 SPECT소견

  • Sohn, Myung-Hee (Department of Nuclear, Chonbuk National University Medical School) ;
  • Jeong, Hwan-Jeong (Department of Nuclear, Chonbuk National University Medical School) ;
  • Lim, Seok-Tae (Department of Nuclear, Chonbuk National University Medical School) ;
  • Kim, Dong-Wook (Department of Nuclear, Chonbuk National University Medical School) ;
  • Yim, Chang-Yeol (Department of Internal Medicine, Chonbuk National University Medical School)
  • 손명희 (전북대학교 의학전문대학원 핵의학교실) ;
  • 정환정 (전북대학교 의학전문대학원 핵의학교실) ;
  • 임석태 (전북대학교 의학전문대학원 핵의학교실) ;
  • 김동욱 (전북대학교 의학전문대학원 핵의학교실) ;
  • 임창열 (전북대학교 의학전문대학원 내과학교실)
  • Published : 2009.02.28
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Abstract

Kasabach-Merritt syndrome (KMS) consists of thrombocytopenia, microangiopathic hemolytic anemia, and localized consumption coagulopathy that develops within vascular hemangioma. This syndrome may also be associated with occult hemangiomas located at various sites. Tc-99m RBC scintigraphy and SPECT have proven to be reliable for confirming or excluding hemangioma. Total body blood pool imaging study during the scintigraphy also provides a means of screening for occult lesions. The authors report the case of a 29-year-old man who presented with a giant hepatic hemangioma complicated by KMS, and underwent Tc-99m RBC scintigraphy and SPECT including a total body blood pool imaging study.

Keywords

References

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