Clinical and Experimental Pediatrics

The Korean Pediatric Society (대한소아청소년과학회)
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Coronary artery fistula associated with single coronary artery

단일관상동맥 동정맥루 1례

  • Kim, Seong Man (Department of Cardiology, College of Medicine, Inje University, Busan Paik Hosital) ;
  • Song, Min Seob (Department of Pediatrics, College of Medicine, Inje University, Busan Paik Hosital) ;
  • Cho, Kwang Hyun (Department of Cardiothoracic Surgery, College of Medicine, Inje University, Busan Paik Hosital) ;
  • Kim, Chul Ho (Department of Pediatrics, College of Medicine, Inje University, Busan Paik Hosital)
  • 김성만 (인제대학교 의과대학 심장내과학교실) ;
  • 송민섭 (인제대학교 의과대학 소아과학교실) ;
  • 조광현 (인제대학교 의과대학 흉부외과학교실) ;
  • 김철호 (인제대학교 의과대학 소아과학교실)
  • Received : 2008.06.06
  • Accepted : 2008.09.01
  • Published : 2008.10.15
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Abstract

A case of a single coronary artery complicated with a coronary artery fistula (CAF) to the right ventricle is extremely rare, and its management strategy and prognosis are not clear. A 5-year-old boy was hospitalized for evaluation of a continuous heart murmur. Transthoracic echocardiography suggested a CAF to the right ventricle, with an enlarged left coronary artery. Cardiac catheterization confirmed the CAF terminating at the right ventricle and the absence of a right coronary artery. The fistula was ligated at the right ventricular side under cardiopulmonary bypass. At follow-up 18 months later, the child was clinically asymptomatic, and coronary angiogram showed no recurrence of the fistula.

단일관상동맥에서 우심실로 유출되는 동정맥루는 보고가 매우 드물며 이 경우 치료 방침이나 예후에 대해 명확하지 않다. 저자들은 지속성심잡음이 들려 시행한 심초음파 검사상 단일 좌관상동맥이 확장되어 있으며 우심실로 유출되는 동정맥루를 진단하였으며 관상동맥조영술로 확진하였다. 체외순환하에 우심실에서 동정맥루를 결찰하였다. 18개월 후 추적시 증상은 없었고 관상동맥조영술상 동정맥루의 재발도 없었다.

Keywords

References

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