Imprint Cytology of a Desmoplastic Small Round Cell Tumor -A Case Report-

결합조직형성소원형세포종양의 압착도말 세포학적 소견 -1예 보고-

  • Kim, Yong-Jin (Department of Pathology, Yeungnam University College of Medicine) ;
  • Kim, Jae-Hwang (Department of Sugery, Yeungnam University College of Medicine) ;
  • Choi, Joon-Hyuk (Department of Pathology, Yeungnam University College of Medicine)
  • 김용진 (영남대학교의과대학 병리과) ;
  • 김재황 (영남대학교의과대학 외과) ;
  • 최준혁 (영남대학교의과대학 병리과)
  • Published : 2007.03.30

Abstract

Desmoplastic small round cell tumor (DSRCT) is a rare malignant mesenchymal neoplasm. It mainly involves the abdominal or pelvic peritoneum of male adolescents. We report here the imprint cytologic features of a case of DSRCT occurring in the intraabdominal cavity of a 21-year-old man. A microscopic examination showed moderate cellularity. The tumor cells were singly arranged and arranged in clusters. The cells had round to oval nuclei with finely granular chromatin, inconspicuous nucleoli and scanty cytoplasm. Some tumor cells showed nuclear molding, and some cells had an epitheloid appearance with a large amount of lightly eosinophilic cytoplasm. A rosette-like pattern was present. Spindle-shaped, fibroblastic stromal cells were occasionally found. The tumor cells were immunoreactive for the markers cytokeratin (AE1/AE3), epithelial membrane antigen (EMA), desmin, vimentin and neuron specific enolase (NSE).

Keywords

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