A Case of Demyelinating Polyneuropathy in Sj$\ddot{o}$gren's Syndrome

쇼그렌증후군에서 병발한 탈수초성 신경병증 1예

  • Ryu, Wi-Sun (Department of Neurology, Seoul National University College of Medicine) ;
  • Kim, Soo-Yeon (Department of Neurology, Seoul National University College of Medicine) ;
  • Kim, Sung-Min (Department of Neurology, Seoul National University College of Medicine) ;
  • Kim, Sung Hun (Department of Neurology, Kangwon National University College of Medicine) ;
  • Hong, Yoon-Ho (Department of Neurology, Seoul Boramae Hospital) ;
  • Sung, Jung-Joon (Department of Neurology, Seoul National University College of Medicine) ;
  • Lee, Kwang-Woo (Department of Neurology, Seoul National University College of Medicine)
  • 류위선 (서울대학교 의과대학 신경과학교실) ;
  • 김수연 (서울대학교 의과대학 신경과학교실) ;
  • 김성민 (서울대학교 의과대학 신경과학교실) ;
  • 김성훈 (강원대학교 의과대학 신경과학교실) ;
  • 홍윤호 (시립보라매병원 신경과) ;
  • 성정준 (서울대학교 의과대학 신경과학교실) ;
  • 이광우 (서울대학교 의과대학 신경과학교실)
  • Received : 2008.02.01
  • Accepted : 2008.05.10
  • Published : 2008.06.30

Abstract

Sj$\ddot{o}$gren's syndrome (SS) is an autoimmune disease characterized by keratoconjunctivitis sicca and xerostomia. About thirty percent of patients with Sj$\ddot{o}$gren's syndrome experience nervous system involvement such as myelopaty, optic neuropathy, and peripheral neuropathy. The most common pattern of peripheral nerve involvement is axonal polyneuropathy. We present a case of demyelinating polyneuropathy in a patient with Sj$\ddot{o}$gren's syndrome, which had been proven by electrophysiology and pathology.

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