• Title/Summary/Keyword: schwannoma

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A case of huge neurilemmoma arising from retropharyngeal space (후인두강에 발생한 거대 신경초종 1례)

  • Jung, Woo-Jin;Kim, In-Kyeong;Lee, Hyun-Seok;Lee, Dong-Wook
    • Korean Journal of Bronchoesophagology
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    • v.11 no.2 s.22
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    • pp.36-39
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    • 2005
  • Neurofibromatosis type II is an autosomal dominant, highly penetrant disease whose hallmark is bilateral vestibular schwannoma. Hearing loss is the most symptom in Neurofibromatosis type II. The patient can also present with tinnitus, disequilibrium, and headache. Cranial nerve symptoms, such as facial numbness or weakness, dysphagia, or hoarseness, can also be present. The authors experienced a case of neurofibromatosis type II having huge retropharyngeal mass, retropharyngeal abscess, and bilateral acoustic neuromas. The infection was controled with aggressive antibiotics with drainage. The huge neurilemmoma in retropharyngeal space was removed successfully via transoral approach. The authors report the case with literature review.

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A Case of Intraparotid Facial Nerve Schwannoma (이하선내 안면신경에서 발생한 신경초종 1례)

  • Sun, Dong-Il;Kim, Min-Sik;Lee, Jeong-Hak;Cho, Seung-Ho
    • Korean Journal of Bronchoesophagology
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    • v.6 no.1
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    • pp.113-117
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    • 2000
  • A neurilemmoma of the facial nerve presenting as a parotid mass is a rare neoplasm and has been reported infrequently in the surgical literature. Diagnosis is usually by tissue biopsy intraoperatively and treatment is surgical with preservetion of facial function. This is a case of a solitary neurilemmoma involving the main trunk of the facial nerve in the posterior part of parotid gland continuing up to vertical segment of the facial nerve, in which the facial nerve had to be sacrificed and free autogenous nerve grafting was done.

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Extramedullary tanycytic ependymoma of the lumbar spinal cord

  • Kim, Dong Ja;Han, Man-Hoon;Lee, SangHan
    • Journal of Yeungnam Medical Science
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    • v.37 no.2
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    • pp.128-132
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    • 2020
  • Tanycytic ependymoma is a rare variant of ependymoma that commonly affects the cervical and thoracic spinal cord. It usually arises as intramedullary lesions, and extramedullary cases are extremely rare. We report a case of a 44-year-old woman who was diagnosed with tanycytic ependymoma in her lumbar spine at level 2-3. The tumor mass developed in an intradural extramedullary location. Histopathologically, tanycytic ependymoma can be misdiagnosed as schwannoma or pilocytic astrocytoma. Immunohistochemical findings such as strong positivity for glial fibrillary acidic protein, perinuclear dot-like positive patterns for epithelial membrane antigen, and focal positivity for S100 protein are helpful in diagnosing tanycytic ependymoma. It is important to be aware of this rare tumor to ensure appropriate patient management and accurate prognosis.

Long-Term Survival after Wide Resection of Malignant Fibrous Histiocytoma of the Chest Wall

  • Shin, Jin Won;Chang, Yong Jin;Cho, Deog Gon;Choi, Si Young
    • Journal of Chest Surgery
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    • v.52 no.1
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    • pp.36-39
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    • 2019
  • Primary malignant fibrous histiocytoma (MFH) of the chest wall is extremely rare and is characterized by aggressive features, including a high incidence of local recurrence and distant metastasis. Surgical resection of the chest wall is the primary modality of management. However, surgical treatment is not generally recommended in patients with evidence of distant metastasis. Here, we present a case of chest wall MFH along with a schwannoma mimicking distant metastasis in the right upper arm. The patient was treated by radical en bloc resection and survived for more than 9 years without recurrence.

A Case of Giant Malignant Peripheral Nerve Sheath Tumor of Neck (경부의 거대 악성 말초 신경성 종양 예)

  • Choonghun Han;Hanaro Park
    • Korean Journal of Head & Neck Oncology
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    • v.40 no.1
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    • pp.43-47
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    • 2024
  • Malignant peripheral nerve sheath tumor (MPNST) is an extremely rare sarcoma of soft tissue. It is locally invasive, frequently recurred and metastasizes distantly, therefore has a very poor prognosis. the most involved sites are human body and extremities, and MPNST occurs and involved very rarely in the parapharynx of neck. MPNST does not react to radiotherapy and chemotherapy, therefore complete surgical resection is the most important treatment. Since immunohistochemical staining is essential for the final diagnosis, it is common to be confirmed after surgery. We report a case of giant MPNST without symptom in the head and neck involving the right parapharynx with multiple distant metastases in a 74-year-old patient on a review of the literature.

Surgical Treatment of Malignant Tumors in Shoulder Girdle (견갑관절 주위 악성종양의 치료경험)

  • Song, Seok-Whan;Chang, Ju-Hai;Kang, Yong-Koo;Kim, Jung-Man;Kim, Hyoung-Min;Rhee, Seung-Koo;Woo, Young-Kyun;Bahk, Won-Jong;Moon, Myung-Sang;Kim, Yang-Soo
    • The Journal of the Korean bone and joint tumor society
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    • v.1 no.1
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    • pp.68-76
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    • 1995
  • To evaluate the clinical result of surgical treatment of malignant tumors in shoulder girdle, nine patients who were treated in Department of Orthopedics, Catholic University Medical College between January 1991 and December 1993, were evaluated. There were 5 men, 4 women. The mean age at operation was 47 years(range from 22 to 64 years). Of 9 patiens, 2 were soft tissue tumors(1 MFH, 1 dermatofibrosarcoma protuberance); one was treated with forequarter amputation, and the other with wide excision, Seven were bone tumor(2 chondrosarcoma, 1 osteosarcoma, 1 MFH, 1 plasmacytoma, 1 thyroid carcinoma metastasis, 1 malignant schwannoma); one patient was treated with segmental excision of proximal humerus, 4 with Malawer type I-A resection and arthroplasty or arthrodesis, 1 with Malawer type V-B resection and arthrodesis. Five patients received adjuvant chemotherapy, with or without local radiation therapy, and one patient received radiation therapy alone. All patients have survived now, but I had local recurrence. Functional results of arthrodesis and arthroplasty were similar.

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Clinical Comparison of Surgical Treatment and Close Observation Without Surgery in the Management of Schwannomas in the Neck (경부에 발생하는 신경초종에서 수술적 치료와 정기적 경과관찰의 임상적 비교)

  • Hong, Sung-Lyong;Jung, Young-Ho;An, Soo-Youn;Hah, J.-Hun;Sung, Myung-Whun;Kim, Kwang-Hyun
    • Korean Journal of Head & Neck Oncology
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    • v.25 no.1
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    • pp.24-27
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    • 2009
  • Backgrounds and Objectives : Most patients with neck schwannomas are asymptomatic. Surgical management of neck schwannomas could cause various complications. The aim of this study is to evaluate the necessity of surgical management in all of the neck schwannoma patients. Material and Methods : Thirty-four patients diagnosed and undergone surgical management as neck schwannomas and 30 patients diagnosed and observed closely by OPD base from 1996 to 2005 were included. The medical records were reviewed retrospectively. Results : In surgical management group, mean age was 39.3 years and mean size of tumors was 4.4cm. Twenty-five patients had their tumors at parapharyngeal space, 2 at anterior neck and 7 at lateral neck. Nerves of origin were vagus nerve in 12 patients, cervical sympathetic chain in 11. Presenting symptoms were neck mass in 22 patients and no symptom in 9. On the other hand, in close observation group, mean age was 47.1 years and mean size of tumor was 3.7cm. Seventeen patients had their tumors at parapharyngeal space, 5 at anterior neck and 8 at lateral neck. Presenting symptoms were neck mass in 13 patients and no symptom in 13. There were no patients with neurologic complications. Mean follow-up duration was 38.2 months and there were only 2 patients whose size of tumors was increased and no patients who had newly emerged symptoms. Conclusion : Neck schwannomas grows slowly, has little chance of malignant transformation, but can complicate serious problems after surgical management. Therefore close observation could be considered in many asymptomatic patients.

Pictorial Review of Rare Pancreatic Tumors and Tumor-Like Lesions (췌장에서 생기는 희귀 종양 및 종양 유사 병변들의 영상 소견)

  • Seung Jae Lee;Sang Soo Shin;Suk Hee Heo;Yong Yeon Jeong
    • Journal of the Korean Society of Radiology
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    • v.81 no.5
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    • pp.1134-1150
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    • 2020
  • Various types of tumors and tumor-like lesions may affect the pancreas. Among them, pancreatic ductal adenocarcinoma is the most common and is generally referred to as "pancreatic cancer." Recently, the detection rates of rare pancreatic tumors and tumor-like lesions have increased owing to technological advancements and increased frequency of imaging tests. Considering that rare pancreatic tumors and tumor-like lesions differ from pancreatic ductal adenocarcinoma in terms of the treatment plan and prognosis, the differential diagnosis of these diseases is clinically relevant. Various imaging tests play an important role in the differential diagnoses of rare tumors, such as acinar cell carcinoma and schwannoma, tumor-like lesions, such as autoimmune pancreatitis and inflammatory pseudotumor, and pancreatic ductal adenocarcinoma, but accurately distinguishing these diseases solely based on imaging findings is difficult. The aim of this pictorial review was to present the imaging findings of rare pancreatic tumors and tumor-like lesions and discuss important points for the differential diagnosis.

Undetermined Fibrous Tumor with Calcification in the Cerebellopontine Angle

  • Cheon, Se-Hun;Kang, Shin-Hyuk;Park, Kyung-Jae;Chung, Yong-Gu
    • Journal of Korean Neurosurgical Society
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    • v.48 no.2
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    • pp.173-176
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    • 2010
  • In this report, we introduce an undetermined fibrous tumor with calcification occurring in the cerebellopontine angle (CPA). A 51-year-old woman was admitted with a short history of dizziness. Computed tomography and magnetic resonance images revealed a $2{\times}2{\times}2\;cm$ sized mass at the left CPA which was round and calcified. There was no dura or internal auditory canal involvement. At surgery, the tumor was located at the exit of 7th and 8th cranial nerve complex. It was very firm, bright yellow and well encapsulated. Histologic findings revealed that the tumor was predominantly composed of fibrous component, scant spindle cells and dystrophic calcification. Immunohistochemical staining demonstrated positive for vimentin and negative for epithelial membrane antigen (EMA), S-100 protein, CD34, factor XIIIa and smooth muscle actin. The diagnosis was not compatible with meningioma, schwannoma, metastatic brain tumors, and other fibrous tumors. Although the tumor was resected in total, long term follow-up monitoring is necessary due to the possibility of recurrence.