Tuberculosis and Respiratory Diseases

The Korean Academy of Tuberculosis and Respiratory Diseases (대한결핵및호흡기학회)
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A Case of Tuberous Sclerosis with Pulmonary Involvement

폐를 침범한 결절성 경화증 1예

  • Ahn, Jong-Ho (Department of Internal Medicine, Seoul National University College of Medicine) ;
  • Suh, Gee-Young (Department of Internal Medicine, Seoul National University College of Medicine) ;
  • Kim, Young-Whan (Department of Internal Medicine, Seoul National University College of Medicine) ;
  • Shim, Young-Soo (Department of Internal Medicine, Seoul National University College of Medicine) ;
  • Kim, Keun-Youl (Department of Internal Medicine, Seoul National University College of Medicine) ;
  • Han, Yong-Chol (Department of Internal Medicine, Seoul National University College of Medicine)
  • 안종호 (서울대학교 의과대학 내과학교실) ;
  • 서지영 (서울대학교 의과대학 내과학교실) ;
  • 김영환 (서울대학교 의과대학 내과학교실) ;
  • 심영수 (서울대학교 의과대학 내과학교실) ;
  • 김건열 (서울대학교 의과대학 내과학교실) ;
  • 한용철 (서울대학교 의과대학 내과학교실)
  • Published : 1992.10.31
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Abstract

Tuberous sclerosis is a syndrome characterized by the facial skin lesion, epilepsy, and mental retardation. Pulmonary involvement is uncommon, but when the lung is involved by tuberous sclerosis it shows characteristic reticulonodular infiltration and cystic changes. We experienced a 34-year-old female patient of known tuberous sclerosis admitted due to pneumothorax. Chest PA showed diffuse fine reticulonodular infiltration and chest CT revealed diffuse cystic changes of the lung. Pleurodesis with tetracycline was done to prevent recurrence, but chylothorax occurred four months after the treatment. Pleurosis was tried again and anti estrogen treatment began.

저자들은 결절성 경화증으로 추적 관찰중인 환자에서 기흉과 유미흉이 발생하고 그 고해상도 전산화 단층촬영의 소견이 알려진 병리적 소견에 부합되는 1예를 경험하였기에 이를 문헌 고찰과 함께 보고하는 바이다.

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