Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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A Case Report of Acute Type II Aortic Dissection in a Patient with Marfan's Syndrome and Who Was 24 Weeks Pregnant - A case report -

임신 24주 Marfan 증후군 환자에서의 급성 제II형 대동맥 박리 - 1예 보고 -

  • Hwang, Ui-Dong (Department of Thoracic ad Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Ryu, Yang-Gi (Department of Thoracic ad Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Lim, Ju-Yong (Department of Thoracic ad Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Chung, Cheol-Hyun (Department of Thoracic ad Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine)
  • 황의동 (울산대학교 의과대학 서울아산병원 흉부외과학교실) ;
  • 유양기 (울산대학교 의과대학 서울아산병원 흉부외과학교실) ;
  • 임주영 (울산대학교 의과대학 서울아산병원 흉부외과학교실) ;
  • 정철현 (울산대학교 의과대학 서울아산병원 흉부외과학교실)
  • Published : 2007.07.05
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Abstract

The causes of aortic dissection are usually hypertension, connective tissue disease such as Marfan syndrome, congenital valvular abnormality such as bicuspid aortic valve, iatrogenic injury, pregnancy and drugs. Previous studies have shown that 50% of all dissections in women less than 40 years age were associated with pregnancy. Almost all aortic dissections during pregnancy occur during the third trimester or during labor and delivery. Marfan's syndrome is a particularly important predisposing factor for aortic dissection during pregnancy. We report here on a case of surgical treatment for acute type II aortic dissection in a Marfan syndrome patient who was 24 weeks pregnant, and we include a review of literature.

일반적으로 대동맥 박리의 원인을 살펴보면 고혈압, Marfan 증후군과 같은 결체 조직성 질환, 이엽성 대동맥 판막과 같은 선천성 판막 질환, 침습적 시술, 임신, 마약 등 여러 가지이다. 이러한 대동맥 박리의 원인들 중 임신은 40세 이하 여성에서 나타나는 대동맥 박리 원인의 약 50%를 차지한다. 임신중의 대동맥 박리는 대부분 임신 제 3분기 또는 출산 중에 발생하고 이 중 약 반수에서 Marfan 증후군과 같은 결체 조직성 질환이 동반된다. 저자들은 임신 24주에 급성 제II형 대동맥 박리가 발생한 Marfan 증후군 환자에서 대동맥 판막을 포함한 상행 대동맥 치환술을 시행하고 추후 임신 38주에 제왕절개를 통해 건강한 태아를 출산한 치험 1예를 문헌 고찰과 함께 보고한다.

Keywords

References

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