Tuberculosis and Respiratory Diseases
- Volume 47 Issue 2
- /
- Pages.259-264
- /
- 1999
- /
- 1738-3536(pISSN)
- /
- 2005-6184(eISSN)
A Case of Scimitar Syndrome (Adult Form)
성인형 Scimitar 증후군 1예
- Kim, Woo-Gyu (Department of Internal Medicine, Sejong General Hospital) ;
- Kim, Jeong-Kyung (Department of Internal Medicine, Sejong General Hospital) ;
- Jeon, Seong-Hee (Department of Internal Medicine, Sejong General Hospital) ;
- Lim, Dal-Soo (Department of Internal Medicine, Sejong General Hospital) ;
- Min, Cheol-Hong (Department of Internal Medicine, Sejong General Hospital) ;
- Park, Hun-Sik (Department of Internal Medicine, Sejong General Hospital) ;
- Lim, Byung-Sung (Department of Internal Medicine, Sejong General Hospital) ;
- Hong, Suk-Keun (Department of Internal Medicine, Sejong General Hospital) ;
- Hwang, Hweung-Kon (Department of Internal Medicine, Sejong General Hospital) ;
- Kim, Mi-Young (Department of Diagnostic Radiology, Sejong General Hospital)
- 김우규 (부천세종병원 내과) ;
- 김정경 (부천세종병원 내과) ;
- 전성희 (부천세종병원 내과) ;
- 임달수 (부천세종병원 내과) ;
- 민철홍 (부천세종병원 내과) ;
- 박헌식 (부천세종병원 내과) ;
- 임병성 (부천세종병원 내과) ;
- 홍석근 (부천세종병원 내과) ;
- 황흥곤 (부천세종병원 내과) ;
- 김미영 (부천세종병원 방사선과)
- Published : 1999.08.30
Abstract
The scimitar syndrome, a rare complex anomaly, is defined as an anomalous right pulmonary venous drainage, partial or complete, to the inferior vena cava. The shape of the Turkish curved sword (scimitar) has provided the name of this syndrome. Additional characteristics of this syndrome such as hypoplasia of the right lung and of the right pulmonary arterial tree, anomalous arterial supply of the right lung from the aorta, dextrocardia and bronchial anomalies are common. Recently we experienced a case of scimitar syndrome (adult form) in a 19-year-old woman patient, so we report the case with a brief review of the literature.
저자들은 흉부 불쾌감 및 호흡곤란을 주소로 내원한 19세 여자환자에서 우연히 흉부사진상 반월도(scimitar) 모양의 음영 및 우측 폐 형성부전이 발견되어 심초음파, 전산화 단층촬영 혈관조영술, 심도자 및 심혈관 조영술 등으로 확진하여 보존적 치료를 시행한 성인형 Scimitar 증후군을 경험하였기에 문헌고찰과 함께 보고하는 바이다.