• Journal of Oral Medicine and Pain
• /
• 제31권4호
• /
• pp.337-346
• /
• 2006

이 논문은 2년 동안 경북대학병원 구강내과를 턱관절 질환을 주소로 내원한 환자 중에 과두흡수가 있는 환자들로서 자기공명영상, 파노라마, 측방횡두개상 그리고 측방 두부방사선 사진들을 모두 촬영한 34명의 환자들만 선택하여, 측방두부방사선 계측으로 과두흡수와 안면부 골격형태의 연관성을 한국인 정상 교합자들의 평균치와 비교 조사하였고, 전치부 개교합이 동반된 군과 개교합이 없는 군을 서로 비교하였으며, 또한 자기공명영상으로 과두흡수와 관절원판변위와의 관련성을 조사한 결과 과두흡수가 잘 발생될 수 있는 환자들은 다음과 같은 특징을 가졌다: (1) 34명중 1명만이 남자로 여자가 대부분이었다, (2) 연령대는 어느 연령에서나 발생가능하나 10대와 20대에서 발병률이 높았다, (3) 환자들은 높은 하악하연각과 높은 하악각을 가졌다. (4) 하악지의 높이는 작게 나타났으며, (5) 전악각 함요(antegonial notch)가 대체적으로 저명하였다, (6) 구치부 교합은 Angle's Class I 관계가 많았으나, ANB각도는 평균 5.54도로 하악의 후퇴를 나타내었다. (7) 과두흡수는 하악하연각이 낮은 경우에는 거의 발생하지 않았다, (8) 통계학적 유의한 차이는 없었으나 개교합이 동반된 군이 개교합이 없는 군보다 hyperdivergent한 골격형태를 가졌다, (9) 자기공명영상사진에서 과두흡수는 대부분 비정복성 관절원판전위와 연관되어 있었다. 수직적 골격성장이 큰 경우 관절원판 전방변위와 과두흡수의 원인이 될 수 있으리라 생각된다.

• 대한장애인치과학회지
• /
• 제15권1호
• /
• pp.65-69
• /
• 2019

본 증례는 유치열에 다수의 치아 우식증을 주소로 내원한 울프-허쉬호른 증후군 환자의 전신마취 하 치과치료에 대한 보고이다. WHS 환자의 특징적인 안모가 관찰되었으며, 발달지연, 정신 지체, 식이 장애 및 이로 인한 합병증 등을 보였다. WHS 환자는 다양한 전신 질환 및 선천성 기형 등을 동반할 수 있으므로, 치과 치료 시 전신적인 상태에 대한 평가가 필요하다. 또한 WHS 환자의 전신마취 시에는 기도 관리와 관련한 특별한 주의가 필요하며 치과 치료 후에도 주기적 관찰 및 지속적인 구강위생 관리 교육이 필요하다.

• 대한두개안면성형외과학회지
• /
• 제24권3호
• /
• pp.111-116
• /
• 2023

Background: In Indonesia, the prevalence of cleft lip and palate increased from 0.08% to 0.12% between 2013 and 2018. Children with cleft deformities typically undergo staged surgery. However, the coronavirus disease 2019 (COVID-19) pandemic has had negative impacts on the healthcare sector, including the suspension of elective procedures; this has raised concerns about the safety of performing surgery and the functional consequences of delaying treatment, the latter of which is associated with poor prognosis. The purpose of this study was to report the characteristics of clefts treated by the Bandung Cleft Lip and Palate Center team during the pandemic period. Methods: This brief comparative study based on a chart review was conducted at the Bandung Cleft Lip and Palate Center. We statistically evaluated data from all patients treated between September 2018 and August 2021. Frequency analysis was performed to analyze the average number of each procedure by age before and during the COVID-19 pandemic. Results: Data from 18-month periods before (n= 460) and during (n= 423) the pandemic were compared. Cheiloplasty procedures were examined (pre-pandemic, n= 230; pandemic, n= 248); before the pandemic, 86.1% were performed according to the treatment protocol (patient < 1 year old), and this proportion non-significantly dropped to 80.6% during the pandemic (p= 0.904). Palatoplasty procedures were also compared (pre-pandemic, n= 160; pandemic, n= 139); the treatment protocol (patient 0.5-2 years old) was followed for 65.5% of procedures before the pandemic and 75.5% during the pandemic (p= 0.509). Additionally, 70 (mean age, 7.94 years) revision and other procedures were performed before the pandemic and 36 (mean age, 8.52 years) during the pandemic. Conclusion: The cleft procedures performed at the Bandung Cleft Lip and Palate Center did not significantly change during the COVID-19 pandemic.

• 대한두개안면성형외과학회지
• /
• 제25권2호
• /
• pp.62-70
• /
• 2024

Background: The management of cleft lip and palate aims at improving the patient's aesthetic and functional outcomes. Delaying primary repair can disrupt the patient's functional status. Long-term follow-up is essential to evaluate the need for secondary repair or revision surgery. This article presents the epidemiology of cleft lip and palate, including comprehensive patient characteristics, the extent of delay, and secondary repair at our institutional center, the Bandung Cleft Lip and Palate Center, Faculty of Medicine, Universitas Padjadjaran, Bandung, Indonesia. Methods: This retrospective study aimed to determine the epidemiology and recurrence rates of cleft lip and palate at the Bandung Cleft Lip and Palate Center, Indonesia, from January 2007 to December 2021. The inclusion criteria were patients diagnosed with cleft lip and/or palate. Procedures such as labioplasty, palatoplasty, secondary lip and nasal repair, and alveolar bone grafting were performed, and data on recurrence were available. Results: In total, there were 3,618 patients with cleft lip and palate, with an age range of 12 months to 67 years. The mean age was 4.33 years, and the median age was 1.35 years. Males predominated over females in all cleft types (60.4%), and the cleft lip was on the left side in 1,677 patients (46.4%). Most cases were unilateral (2,531; 70.0%) and complete (2,349; 64.9%), and involved a diagnosis of cleft lip and palate (1,981; 54.8%). Conclusion: Delayed primary labioplasty can affect daily functioning. Primary repair for patients with cleft lip and palate may be postponed due to limited awareness, socioeconomic factors, inadequate facilities, and varying adherence to treatment guidelines. Despite variations in the timing of primary cleft lip repair (not adhering to the recommended protocol), only 10% of these patients undergo reoperation. Healthcare providers should prioritize the importance of the ideal timing for primary repair in order to optimize physiological function without compromising the aesthetic results.

• Journal of Korean Neurosurgical Society
• /
• 제44권4호
• /
• pp.240-244
• /
• 2008

Objective : Sotos Syndrome is characterized by macrocephaly, overgrowth, and developmental delay, and more than 300 patients have been reported worldwide to date. The authors reviewed the clinical characteristics of 8 patients with Sotos Syndrome in Korea for a new understanding and treatment strategies. Methods : The medical records of a total of eight Korean children with Sotos Syndrome were reviewed. All patients underwent developmental checkup, lumbar punctures for measurement of intracranial pressure (ICP), brain and spine magnetic resonance imaging and computerized tomography. Results : All 8 patients showed macrocephaly and the characteristic craniofacial features of Sotos Syndrome. Other clinical characteristics shown were overgrowth (7/8), developmental delay (7/8), congenital heart defect (3/8), flat foot (8/8), scoliosis (4/8), spina bifida (8/8), hydrocephalus (4/8), cavum vergae (3/8), and increased subdural fluid collection (5/8). Mean ICP measured via lumbar puncture was $27.35{\pm}6.25\;cm$ $H_2O$ (range 20 to 36 cm $H_2O$). Two patients received ventriculo-peritoneal shunt, and 1 patient underwent subduro-peritoneal shunt with improvement. Spinal orthosis was applied to 4/5 patients with scoliosis and 4/8 children with flat foot were provided with foot orthosis. Conclusion : In this first Korean study of 8 Sotos Syndrome patients we demonstrated the presence of spina bifida and increased ICP, which had not been previously described. The authors therefore suggest that all patients with Sotos Syndrome should undergo examination for the presence of spina bifida, and that shunt procedures would improve development and alleviate clinical symptoms.

• Clinical and Experimental Pediatrics
• /
• 제59권1호
• /
• pp.16-23
• /
• 2016

Purpose: The 1p36 deletion syndrome is a microdeletion syndrome characterized by developmental delays/intellectual disability, craniofacial dysmorphism, and other congenital anomalies. To date, many cases of this syndrome have been reported worldwide. However, cases with this syndrome have not been reported in Korean populations anywhere. This study was performed to report the clinical and molecular characteristics of five Korean patients with the 1p36 deletion syndrome. Methods: The clinical characteristics of the 5 patients were reviewed. Karyotyping and multiplex ligation-dependent probe amplification (MLPA) analyses were performed for genetic diagnoses. Results: All 5 patients had typical dysmorphic features including frontal bossing, flat right parietal bone, low-set ears, straight eyebrows, down-slanting palpebral fissure, hypotelorism, flat nasal roots, midface hypoplasia, pointed chins, small lips, and variable degrees of developmental delay. Each patient had multiple and variable anomalies such as a congenital heart defect including ventricular septal defect, atrial septal defect, and patent duct arteriosus, ventriculomegaly, cryptorchism, or hearing loss. Karyotyping revealed the 1p36 deletion in only 1 patient, although it was confirmed in all 5 patients by MLPA analyses. Conclusion: All the patients had the typical features of 1p36 deletion. These hallmarks can be used to identify other patients with this condition in their early years in order to provide more appropriate care.

• 치과방사선
• /
• 제27권1호
• /
• pp.231-241
• /
• 1997

The aneurysmal bone cyst is a nonmalignant reactive bone lesion. Developing rarely in the craniofacial region, and more commonly affecting the long bones and the spine, the lesion has variable etiopathogenic characteristics. The authors diagnosed a 33-year-old female as aneurysmal bone cyst after undergoing clinical, radiological and histological examinations. The characteristics were as followed: 1. The patient complained of pain and swelling of the right preauricular area. 2. The conventional radiograms showed a relatively well defined radiolucent lesion with partially scalloping margin. The cortical bone of the right condyle was thinned and expanded by the lesion. 3. Bone scintigraphy with ~c demonstrated ring-like or doughnut-pattern accumulation of radioactivity. 4. On Tl-weighted imaging of MRI, the lesion on the right condyle had middle signal intensity. T2-weighted MRI demonstrated multiple high signal intensities seperated by septa which had low signal intensity. Finger in balloon appearance was seen. 5. Histologically, the lesion was composed of large sinusoidal blood spaces lined by fibroblasts and histiocytes. Its fibrous stroma consisted of fibroblstic element, multinucleated giant cells, extravasated erythrocytes and focal hemosiderin pigmentation. New bone formation was also observed around larger sinusoidal spaces.

• Tuberculosis and Respiratory Diseases
• /
• 제47권2호
• /
• pp.218-230
• /
• 1999

연구배경: 두개안면 및 상기도의 해부학적 이상은 폐쇄성 수면 무호흡 발생과 밀접한 관련이 있는 것으로 알려져 있다. 저자들은 한국인 폐쇄성 수면 무호흡 증후군 환자가 지니고 있는 두개안면 및 상기도의 해부학적 특성을 평가하고, 폐쇄성 수면 무호흡의 발생을 예측함에 있어서 두개골계측분석의 임상적 유용성을 조사하고자 하였다. 방법: 폐쇄성 수면 무호흡 증후군 환자 39명(OSAS), 단순코골이 39명(simple snorers) 및 정상인 20명(control)을 대상으로 Riley 등의 방법을 이용한 두개골계측분석의 각 계측치와 수면다원검사의 각 지표와의 상호 관련성을 분석하였다. 결과: Pm-UPW길이와 V-LPW길이는 OSAS 및 simple snorers 에서 control에 비해 각각 유의하게 짧았으며 (p<0.01), PAS 깊이는 simple snorers가 control에 비해 짧았다 (p<0.05). ANS-Gn길이는 OSAS가 control에 비해 유의하게 길었고 (p<0.01), PNS-P길이는 OSAS 및 simple snorers가 control에 비해 각각 유의하게 길었다(p<0.01). MP-H길이는 OSAS가 control 및 simple snorers 에 비해 각각 유의하게 길었고 (p<0.01), simple snorers는 control에 비해 길었다(p<0.05). NL/Pm-P각도는 OSAS가 control 에 비해 작았다(p<0.05). MP-H길이는 OSAS에서 무호흡-저호흡지수와 유의한 상관관계가 있었으며 (r=0.561, p<0.01), OSAS와 simple snorers를 합한 대상에서도 MP-H 길이와 무호흡-저호흡지수는 유의한 상관관계가 있었다(r=0.511, p<0.01. PNS-P길이는 OSAS와 simple snorers를 합한 대상에서 무호흡-저호흡지수와 관련성이 있었다(r=0.286, p<0.05). 전체 대상에서 남자의 비만도가 PNS-P길이(r=0.355, p<0.01) 및 MP-H길이(r=0.460, p<0.01)와 유의한 상관관계가 있었다. 결론: 두개골계측분석은 폐쇄성 수면 무호흡 증후군의 원인이 될 수 있는 두개안면 및 상기도약 해부학적 특성을 평가할 수 있는 유용한 검사이다. 여러 가지 두개골계 측치중에서 설골의 위치를 나타내는 MP-H길이는 수면중에 발생 가능한 상기도의 협착 혹은 폐쇄 정도를 예측하는 자료로서 임상적 유용성이 높을 것으로 생각된다.

• 대한치과교정학회지
• /
• 제28권2호
• /
• pp.219-229
• /
• 1998

심한 골격성 III급 부정교합을 가진 성인환자는 많은 경우 심미성증진과 기능증진을 위해 악교정수술과 교정치료를 병행하여 치료하게 된다. 이러한 경우 진단과 치료계획 수립시 중요한 의미를 가지는 경조직 및 연조직 측모윤곽선의 형태를 정상교합자와 비교 분석하고, 두개악안면구조의 특성을 파악하여 부조화의 소재를 규명하고자 이 연구가 시행되었다. 골격성 III급 부정교합으로 진단된 환자 중 ANB각의 차이가 -2이하인 18세 이상의 성인남녀 환자 112명의 측모두부 규격 엑스선 사진을 연구자료로 이용하였으며 평균연령은 23.1세였다. 대조군으로는 성인 정상교합자 50명의 측모 두부 규격 엑스선 사진을 대상으로 하였으며 남, 녀 각 25명씩이었다. 전후방기준으로는 Nasion perpendicular to FH line을 사용하였으며, 수평 기준선으로는 FH line을 사용하였다. 이 연구에서 정상교합자와 비교한 심한 III급 부정교합자 안면골격의 특징을 다음과 같다. 1. 나지온점에서 프랑크프르트 수평선에 내린 수선을 기준선으로 III급 부정교합자의 경조직 측모 윤곽을 평가하였을 때, III급 부정교합자의 전두부, 상악의 전방돌출도는 정상과 유사하였으나, 하악은 정상에 비하여 심하게 돌출되어 있었다. 2. III급 부정교합자의 연조직 측모윤곽은 오목하였다. III급 부정교합자의 연조직 두께는 전두부에서는 정상과 차이가 없었으나, 상순은 두껍고 비상순각은 작았으며, 하순과 하순구부위의 연조직은 얇고 하순의 외번도는 작았다. 3. III급 부정교합자의 두개저(전방두개저의 길이, 후방두개저의 길이 및 안상각)는 정상에 비하여 작았다. 4. III급 부정교합자에서 두개저에 대한 중안면부(안와하연점)의 전후관계는 정상과 유사하였으나,중안면부의 길이는 짧았다. 5. III급 부정교합자에서 두개저에 대한 상악의 전후방관계는 정상과 유사하였으나 상악골의 길이는 짧았다. 6. III급 부정교합자에서 두개저에 대한 하악의 전후관계는 전방돌출되어 있었으며, 하악지 및 하악체 길이는 크고, 하악각이 크며, 이부각(Chin angle)이 작았다. 7. III급 부정교합자의 상악 절치는 전방경사되어 있었으며, 하악 절치는 설측경사되어 있었다.

• 대한소아치과학회지
• /
• 제26권1호
• /
• pp.172-184
• /
• 1999

The present study was performed to identify morphologic sub-groupings in Korean children with Class I malocclusions, and to find out anatomic differences between the sub-groups. Standardized lateral cephalometric radiographs of 152 Korean children, aged between 6 and 12 years, with Class I malocclusions were analyzed by the Counterpart Analysis. A statistical method, Ward's Minimum Variance Cluster Analysis, was employed to divide the sample into sub-groups those with similar morphologic characteristics. The results were as follows; 1. There appeared two facial types, Type I and Type II, in Korean children with Class I malocclusions, 48.7% and 51.3%, respectively. 2. In both sub-groups, there existed strong Class III skeletal patterns due to a counterclockwise rotation of the Middle Cranial Fossa alignment, and strong Class II skeletal patterns due to the long Posterior Maxillary vertical dimension and a clockwise rotation of the Ramus alignment. 3. There were no significant differences in Upper Anterior Facial Height between Type I and Type II, $52.6{\pm}2.92mm\;and\;52.8{\pm}3.23mm$, respectively. 4. The Lower Anterior Facial Height in Type II was longer ($66.0{\pm}4.03mm$) due to the long Posterior Maxillary vertical dimension, the clockwise rotation of the Ramus alignment, and a clockwise rotation of the Mandibular plane alignment than that of Type I ($64.2{\pm}4.15mm$).