Tuberculosis and Respiratory Diseases

The Korean Academy of Tuberculosis and Respiratory Diseases (대한결핵및호흡기학회)
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A Case of Sj$\ddot{o}$gren's Syndrome with Multiple Bullae Secondary to Pulmonary Amyloidosis and Lymphocytic Infiltration of Interstitium and Bronchioles

폐 유전분증(Amyloidosis)과 다발성 수 (Bullae), 폐 간질내 임파구 침윤이 동반된 Sj$\ddot{o}$gren's 증후군 1예

  • Kim, Dong-Il (Department of Internal Medicine, Asan Medical Center, Ulsan University) ;
  • Lim, Yun-Jeong (Department of Internal Medicine, Asan Medical Center, Ulsan University) ;
  • Oh, Yung-Ha (Department of Diagnostic Pathology, Asan Medical Center, Ulsan University) ;
  • Kim, Hyung-Soo (Department of Radiology, Asan Medical Center, Ulsan University) ;
  • Lee, Jin-Sung (Department of Radiology, Asan Medical Center, Ulsan University) ;
  • Kim, Dong-Soon (Department of Internal Medicine, Asan Medical Center, Ulsan University)
  • 김동일 (의과대학 서울중앙병원 내과학교실) ;
  • 임윤정 (의과대학 서울중앙병원 내과학교실) ;
  • 오영하 (의과대학 서울중앙병원 병리학교실) ;
  • 김형수 (의과대학 서울중앙병원 방사선학교실) ;
  • 이진성 (의과대학 서울중앙병원 방사선학교실) ;
  • 김동순 (의과대학 서울중앙병원 내과학교실)
  • Published : 1997.12.31
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Abstract

Sj$\ddot{o}$gren's syndrome(SS) is a chronic inflammatory disorder characterized by lymphocytic infiltration of lacrimal and sailvary glands, which results in dry eyes and dry mouth. SS may exist as a primary condition or as a secondary condition in association with connective tissue disease such as rheumatoid arthritis, systemic lupus erythematosus, or progressive systemic sclerosis. We experienced a patient with primary SS who developed multiple bullae, nodular type of pulmonary amyloidosis and lymphocytic interstitial peumonitis. We believe this to be the first reported case of SS acompanied by these three types pulmonary manifestations at the same time.

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