• 제목/요약/키워드: Seoul National University Hospital

검색결과 7,282건 처리시간 0.046초

Hemophagocytic lymphohistiocytosis diagnosed by brain biopsy

  • Ju, Hee Young;Hong, Che Ry;Kim, Sung Jin;Lee, Ji Won;Kim, Hyery;Kang, Hyoung Jin;Park, Kyung Duk;Shin, Hee Young;Chae, Jong-Hee;Phi, Ji Hoon;Cheon, Jung-Eun;Park, Sung-Hye;Ahn, Hyo Seop
    • Clinical and Experimental Pediatrics
    • /
    • 제58권9호
    • /
    • pp.358-361
    • /
    • 2015

  • Hemophagocytic lymphohistiocytosis (HLH) is characterized by fever, splenomegaly, jaundice, and pathologic findings of hemophagocytosis in bone marrow or other tissues such as the lymph nodes and liver. Pleocytosis, or the presence of elevated protein levels in cerebrospinal fluid, could be helpful in diagnosing HLH. However, the pathologic diagnosis of the brain is not included in the diagnostic criteria for this condition. In the present report, we describe the case of a patient diagnosed with HLH, in whom the brain pathology, but not the bone marrow pathology, showed hemophagocytosis. As the diagnosis of HLH is difficult in many cases, a high level of suspicion is required. Moreover, the pathologic diagnosis of organs other than the bone marrow, liver, and lymph nodes may be a useful alternative.

  • https://doi.org/10.3345/kjp.2015.58.9.358 인용 PDF KSCI

Extracardiac Conduit Fontan Operation and Right Ventricular Exclusion Procedure for Right Ventricle Failure after Repair of Partial Atrioventricular Septal Defect

  • Yang, Chan Kyu;Jang, Woo Sung;Choi, Eun-Suk;Cho, Sungkyu;Choi, Kwangho;Nam, Jinhae;Kim, Woong-Han
    • Journal of Chest Surgery
    • /
    • 제47권3호
    • /
    • pp.275-279
    • /
    • 2014

  • A 13-year-old girl, who had undergone the total correction of partial atrioventricular septal defect at the age of 4 years, was admitted with severe tricuspid regurgitation in echocardiography. She had received one-and-a-half ventricle repair during follow-up. Her right ventricle showed global akinesia, and the ejection fraction of the left ventricle was 25% with paradoxical interventricular septal motion. We performed right ventricular exclusion adjunct to the Fontan procedure. She is doing well two years after the operation without complications.

  • https://doi.org/10.5090/kjtcs.2014.47.3.275 인용 PDF KSCI