• Clinical and Experimental Pediatrics
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• v.50 no.2
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• pp.209-212
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• 2007

Acrodermatitis enteropathica (AE) is a rare autosomal recessive disorder of early infancy, and is characterized by periorificial dermatitis, alopecia, and intractable diarrhea. Serum zinc levels are usually low in untreated patients and the oral administration of zinc sulfate can clear skin lesions and other symptoms. Although premature and cow's milk-fed infants are at particular risk of developing AE, there have been a few reports about AE in term and breast-fed infants. We report a case of transient AE in a 4-month-old breast-fed infant. This patient suffered from diarrhea and dermatitis for more than a month. Her skin lesions were erythematous, scaly, crusted, psoriasiform, eczematous, with an eruption at the chin, and a periorificial disposition with involvement of the flexural areas of lower extremities. Her serum zinc level was almost normal at $129{\mu}g/dL$ (reference range: $60-121{\mu}g/dL$), but the zinc level in her hair was low: 8 mg percent (reference range: 10-21 mg percent). Skin biopsy findings were consistent with AE. Seven days after zinc supplementation, the skin lesions and diarrhea improved. The authors recommend that a clinical trial of zinc supplementation be considered in cases where there are suspicious of AE, even when the serum zinc level is normal.

• Archives of Plastic Surgery
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• v.40 no.1
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• pp.36-43
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• 2013

Background Because there are numerous methods for reconstruction of the lower lip, it is not easy to choose the optimal method. In choosing the surgical method for lower lip reconstruction, we obtained acceptable outcomes based on our treatment strategy, which included either a barrel-shaped excision or the Webster modification of the Bernard operation. We report on the surgical outcomes based on our treatment strategy. Methods This study included 26 patients who underwent lower lip reconstructive surgery from September 1996 to September 2010. The operation was done using either a barrel-shaped excision or the Webster modification, considering the location of the defect, the size of the defect, and the amount of residual tissue on the lateral side of the vermilion after excision. Results In our series, 3 patients underwent a single barrel-shaped excision, and nine patients underwent a double barrel-shaped excision. In addition, the unilateral Webster modification was performed on in 6 patients, and there were eight cases of bilateral Webster modification. All of the patients except one were satisfied with the postoperative shape of the lip. In one case both recurrence and dehiscence occurred. One patient had a good postoperative lip shape, but had difficulty wearing a denture, and also underwent commissuroplasty. Furthermore, there were two patients who complained of drooling, and 4 with paresthesia. Conclusions A soft tissue defect resulting from wide excision of a lower lip malignancy can be successfully reconstructed using only one of two surgical methods: the barrel-shaped excision or the Webster modification of the Bernard operation.

• Tunnel and Underground Space
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• v.23 no.1
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• pp.13-30
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• 2013

Increase of pore fluid pressure resulting from injection of $CO_2$ may reactivate pre-existing faults, and the induced seismic activities can raise the safety issues such as seal integrity, restoration of storage capacity, and, in the worst case, removal of previously injected $CO_2$. Thus, fault stability and potential for $CO_2$ leakage need to be assessed at the stage of site selection and planning of injection pressure, based on the results of large-scale site investigations and numerical modeling for various scenarios. In this report, studies on the assessment of fault stability during injection of $CO_2$ were reviewed. The seismic activities associated with an artificial injection of fluids or a release of naturally trapped high-pressure fluids were first examined, and then site investigation methods for the magnitude and orientation of in situ stresses, the distribution and change of pore fluid pressure, and the location of faults were generally summarized. Recent research cases on possibility estimation of fault reactivation, prediction of seismic magnitude, and modeling of $CO_2$ leakage through a reactivated fault were presented.

• Clinics in Shoulder and Elbow
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• v.14 no.1
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• pp.1-5
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• 2011

Purpose: The purpose of this study was to evaluate the radiologic and clinical outcomes after operative treatment using endobuttons for unstable distal clavicle fractures. Materials and Methods: Between October 2007 and September 2009, 9 consecutive patients who were followed up for at least more than 12 months after operative treatment using a TightRope$^{(R)}$ were studied. The radiologic results on the serial plain radiographs and the clinical results according to the American Shoulder Elbow Surgeons (ASES) score were analyzed. Result: Bony union was shown in 8 cases (88.9%) and the average time to union was 12.9 (range: 9~16) weeks. The average coracoclavicular distances at the postoperative and final follow-up were 5.6 mm and 6.2 mm, respectively, with no statistically significant difference (p>0.05). The average ASES score was 90.3 (range: 78~96) and the clinical outcomes were 6 excellent, 2 good and one fair. There were no complications such as implant failure or infection except for one case of nonunion due to loss of the initial reduction. Conclusion: A major advantage of TightRope$^{(R)}$ fixation for unstable distal clavicle fractures is that no further surgery is needed to remove the implant. We suggest that this technique provides an alternative for fracture with a distal fragment, which is difficult to fix.

• Clinics in Shoulder and Elbow
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• v.13 no.2
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• pp.270-274
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• 2010

Purpose: Here we present tardy ulnar nerve palsy cases that were caused by the anconeus epitroch-learis muscle. Materials and Methods: A 37 year old female patient presented with tardy ulnar nerve palsy findings for the elbow. During surgery, an atypical anconeus epitrochlearis muscle was observed, which originated from the triceps aponeurosis and inserted into the medial intermuscular septum. Muscle resection, nerve decompression and ulnar nerve anterior transposition were done. A 35 year old male patient presented with tardy ulnar nerve palsy findings for the elbow. During surgery, a typical anconeus epitrochlearis muscle was found. Muscle resection, nerve decompression and ulnar nerve anterior transposition were done. Results and Conclusion: Tardy ulnar nerve palsy can be associated with and caused by either an atypical or a typical anconeus epitrochlearis muscle.

• Pediatric Infection and Vaccine
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• v.27 no.1
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• pp.77-82
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• 2020

Ascariasis is the most common helminthic infection in humans. However, its prevalence has been very low in Korea since the 1990s. Recently, there have been several case reports on intestinal obstruction or pancreaticobiliary disease due to infection with Ascaris lumbricoides in adults. However, cases of ascariasis in children have rarely been reported in Korea. We report a case of ascariasis in a 2-year-old boy who experienced expulsion of an adult ascaris worm from his anus. His mother found the worm in his diaper in the morning. His medical history was nonsignificant for any previous illnesses. There were no specific symptoms, and no abnormal findings were found on physical examination. The worm was pink, elongated, and cylindrical; it was 25 cm long and 5 mm wide. Unfertilized eggs of A. lumbricoides were detected in his stool specimen. He was treated with albendazole and remained asymptomatic at follow-up. As long as the number of immigrants from endemic areas and people returning from overseas trips, and import of agricultural products keep increasing, ascariasis can still occur in Korea. Therefore, it is necessary to raise awareness regarding ascariasis.

• Pediatric Infection and Vaccine
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• v.7 no.2
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• pp.250-256
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• 2000

The incidence of tuberculosis has been decreased, and especially the incidence of severe complicated tuberculosis has been markedly decreased as the result of widely used BCG vaccines. But tuberculosis is still an important community accquired infectiouse disease in the world despite continued worldwide efforts to control the disease. Miliary tuberculosis, the most serious complicated tuberculosis, can be occurred by lymphohematogenous dissemination of tuberculosis, and intracranial tuberculoma with or without tuberculosis meningitis can be developed in case of miliary tuberculosis. In general, serious tuberculosis infections such as miliary tuberculosis and CNS tuberculosis are developed especially in young infants and children in cases of delayed diagnosis and treatment despite receiving BCG vaccination, and usually those patients have contact sources. Intrcranial tuberculoma in children are usually found near infratentorial site at the base of cerebellum, and clinically symptoms and signs of increased intracranial pressure developed before treatment. Serial brain CT or MRI is a good non-invasive diagnostic modality of intracranial tuberculoma. Although surgical intervention was initially advocated as the mainstay of intracranial tuberculoma therapy, but many recent clinical studies indicate that intracranial tuberculoma can be cured with medical treatment alone. We experienced a case of 3 months old male patient, who was diagnosed as having miliary tuberculosis associated with multiple intracranial tuberculoma. He received BCG vaccination at 4 weeks after birth, and his father was confirmed as active pulmonary tuberculosis patient after this patient's admission. We report this case with a review of related literatures.

• Childhood Kidney Diseases
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• v.18 no.2
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• pp.128-131
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• 2014

Histopathologic evidence of "full-house" immune complex deposits is a pathognomonic feature of lupus nephritis. This report presents the case of a 12-year-old boy with persistent microscopic hematuria and proteinuria. He was diagnosed with "full-house" nephropathy based on a renal biopsy. However, there was no other clinical or biological evidence of systemic lupus erythematosus (SLE). Although the potential for isolated "full-house" nephropathy preceding SLE is unclear, such patients should be followed for clinical signs and autoantibodies of SLE. In most cases, microscopic hematuria has a good prognosis, and follow-up usually requires only regular urinalysis. However, we should be aware of isolated "full-house" nephropathy that remains asymptomatic for a long time, as few patients with no clinical signs and negative serology ultimately develop SLE.

• Childhood Kidney Diseases
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• v.18 no.1
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• pp.51-55
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• 2014

Primary renal artery aneurysm has been estimated to account for an incidence of 0.015-1% with associated morbidities including renovascular hypertension and rupture. Renovascular hypertension associated renal artery aneurysms in children is not a common disease. In patients with complicated renal vascular disease, renal autotransplantation has been used as an alternative to percutaneous transluminal angioplasty, which may be hazardous in these situations. We report a case of a renal artery aneurysm in a 13-year-old Korean child presenting hypertension detected during school health examination. Preoperative workup demonstrated a $2.8{\times}2.1{\times}1.9$ cm saccular aneurysm in the right renal hilum that was not amendable to endovascular repair. A surgical strategy including extracorporeal renal artery reconstruction with autotransplantation was applied in order to restore renal artery anatomy and to treat renovascular hypertension. Immediately he complained of severe right flank pain and postoperative doppler sonography revealed lack of perfusion. On the 5th day after autotransplantation, the patient underwent a transplant nephrectomy. He was well postoperatively and was found to have a normal kidney function and stable blood pressure control without antihypertensive medication. This is the first pediatric case of renal artery aneurysm in Korea who underwent extracorporeal repair followed by autotransplantation failure. More pediatric cases with renal artery aneurysm should be reported to identify therapeutic outcome and long term prognosis.

• The Journal of the Petrological Society of Korea
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• v.4 no.1
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• pp.20-30
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• 1995

We report major element chemistry of the Chuncheon amphibolite in the Precambrian Kyonggi massif and discuss its origin. On the basis of areal distribution and chemical difference, the Chuncheon amphibolite can be divided into the Gubongsan arnphibolite in the Gubongsan Group east of Chuncheon city and the Sangguli amphibolite in the Yongduri gneiss complex occurring to the southeast of the Gubongsan Group. Overall major element characteristics of the Chuncheon amphibolite indicate an igneous precursor, although it shows concordant relationship with metasedimentary rocks in many cases. The parental rock of the amphibolite has tholeiitic composition with 45-53wt% $SiO_2$. The Sangguli amphibolite has lower MgO than the Gubongsan one. The difference in $TiO_2$/P_2O_5 ratio between the two amphibolites suggests that they are not genetically related. In MgO variation diagrams, $Na_2O$, $Fe_2O_3$ and $Al_2O_3$ show scattered pattern, while MgO has positive correlation with CaO and negative one with $SiO_2$, $TiO_2$, $P-2O_5$ and $K_2O$. These variations can be interpreted as the result of differentiation of basaltic magma with fractionation of olivine, pyroxene, and plagioclase. Tectonic discrimination using major elements generally suggest withinplate environment for the Chuncheon amphibolite which is similar to that of the amphibolite in the Ogcheon belt.