Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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Staged Total Correction of Complexes Anomalous Origin of Right Pulmonary Artery from the Ascending Aorta One Case Report

상행 대동맥에서의 우폐동맥 이상기시증을 동반한 복잡 심기형의 단계적 완전 교정술-1례 보고-

  • 정일상 (세종병원 흉부외과) ;
  • 한재진 (세종병원 흉부외과, 세종병원 소아과)
  • Published : 1997.03.01
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Abstract

We experienced a case of anomalous origin of right pulmonary artery from the ascending aorta associated with pulmonary atresia, ventricular septal defect, absence of left pulmonary artery afld multiple major aortopulmonary collateral artery (MAPCA). At ten month of age, left pulmonary artery creation with unifocalization and right pulmonary artery banding were performed as the Urst stage, followed by coil embolization of right MAPCA 1 month later, and 1 year later, the total correction was done. After total repair, the patient showed good postoperative course and excellent angiographic and hemodynamic results at 1 year follow-up study.

세종병원 흉부외과에서는 폐동맥 페색증, 좌측폐동맥 무형성증, 심실중격결손증, 다발성 MAPCA등을 동반한 상행 대동맥으로부터 이상기시한 우폐동맥 11례를 경험하였다. 10개월 때 1단계 수술로써 좌측 unifocalization과 함께 좌폐동맥을 만들고 우폐동맥 벤딩을 하였고, 1개월후 우측 MAPCA의 coil 색전술 단계를 거쳐, 1년후 완전 교정술을 시행하였다. 술후 경과는 양호하였고 수술 1년후 조영술과 혈역학적 검사상 만족스런 결과를 얻을 수 있었다.

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References

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