• Clinical and Experimental Pediatrics
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• 제57권2호
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• pp.91-95
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• 2014

Griscelli syndrome type 2 (GS2) is a rare autosomal recessive disease caused by mutations in the RAB27A gene. It is characterized by cutaneous hypopigmentation, immunodeficiency, and hemophagocytic lymphohistiocytosis. We describe 2 brothers who had GS2 with clinically diverse manifestations. The elder brother presented with a purely neurological picture, whereas the younger one presented with fever, pancytopenia, hepatosplenomegaly, and erythema nodosum. Considering that cutaneous hypopigmentation was a common feature between the brothers, genetic analysis for Griscelli syndrome was performed. As the elder sibling had died, mutation analysis was only performed on the younger sibling, which revealed a novel homozygous mutation in the RAB27A gene on chromosome 15 showing a single-base substitution (c.136T>A p.F46I). Both parents were heterozygous for the same mutation. This confirmed the diagnosis of GS2 in the accelerated phase in both siblings. The atypical features of GS2 in these cases are a novel mutation, isolated neurological involvement in one sibling, association with erythema nodosum, and 2 distinct clinical presentations in siblings with the same genetic mutation.

• Perspectives in Nursing Science
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• 제15권1호
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• pp.1-10
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• 2018

Purpose: The purpose of this study was to examine the usefulness of the Myers-Briggs Type Indicator (MBTI) through a character analysis of a novel and to improve the understanding of various types of people. This study aimed to increase nurses' understanding and empathy regarding the personality of various patients. Methods: This study categorized the characters in the novel Our Happy Time based on MBTI and analyzed their personality characteristics. Results: It is important for nurses to understand that the following types of patients can be identified using the MBTI: those with a concise explanation (ENTP), a modest attitude (ISFJ), an objective response (ENFJ), and a logical response (ENTJ). Conclusion: It is important for nurses to broaden their understanding of various personality types and backgrounds related to the formation of patients' personalities that they encounter in the clinical field via analyses using the MBTI personality types. Furthermore, understanding communication skills can be an important first step in resolving conflicts that occur during peer interactions.

• BMB Reports
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• 제37권2호
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• pp.159-166
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• 2004

Angiostatin is a potent anti-angiogenic protein. To examine the angiostatin-interacting proteins, we used the display-cloning method with a T7 phage library presenting human cDNAs. The specific T7 phage clone that bound to the immobilized angiostatin was isolated, and a novel gene encoding the displayed polypeptide on the isolated T7 phage was identified. The displayed angiostatin-binding sequence was expressed in E. coli as a soluble protein and purified to homogeneity. This novel angiostatin-binding region interacted specifically to angiostatin with a dissociation constant of $3.4{\times}10^{-7}\;M$. A sequence analysis showed that the identified sequence was a part of the large ORF of 1,998 amino acids, whose function has not yet been characterized. A Northern analysis indicated that the gene containing the angiostatin-binding sequence was expressed differentially in the developmental stages or cell types.

• Journal of international Conference on Electrical Machines and Systems
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• 제1권1호
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• pp.47-53
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• 2012

A novel 6/5 switched reluctance motor (SRM) with short flux path is presented in this paper. The concept of this proposed motor is a novel SR motor with six stator and five rotor poles. The stator is constructed with three independent and physically separate C-core segments, and the rotor is composed of five poles. This motor, with a new selection for the number of stator/rotor poles, achieves a short flux path, which reduces the magnetomotive force required to drive the motor. To verify the performance of the proposed motor, a comparison with conventional SR motors with the same dimensions is executed. The comparison demonstrates that the proposed motor offers better performance in terms of maximum torque production. Furthermore, Finite Element Analysis (FEA) and Matlab/Simulink software are used to predict and simulate the performance of the proposed motor.

• Smart Structures and Systems
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• 제12권3_4호
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• pp.291-308
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• 2013

A novel concept of transmissibility based on a wavelet transform for structural damage detection is presented in this paper. The main objective of the research was the development of a method for detecting slight damage at the incipient stage. As a vibration-based approach, the concept of transmissibility has attracted considerable interest because of its advantages and effectiveness in damage detection. However, like other vibration-based methods, transmissibility-based approaches suffer from insensitivity to slight local damage because of the regularity of the traditional Fourier transform. Therefore, the powerful signal processing techniques must be found to solve this problem. Wavelet transform that is able to capture subtle information in measured signals has received extensive attention in the field of damage detection in recent decades. In this paper, we first propose a novel transmissibility concept based on the wavelet transform. Outlier analysis was adopted to construct a damage detection algorithm with wavelet-based transmissibility. The feasibility of the proposed method was numerically investigated with a typical six-degrees-of-freedom spring-mass system, and comparative investigations were performed with a conventional transmissibility approach. The results demonstrate that the proposed transmissibility is more sensitive than conventional transmissibility, and the former is a promising tool for structural damage detection at the incipient stage.

• Journal of Electrical Engineering and Technology
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• 제5권2호
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• pp.220-227
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• 2010

This paper presents a novel fault location scheme on Korean AC electric railway systems. On AC railway system, because of long distance, 40[km] or above, between two railway substations, a fault location technique is very important. Since the fault current flows through the catenary system, it must be modeled exactly to analyze the fault current magnitude and fault location. In this paper, suggesting the novel scheme of fault location, a 9-conductor modeling technique including boost wires and impedance bonds is introduced based on the characteristics of Korean AC electric railway. After obtaining a 9-conductor modeling, the railway system is constructed for computer simulation by using PSCAD/EMTDC. By case studies, we can verify superiority of a new fault location scheme and propose a powerful model for fault analysis on electric railway systems.

• Journal of Magnetics
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• 제21권4호
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• pp.635-643
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• 2016

Improvements were made in the study for the design of the conventional Eddy Current Separator (ECS) used for separating small sized non-ferrous particles in the waste. These improvements include decreasing the air gap between the material and magnetic drum, making the drum position adjustable and placing the splitter closer to the drum. Thus, small particles were separated with high efficiency. The magnetic drum was removed from inside the ECS conveyor belt system as design change and was placed as a separate unit. Hence, the force generated on the test material increased by about 5.5 times while the air gap between the non-ferrous materials and drum decreased from 3 mm to 1 mm. The non-metal material in the waste is separated before the drum in the novel design. Whereas non-ferrous metal particles are separated by falling into the splitter as a result of the force generated as soon as the particles fall on the drum. Every material that passes through the drum can be recycled as a result of moving the splitter closer to the contact point of the drum. In addition, the drum can also be used for the efficient separation of large particles since its position can be adjusted according to the size of the waste material. The performance of the novel design ECS was verified via analytical approaches, finite element analysis (FEA) and experimental studies.

• 전력전자학회:학술대회논문집
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• 전력전자학회 2019년도 전력전자학술대회
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• pp.11-13
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• 2019

This paper proposes a novel high step-up non-isolated DC-DC converter, suitable for regulating dc bus in various inherent low voltage micro sources especially for photovoltaic (PV) and fuel cell sources. This novel high voltage Non-isolated Boost DC-DC converter topology is best replacement, where high voltage conversion ratio is required without the transformer and also need continuous input current. Since the proposed topology utilizes the stack-based structure, the voltage gain, and the efficiency are higher than other conventional non-isolated converters. Switches in this topology is easier to control since its control signal is grounding reference. Also, there is no need of extra gate driver and extra power supply for driver circuit, which reduces the cost and size of system. In order to show the feasibility and practicality of the proposed topology principle operation, steady state analysis and simulation result is presented and analyzed in detail. To verify the performance of proposed converter and theoretical analysis 360W laboratory prototype is implemented.

• 한국산학기술학회논문지
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• 제20권6호
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• pp.113-125
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• 2019

본 연구는 중국 IP산업에서 웹소설드라마 분석을 통해 소비자 대중심리를 알아보고 웹소설 파생상품의 제작방향을 파악하기 위한 연구이다. 이를 위해 중국 웹소설드라마 특성이 파생상품의 수용태도와 행동의도에 어떠한 영향을 미치는지를 분석하였다. 자료수집은 2018.10.15일~10.22일까지 중국 현지인들을 대상으로 수집한 설문조사 자료 612부를 표본으로 삼았다. 통계처리는 데이터 코딩(data coding)과 데이터 크리닝(data cleaning)과정을 거쳐, SPSS v. 21.0 통계 패키지 프로그램을 활용하여 분석하였다. 분석방법은 빈도분석, 탐색적 요인분석, 독립표본 t-test, 일원변량분석(One way ANOVA), 사후검정 Duncan test, 상관관계분석, 다중회귀분석을 실시하였다. 연구결과는 다음과 같다. 첫째, 웹소설드라마 특성인 화제성, 공감성, 흥미성이 파생상품 수용태도인 인지적인 태도 및 정서적인 태도에 유의적인 상관관계를 이루고 있다. 동시에 공감성이 화제성 및 흥미성보다 더 유의적인 영향을 미친 것으로 나타났다. 둘째, 화제성, 공감성, 흥미성으로 구성된 웹소설드라마 특성이 행동의도에 미치는 상관관계에서 웹소설드라마 모든 특성이 행동의도에 긍정적인 영향을 미쳤다. 특히 흥미성 및 화제성보다 공감성이 구매의도 및 추천의도에 더 유의미한 영향을 미친 것이다. 셋째, 정서적 태도가 구매의도 및 추천의도에 미치는 영향은 인지적 태도가 구매의도 및 추천의도에 미치는 영향보다 더 긍정적인 것으로 나타났다. 연구결과는 중국 웹소설의 파생상품 제작방향 설정을 위한 기초자료이자 제작지침으로서 유용한 의미를 갖는다.

• 대한전기학회:학술대회논문집
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• 대한전기학회 2011년도 제42회 하계학술대회
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• pp.1089-1090
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• 2011

This paper presents a novel two-phase two-pole permanent magnet synchronous motor (PMSM) with asymmetric U-core stator structure. The construction and parameters of the novel two-phase U-core PMSM are compared with a conventional U-core single-phase PMSM (SPMSM). Then transient characteristics such as torque, back-emf, and power loss of the both PMSMs are analyzed by using 3-D Finite Element Method (FEM). Under the same condition of rated input current, synchronous speed, similar dimensions and volume, FE results show that the two-phase PMSM with U-core stator has significantly less torque ripple than single-phase U-core PMSM, with similar power loss and efficiency.