• Advances in pediatric surgery
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• 제19권2호
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• pp.156-161
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• 2013

Congenital segmental dilatation of the colon is a very rare entity of unknown etiology, characterized by a localized dilatation of a bowel segment of the colon of variable length and an abrupt transition between the normal and dilated intestine. It can affect any part of the colon, with the rectosigmoid colon being the most commonly affected site. The clinical and radiological features may resemble that of Hirschsprung disease, but differ in that the normal ganglion cells are found in the dilated and normal segment of the colon. We performed laparoscopic-assisted transanal endorectal pull-through for segmental dilatation of rectosigmoid colon in an 8-year-old boy with chronic constipation since the age of 5 months.

• Advances in pediatric surgery
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• 제4권2호
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• pp.166-171
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• 1998

Segmental dilatation of the small intestine is a rare form of the congenital intestinal anomaly. Many other combined anomalies have been reported in, but the association with colonic duplication has not been reported in the literature. We report a case of segmental dilatation of the distal ileum associated with colonic duplication. The main clinical and pathogenic aspects are discussed, and the literatures are reviewed.

• Advances in pediatric surgery
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• 제1권2호
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• pp.181-185
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• 1995

Segmental intestinal dilatation is rare, which causes symptom of bowel obstruction and requires resection. The resection is not only diagnostic but also curative procedure. Recently, author experienced 2 cases of segmental dilatation of the ileum due to focal agenesis of the intestinal muscularis in 7 day & 4 day-old female neonates. The post operative recovery was excellant in the first case after resection of dilated ileum(15cm in length) and end to end anastomosis, and discharged at 20th day. But in the second case, the passage disturbance was not relieved after resection of dilated ileum (30cm in length), and author re-resected 80cm more of dilated proximal ileum at 2 weeks after the first operation. This baby discharged after diarrhea control with Loperin on 1 month after the second operation. Final histologic examination showed 1) normal population of ganglion cells in both narrowed & dilated ileum in both cases. 2) focal abscence of muscularis propria in both cases. 3) relative hypertrophy of inner circular muscle layer and thinned, multiple fragmented outer longitudinal muscle layer in case 2.

• Advances in pediatric surgery
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• 제1권1호
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• pp.68-72
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• 1995

Segmental dilatation of the colon is a very rare disease entity of unknown etiology and may mimic Hirschsprung's disease. It is characterized by dilatation of a segment of the colon of variable length with obstruction due to lack of peristalsis in a normally innervated intestine. Recently authors experienced a case of segmental dilatation of the sigmoid colon in a 6 month-old male, who presented with severe constipation, abdominal distention, and abdominal mass since 2 months of age. Down's syndrome and congenital nystagmus were associated. Barium enema demonstrated focal dilatation of the sigmoid colon, but the rectum and descending colon proximal t o the affected colon were of normal caliber. Rectal suction biopsy with acetylcholinesterase staining was normal and anorectal manometry showed normal rectosphincteric reflex. At operation, there was a massively dilated and hypertrophied sigmoid colon with increased tortuous serosal vessels, measuring 15 cm in length and 10 cm in width. Teniae coli were identifiable in the affected segment. Frozen section biopsies at the proximal, affected, and distal colon showed ganglion cells. Descending loop colostomy was constructed initially and segmental resection and end to end colocolostomy were carried out 3 months later. Final histologic examination showed 1) normal colonic mucosa with ganglion cells, 2) prominent submucosal fibrosis and marked muscular hypertrophy, 3) unremarkable acetylcholinesterase activity and immunohistochemical findings against S-100 protein. On 8 months follow-up, he has been doing well and moves bowels 1-2 times daily.

• 대한한방내과학회지
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• 제26권4호
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• pp.912-917
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• 2005

Caroli's disease is a non-obstructive dilatation of the intrahepatic bile ducts. It is a rare congenital disorder that classically causes saccular ductal dilatation, which usually it segmental dilatation. Caroli's disease is associated with recurrent bacterial cholangitis and stone formation. A 57 years-old female inpatient suffering from cholangitis due to Caroli's disease was admitted at Wonkwang University Jeonju Oriental Medicine Hospital. The patient was treated with herbal medicine such as Yongdamsagan-tang and acupuncture. As result, there was improvement of symptoms. The process and content of treatment and the patient's recovery over general symptoms is described.

• Journal of Chest Surgery
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• 제28권7호
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• pp.698-703
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• 1995

Dextrocardia means right-sided position of the heart in the chest irrespective of the cause. For the absolute diagnosis of the dextrocardia, the segmental analysis of heart is necessary. Once the segmental analysis of the dextrocardia is made, it is often relatively easy to identify the presence of any associated defects based on conventional methods including physical examination, EKG, echocardiography, and angiocardiography. Two cases of dextrocardia with congenital heart disease were treated surgically.A eleven - months old boy was operated under diagnosis of ASD, VSD, and bilateral SVC with mirror - image dextrocardia {I,L,I} by primary closure of ASD and VSD.A twenty-four months old girl was operated under diagnosis of ASD, VSD, and PS with corrected TGA {I,D,D} by primary closure of ASD, VSD and dilatation of pulmonary stenosis. Both of them were discharged healthily after operation.

• Journal of Chest Surgery
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• 제6권2호
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• pp.151-158
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• 1973

Author studied the pathogenesis of Sino-bronchiectasis with review of clincal and pathological findings of resected lungs in 24 eases of bronchiectasis,and the results were as follows: 1. Of the 24 eases of bronchiectasis, Sino-bronchiectasis were found in 11 cases and these cases most commonly, developed in first and second decade of life. In a majority of these cases,the main symptoms were the signs of wet bronchiectasis. 2. The typical roentgenograrn changes of plain chest x rays were increase in size and loss of definition of the markings and bronchographically revealed the cylindrical or tubular form in majority of these cases. 3. Pathologically Sino-bronchiectasis involved specific segmental areas of the lungs such as left basal and S4+5 segments and revealed commonly tubular dilatation. The most common findings of bronchial wall of dilated bronchus were the inflammatory cellular infiltration and cylindrical hyperplasia of mucus epithelial layers. 4. It was suspected that there were some causal relations in pathogenesis between chronic sinusitis and bronchiectasis.

• Journal of Chest Surgery
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• 제19권4호
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• pp.688-694
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• 1986

Takayasu`s disease is an arteritis of unknown etiology involving larger elastic arteries such as aorta and its branches, pulmonary arteries and rarely coronary arteries. Especially, aortic root involvement with the valvular leaflets has been reported in several cases of Takayasu`s arteritis. Recently we have experienced one case of Takayasu`s arteritis involving left subclavian artery, descending aorta, left renal artery and multiple valvular leaflets. The patient was 33 year-old female and admitted with complaints of cough, dyspnea and general weakness. Aortogram revealed extensive type of arteritis showing dilatation of ascending aorta, segmental narrowing of thoracic aorta and Riolan`s anastomosis. Double valve replacement [mitral and aortic valve] and tricuspid valve annuloplasty were performed. The patient made an excellent postoperative recovery and has shown striking improvement in cardiac status, NYHA functional class II eight months after operation.

• The Korean Journal of Pain
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• 제6권2호
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• pp.265-269
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• 1993

Subdural block is a rare but well recognized complication of epidural anesthesia. The placement of local anesthetics into the subdural space can lead to potentially life-threatening conditions. A healthy 46-year-old women underwent total abdominal hysterectomy under continuous lumber epidural anesthesia. The technical procedure for continuous epidural catheterization went smoothly without a single problem. However, signs of high epidural block such as apnea, cranial nerve paralysis and pupil dilatation developed gradually, about 20 minutes after the epidural injection of 2% lidocaine 20 ml through the epidural catheter. Such extensive segmental block can only be explained as the result of injection into subdural space even if it was not confirmed radiologically.

• Journal of Chest Surgery
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• 제37권7호
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• pp.617-621
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• 2004

양성 식도협착에 대한 분절절제술 및 단단문합술은 식도-장관 문합술에 비해 수술침습도가 적고 식도 고유기능을 보존할 수 있으므로, 짧은 분절의 식도협착에서 수술방법으로 고려해야 하지만 임상 보고나 분석에 대한 연구는 매우 적은 실정이다. 본원 흉부외과에서는 수술 후 문합부 협착이 있는 13개월 여아와 부식성 식도협착이 있는 27세 여자를 대상으로 단단문합술을 적용한 임상경험을 하였기에 보고하는 바이다. 생후 2일째 식도무형성증-식도기관누공에 대한 수술 후 발생한 문합부 협착인 경우는 결과가 좋았으나, 경부 식도의 고도 부식성협착에서는 단단문합술 후 다시 협착이 재발하여 인후-대장-위 문합술을 시행하게 되었다. 양성 식도협착에 대한 단단문합술은 협착의 범위와 원인에 따라 적응증을 선택하여 사용된다면 좋은 치료 방법이라고 생각하나 더 많은 연구가 필요하리라 생각한다.