Tuberculosis and Respiratory Diseases
- Volume 42 Issue 3
- /
- Pages.375-380
- /
- 1995
- /
- 1738-3536(pISSN)
- /
- 2005-6184(eISSN)
A Case of Lymphangioleiomyomatosis with Pregnancy
임신으로 악화된 폐의 임파관평활근종증 l예
- Kim, Seong-Ook (Department of Infernal Medicine, College of Medicine, Gyeongsang National University) ;
- Kim, Min-Gu (Department of Infernal Medicine, College of Medicine, Gyeongsang National University) ;
- Won, Yong-Hwan (Department of Infernal Medicine, College of Medicine, Gyeongsang National University) ;
-
Kim, Ho-Cheol
(Department of Infernal Medicine, College of Medicine, Gyeongsang National University)
;
- Hwang, Young-Sil (Department of Infernal Medicine, College of Medicine, Gyeongsang National University) ;
- Kim, Jong-Hwa (Department of Obstetrics & Gynecology, College of Medicine, Gyeongsang National University)
- 김성욱 (경상대학교 의과대학 내과학교실) ;
- 김민구 (경상대학교 의과대학 내과학교실) ;
- 원용환 (경상대학교 의과대학 내과학교실) ;
-
김호철
(경상대학교 의과대학 내과학교실)
;
- 황영실 (경상대학교 의과대학 내과학교실) ;
- 김종화 (경상대학교 의과대학 산부인과학교실)
- Published : 1995.06.30
Abstract
The lymphangioleiomyomatosis(LAM) is a rare disorder, which afflicts mainly young woman of childbearing age, characterized by proliferation of immature smooth muscle cell in the lymphatics. We experienced a case of LAM in 26-years-old pregnant woman, confirmed pathologically by inguinal lymph node biopsy. She has suffered from exertonal dyspnea and dry coughing. The symptoms and chest X-ray were aggravated with pregnancy, but improved after delivery with two times of pregnancy. The chest X-ray showed diffuse reticulonodular infiltration and chest HRCT showed diffuse scattered tiny thin-walled cyst of lung parenchyma. We noted chylous ascites of which triglyceride level is 396 mg/dl. After delivery, the symptoms were getting better. We treated with medroxyprogesterone and planned close observation and follow-up.