• Neonatal Medicine
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• 제25권1호
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• pp.49-52
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• 2018

Arterial tortuosity syndrome (ATS) is a very rare autosomal recessive connective tissue disease characterized by generalized elongation and tortuosity of the medium- to large-sized arteries, and other systemic connective tissue manifestations. To date, this disease entity has not been reported in Korea. We report a case of ATS diagnosed in a neonate who presented with severe elongation and tortuosity of the aorta and its major branches, as well as the intracranial arteries. Additionally, the patient presented with a tortuous dilatation of the inferior vena cava, an aneurysmal dilatation of the extra-hepatic bile ducts, and an inguinal and sliding hiatal hernia. The diagnosis was confirmed using DNA sequencing analysis, and the patient demonstrated a compound heterozygosity for two novel mutations (c.738delG [p.Gln247Serfs*33] and c.362T>C [p.Ile121Thr]) in exon 2 of the SLC2A10 gene. Genetic analysis also confirmed that both parents were heterozygous carriers of the responsible mutations. Owing to such clinical manifestations, ATS is often misdiagnosed as other connective tissue diseases including Loeys-Dietz syndrome, Marfan syndrome, and Ehlers-Danlos syndrome. In patients presenting with a high index of suspicion, thorough clinical evaluation and screening for ATS including computed tomography or magnetic resonance angiography and target gene analysis are necessary for early diagnosis and management.

• 기술사
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• 제17권3호
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• pp.6-21
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• 1984

A rock slide in amount of 100 tons in weight happened at 7: 10 a.m., 4th October 1982, on the southwestern ridge of Mt. Seunghag, Busan City. The original rock mass of the rock slide is located 850m west from the Dangri Crushed Stone Quarry. The geology of the area consists of agglomerate, andesite, andesitic tuff, and shale hornfels of the Cretaceous Yucheon Group. The rock blocks were first shifted along the steep joint plane on an andesite outcrop at the site and then to the eastern foot of the mountain slope where some private houses are placed. The mountain slope is covered with thick superficial soil. A slided monolithic-block with 83 tons in weight from the rock slide met with an accident of striking against a house with a tremendous force, to which much damage was done as much as its half was destroyed. The rock-slided block pierced the board-floored room only posited at the center and by the bedroom of the house making a pass like a bullet hole, and hence cut a big pine tree with 24 centimeters in diameter at a distance of 26 meters down the house. However nobody was killed or injured in the stricken house, though seven family members were stayed therein at the very time of accident. They really met a rare opportunity in an unhappy disaster. Measurements of the rock slide were made in the course of the field survey. The monolithic mass was transported by way of saltation, rolling, and sliding to a distance of 300 meters down along the slope dipping 30$^{\circ}$ east. It took about 16 seconds front tile outcrop to the terminal. The acceleration value of the monolithic rock slide is 2.35m/sec$^2$.

• 터널과지하공간
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• 제17권6호
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• pp.438-447
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• 2007

본 기술보고서는 Lisbon에서 개최된 2007 ISRM Congress에서 발표된 논문을 소개한 것이다. 이는 SRM(합성암반체)에 관한 연구결과이며, 이의 중요성과 향후 잠재력을 강조하고 있는 Fairhurst 교수가 직접 발표한 논문이다. 절리 암반의 특성을 규명하는 SRM 접근법은 현존하는 경험적 접근법이나 절리 암반의 거동에 대한 현재의 이해정도와 관련지어 재검토된다. 이 재검토 논문에서 절리 암반의 역학적 거동에 영향을 미치는 주요 요소들이 어떻게 고려되는가를 기술하며, 또 SRM 접근법이 상당히 발전되어 현장에 적용된 사례를 보여준다. PFC-3D에서 BP 모델링과 DFN 모사법 등의 두개의 잘 정립된 방법에 기초를 두고 있는 이 기법은 새로운 미끄러지는 절리모델을 사용한다. 이 모델은 모든 응력경로에 의하여 힘을 받고 있는 수천개의 기존 절리를 포함하는 대규모 암반체를 모사할 수 있게 하는 것이다. 암반의 강도 및 취성도, 완전 순응 행렬의 전개, 그리고 초기의 파쇄 등이 SRM 시험에서 얻어지는 결과이다.

• Archives of Reconstructive Microsurgery
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• 제1권1호
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• pp.9-16
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• 1992

Volkmann's ischemic contracture is the end result of an untreated, delayed or Inadequately decompressed compartment syndrome in which muscle ischemia and necrosis have occurred. Once the muscle necrosis have happened, the involved muscle undergo permanent change into fibrous tissue. So secondary shortening and distal joint contracture will be a final outcome, which results in marked functional impairment of hand and forearm. Even though several procedures, such as muscle sliding operation has been attempted, overall results were far from satisfaction, compare to healthy opposite hand. The management of these unfavorable condition of the forearm and hand was regarded as one of challenging area in orthopedics. Recently new approach, using microsurgical technique which transfers functioning muscle unit, has been developed and its result was much better than any other methods in the aspect of an active motion. Among these musculocutaneous free flaps, gracilis has obtained special reputation due to its easiness to handle such as elevation of flap and reliable neurovascular pedicle. Other advantages are flexibility of flap size to adjust variable size of the defect in the forearm and minor morbidity of the donor site. Authors have performed 7 cases of functioning gracilis musulocutaneous free flap transplantation for the functional loss of forearm and hand due to Volkmann's ischemic contracture or muscle and skin defect due to severe trauma since November, 1981 till May, 1991. The results in most cases were satisfactory and acceptable.

• Structural Engineering and Mechanics
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• 제44권6호
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• pp.775-799
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• 2012

This work approaches the structural performance of masonry arches that have a small ratio between number of vossoirs and span length. The aim of this research is to compare and validate three different methods of analysis (funicular limit analysis F.L.A., kinematic limit analysis K.L.A. and plane stress Finite Element Analysis F.E.A.) with an experimental campaign. 18 failure tests with arches of different shapes and boundary conditions have been performed. The basic failure mechanism was the formation of enough hinges in the geometry. Nevertheless, in few cases, sliding between vossoirs also played a relevant influence. Moreover, few arches didn't reach the collapse. The FLA and KLA didn't find a solution close to the experimental values for some of the tests. The low number of vossoirs and joints become a drawback for an agreement between kinematic mechanism, equilibrium of forces and geometry constraints. FLA finds a lower bound whereas KLA finds an upper bound of the ultimate load of the arch. FEA is the most reliable and robust method and it can reproduce most of the mechanism and ultimate loads. However, special care is required in the definition of boundary conditions for FEA analysis. Scientific justification of the more suitability of numerical methods in front of classic methods at calculating arches with a few vossoirs is the main original contribution of the paper.

• 한국운동역학회지
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• 제26권4호
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• pp.333-341
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• 2016

Objective: The purpose of this study was to assess the consistency of the gliding and push-off motion for single leg skating from the first to fourteenth steps. We hypothesized that: 1) there would be no difference in stroke trajectory, step rate, and cycle rate between the left and right steps of gliding; and 2) there would be a difference in the resultant velocity of toe push-off and the horizontal velocity of the center of mass after six step push-offs. Method: The study included five male 500-m speed skaters (mean height, $1.80{\pm}0.02m$; mean weight, $76.8{\pm}3.96kg$; record, $35.83{\pm}0.30sec$; 100-m record, <9.97 sec). Data were collected from the first to fourteenth steps (40 m) and recorded using five digital JVC GR-HD1KR video cameras (Victor Co., Japan) operating at a sampling frequency of 60 fields/sec and shutter speed of 1/500 sec. For each film frame, the joint positions were digitized using the KWON3D motion analyzer. Position data were filtered with low-pass Butterworth $4^{th}$ order at the cut-off frequency of 7.4 Hz. Results: The right toe of the skating trajectories at $2^{nd}$, $5^{th}$, and $7^{th}$ strokes differed from those of the left toe. The angles of the right and left knee demonstrated unbalanced patterns from the flexion and extension legs. The step and cycle rates of the right and left leg differed from the start until 20 m. The resultant velocities of the toe at the push-off phase and of the body mass center diverged before the six push-offs. Conclusion: This study's findings indicate that the toe of skating trajectory on left and right sliding after push-off should maintain a symmetrical trajectory. The resultant velocity of toe push-off and horizontal velocity from the center of body need to be separated after about six step push-offs.

• 드라이브 ㆍ 컨트롤
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• 제11권2호
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• pp.30-35
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• 2014

The pumps of electro-hydrostatic actuators operate most frequently in boundary lubrication speed range, as they compensate for the position control errors as a control element. When conventional swash plate type piston pumps are applied to electro-hydrostatic actuators, the frictional power losses as well as the wear rate of sliding components, such as piston shoes can increase drastically under the boundary friction condition. In this paper, the power losses of the piston shoes were investigated which were engendered by a frictional solid-to-solid contact and leakage flow rate of their hydrostatic bearing. In order to reduce them, DLC-coating was applied to the swash plate and the ball joint of pistons along with its effects were demonstrated. In addition, it was also shown that the wear rate of the piston shoes could be markedly reduced using the DLC-coated swash plate.

• 대한구강악안면병리학회지
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• 제42권5호
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• pp.145-152
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• 2018

A 57 years old female complained of severe pain on the right temporomandibular joint (TMJ) area. Her right condyle had been partly resected under surgical operation 13 years ago due to condyle hypertrophy, thereafter she felt dull pain on TMJ area and recently the lesion became severely swelled and painful leading to cancer phobia. The present radiological views showed slightly enlarged and sclerosed condyle with increased radiopacity, but its articular sliding function was almost disable during mouth opening. The patient's TMJ lesion was carefully managed with conservative physiotherapy and pain treatment. The microsection of condyle head obtained from the previous operation was re-evaluated histologically, and it was finally diagnosed as osteochondrosis dissecans (OCD), exhibiting hyperplastic proliferation of cartilage in condyle head and marked vascular dilatation in epiphyseal zone. This abnormal cartilage tissue was distinguishable from normal cartilage tissue found in the peripheral cartilaginous cap of the same microsection. The involved cartilage cap showed thick hypertrophic chondrocyte zone with horizontal and vertical clefts accompanying diffuse hyaline degeneration. The superficial fibrous zone of cartilage cap was thickened and frequently peeled off, while lower hypertrophic zone of cartilage cap was highly cellular and proliferative. Consequently, the endochondral ossification became aberrant and resulted pre-mature apoptosis of many hypertrophic chondrocytes, followed by diffuse and mild inflammatory reaction in the underlying marrow tissue. Therefore, it was suggested that this hypertrophic condyle lesion, OCD, be differentiated depending on radiological and histological features from ordinary condyle hyperplasia, osteochondroma, and osteoarthritis, and that the pathological confirmation of OCD may provide a reliable modality for dental and medical treatment of chronic and painful TMJ lesion.

• Earthquakes and Structures
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• 제24권6호
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• pp.439-453
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• 2023

Older brick masonry structures generally suffer from low strength defects. Using a cement mortar layer (CML) or steel-meshed cement mortar layer (S-CML) to reinforce existing low-strength brick masonry structures (LBMs) is still an effective means of increasing seismic performance. However, performance indices such as lateral displacement ratios and skeleton curves for LBMs reinforced with CML or S-CML need to be clarified in performance-based seismic design and evaluation. Therefore, research into the failure mechanisms and seismic performance of LBMs reinforced with CML or S-CML is imperative. In this study, thirty low-strength brick walls (LBWs) with different cross-sectional areas, bonding mortar types, vertical loads, and CML/S-CML thicknesses were constructed. The failure modes, load-carrying capacities, energy dissipation capacity and lateral drift ratio limits in different limits states were acquired via quasi-static tests. The results show that 1) the primary failure modes of UBWs and RBWs are "diagonal shear failure" and "sliding failure through joints." 2) The acceptable drift ratios of Immediate Occupancy (IO), Life Safety (LS), and Collapse Prevention (CP) for UBWs can be 0.04%, 0.08%, and 0.3%, respectively. For 20-RBWs, the acceptable drift ratios of IO, LS, and CP for 20-RBWs can be 0.037%, 0.09%, and 0.41%, respectively. Moreover, the acceptable drift ratios of IO, LS, and CP for 40-RBWs can be 0.048%, 0.09%, and 0.53%, respectively. 3) Reinforcing low-strength brick walls with CML/S-CML can improve brick walls' bearing capacity, deformation, and energy dissipation capacity. Using CML/S-CML reinforcement to improve the seismic performance of old masonry houses is a feasible and practical choice.

• Geomechanics and Engineering
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• 제32권4호
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• pp.375-385
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• 2023

There are many joint fissures distributed in the engineering rock mass. In the process of geological history, the underground rock mass undergoes strong geological processes, and undergoes complex geological processes such as fracture breeding, expansion, recementation, and re-expansion. In this paper, the damage-stick-slip process (DSSP), an analysis model used for rock mass failure slip, was established to examine the master control and time-dependent mechanical properties of the new and primary fractures of a multi-fractured rock mass under the action of stress loading. The experimental system for the recemented multi-fractured rock mass was developed to validate the above theory. First, a rock mass failure test was conducted. Then, the failure stress state was kept constant, and the fractured rock mass was grouted and cemented. A secondary loading was applied until the grouted mass reached the intended strength to investigate the bearing capacity of the recemented multi-fractured rock mass, and an acoustic emission (AE) system was used to monitor AE events and the update of damage energy. The results show that the initial fracture angle and direction had a significant effect on the re-failure process of the cement rock mass; Compared with the monitoring results of the acoustic emission (AE) measurements, the master control surface, key blocks and other control factors in the multi-fractured rock mass were obtained; The triangular shaped block in rock mass plays an important role in the stress and displacement change of multi-fracture rock mass and the long fissure and the fractures with close fracture tip are easier to activate, and the position where the longer fractures intersect with the smaller fractures is easier to generate new fractures. The results are of great significance to a multi-block structure, which affects the safety of underground coal mining.