Anomalous Origin of the Left Coronary Artery from the Pulmonary Artery in an Adult - A case report -

성인에서 발견된 좌관상동맥의 폐동맥 이상기시증 - 1예 보고 -

  • Kim, Keun-Woo (Department of Thoracic and Cardiovascular Surgey, Gil Medial Center, Gachon University of Medicine and Science) ;
  • Choi, Chang-Hyu (Department of Thoracic and Cardiovascular Surgey, Gil Medial Center, Gachon University of Medicine and Science) ;
  • Park, Chul-Hyun (Department of Thoracic and Cardiovascular Surgey, Gil Medial Center, Gachon University of Medicine and Science) ;
  • Jeon, Yang-Bin (Department of Thoracic and Cardiovascular Surgey, Gil Medial Center, Gachon University of Medicine and Science) ;
  • Lee, Jae-Ik (Department of Thoracic and Cardiovascular Surgey, Gil Medial Center, Gachon University of Medicine and Science) ;
  • Park, Kook-Yang (Department of Thoracic and Cardiovascular Surgey, Gil Medial Center, Gachon University of Medicine and Science)
  • 김건우 (가천의과학대학교 길병원 흉부외과) ;
  • 최창휴 (가천의과학대학교 길병원 흉부외과) ;
  • 박철현 (가천의과학대학교 길병원 흉부외과) ;
  • 전양빈 (가천의과학대학교 길병원 흉부외과) ;
  • 이재익 (가천의과학대학교 길병원 흉부외과) ;
  • 박국양 (가천의과학대학교 길병원 흉부외과)
  • Published : 2007.07.05

Abstract

Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) has rarely been reported on in adults because 90% of the untreated infants die in the first year of life. We report here on a case of AICAPA that was detected in a 41-year-old woman and she was successfully treated by direct re-implantation of the anomalous coronary artery into the aorta.

좌관상동맥-폐동맥 이상기시증(anomalous origin of the left coronary artery from pulmonary artery, ALCAPA)은 적절한 외과적 처치를 하지 않을 경우 90%에서 생후 1년 이내에 심근 허혈로 사망하므로, 성인에서 발견되는 경우는 매우 드물다. 저자들은 심부전 증상으로 내원한 41세 ALCAPA 환자 1예를 경험하였고, 직접 좌관상동맥-대동맥 이식술을 시행하여 좋은 결과를 얻었기에 이를 보고하는 바이다.

Keywords

References

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