Tuberculosis and Respiratory Diseases

The Korean Academy of Tuberculosis and Respiratory Diseases (대한결핵및호흡기학회)
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A Case of Behçet's Disease with Superior Vena Cava Syndrome

상대정맥증후군을 유발한 Behçet병 1예

  • Kim, Young-Jee (Department of Internal Medicine, Eulji Hospital, Eulji Medical College) ;
  • Kim, Sang-Hun (Department of Internal Medicine, Eulji Hospital, Eulji Medical College) ;
  • Lee, Sang Moo (Health Insurance Review Agency) ;
  • Ahn, Youngsoo (Department of Internal Medicine, Eulji Hospital, Eulji Medical College)
  • 김영지 (을지의과대학, 노원을지병원, 호흡기내과) ;
  • 김상훈 (을지의과대학, 노원을지병원, 호흡기내과) ;
  • 이상무 (건강보험심사평가원) ;
  • 안영수 (을지의과대학, 노원을지병원, 호흡기내과)
  • Published : 20040000
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Abstract

As a chronic multisystemic inflammatory disorder, Behçet's disease may manifest vascular, cardiac, neurological and gastrointestinal abnormalities. However, involvement of large veins, such as thrombosis of the superior or inferior vena cava, is a very rare complication. Herein, a case of superior vena cava syndrome, due to the thrombotic obstructions of the subclavian and brachiocephalic vein, is reported in a 27-year old woman with chronic Behçet's disease.

저자들은 베체트병을 진단받고 치료 받던 환자가 안면부종, 상지부종으로 내원 상대정맥 증후군으로 진단 후 혈전용해제와 스테로이드 치료로 호전을 보인 1예를 경험 하였기에 문헌고찰과 함께 보고하는 바이다.

Keywords

References

  1. Lee LA. Beh$\c{c}$et's syndrome. Semin Cutan Med Surg 2001;20:53-7
  2. Ko$\c{c}$ Y, G$\"u$ll$\"u$ I, Akpek G, Akpolat T, Kansu E, Kiraz S, et al. Vascular involvement in Beh$\c{c}$et's disease. J Rheumatol 1992;19:402-10
  3. O'Duffy JD. Vasculitis in Beh$\c{c}$et's disease. Rheum Dis Clin North Am 1990;16:423-31
  4. Kuzu MA, $\"O$zaslan C, K$\"o$ksoy C, G$\"u$rler A, T$\"u$z$\"u$ner A. Vascular involvement in Beh$\c{c}$et's disease. World J Surg 1994;18:948-53
  5. 박광주, 박승호, 김상진, 김형중, 장 준, 안철민, 김성규, 이원영. Behçet 증후군에서 폐침범의 임상양상에 관한 고찰. 결핵 및 호흡기질환 1996;43:763-8
  6. D$\"u$ndar S, Yazici H. Superior vena cava syndrome in Beh$\c{c}$et's di-sease. Vasc Surg 1984;18:28-33
  7. Thomas I, Helmold ME, Nychay S. Beh$\c{c}$et's disease presenting as superior vena cava syndrome. J Am Acad Dermatol 1992;26:863-5
  8. Cadman EC, Landberg WB, Mitchell MS. Pulmonary manifestation in Beh$\c{c}$et's syndrome. Arch Intern Med 1976;136:944-7
  9. Ko GY, Byun JY, Choi BG, Cho SH. The vascular manifestations of Beh$\c{c}$et's disease. Br J Radiol 2000;73:1270-4
  10. Chang H, Kim J. The clinical features of Beh$\c{c}$et's disease in Yongdong districts. J Korean Med Sci 2002;17:784-9
  11. Demiro$\u{g} $lu H, Bari$\c{s}$ta İ, D$\"u$ndar S. Assessing the risk of deep vein thrombosis in Beh$\c{c}$et's disease. Thromb Res 1996;84:297-8
  12. International study group of Beh$\c{c}$et's disease. Criteria for diagnosis of Beh$\c{c}$et's disease. Lancet 1990;335:1078-80
  13. 김훈수, 조재화, 양문희, 김현정, 박병준, 김영신 외 3명. 폐동맥류의 발현으로 진단된 용의형 베체트병 1예. 결핵 및 호흡기질환 2002;52:405-10
  14. Ko SH, Kang SK, Lee SK, Song HS. Massive thrombosis after central venouscatheterization in a patient with previously undiagnosed Beh$\c{c}$et's disease. J Korean Med Sci 2001;16:814-6
  15. Poulter LW, Lehner T. Immunohistology of oral lesions from patients with recurrent oral ulcers and Beh$\c{c}$et's syndrome. Clin Exp Immunol 1989;78(2):189-95