• Journal of the Korean Association of Oral and Maxillofacial Surgeons
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• v.36 no.5
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• pp.434-437
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• 2010

A melanotic neuroectodermal tumor of infancy (MNTI) is a uncommon osteolytic pigmented neoplasm that primarily affects the jaws of newborn infants. Most patients (> 90%) present with the tumor in the first year of life. Approximately 65% form in the maxilla, 11% in the mandible, 5% in the brain and elsewhere. MNTI is normally benign, but up to 15% may recur and a few have metastasized. Approximately 200 cases of MNTI have been reported but only 2 of them presented as multifocal. A case of MNTI in a 7 month old boy was encountered. The chief complaint was maxillary anterior ridge swelling. The incisional biopsy findings were MNTI. Two months after the first operation, mild swelling of another site was observed. The infant was examined periodically since undergoing two procedures with no recurrence. This case demonstrates the possibility of a multicentric MNTI. We report a multicentric MNTI with a review of the relevant literature.

• Journal of Dental Anesthesia and Pain Medicine
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• v.15 no.3
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• pp.161-165
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• 2015

Long QT syndrome (LQTs) is a rare congenital disorder of the heart's electrical activity. Patients with LQTs are at increased risk of developing fatal ventricular arrhythmias. Elevated levels of sympathetic stimulation can exacerbate this risk. Successful behavior management is indispensable in the treatment of patients with LQTs. However, many drugs involved in pharmacologic behavior management are known to adversely affect the QT interval. Therefore, careful selection of a sedative drug is essential in avoiding such incidences. A 10-year-old boy with a known diagnosis of LQTs required restorative treatment due to dental caries at the permanent molar. He required sedation since treatment was painful and dental phobia can trigger sympathetic stimulation, creating a dangerous situation for patients with LQTs. Therefore, the treatment was performed over two sessions under moderate sedation involving propofol combined with nitrous oxide. Restorative treatment was successful without any complications under sedation with a target-controlled infusion (TCI) of propofol. There was no significant QT prolongation during pulpal treatment. Propofol TCI may be a good candidate for sedation in patients with LQTs.

• Korean Journal of Health Education and Promotion
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• v.22 no.2
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• pp.173-193
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• 2005

Objectives: The purpose of this study is to analyze the peer group factor related to adolescent smoking in the social structure(network) of adolescent groups, by applying the theory of social network. Methods: The data was collected from boy students of one high school located in Gun-Po city of Kyonggi Province. The total number of the sample was 605(223 first grade, 198 second grade, 184 third grade). The survey using the questionnaire was carried out in April 2005. Social position is finally classified as clique member, liaison, isolate group by using the NetMiner II 2.5 version. Results: The current smoking rate was 15.0%, and the life-time smoking rate was 34.9%. The smoking rate increased significantly, as the grade went up. And it was significantly high among the group having smoking friends. The logistic regression analysis showed that the odds ratio of the smoking friends group was about 4 times higher than the no smoking friends group in experience of smoking. But the smoking rate was higher significantly in the isolate group within the network composed of 2. person's social-link. The odds ratio of the isolate group was about 4.5 times higher than the clique member. However, this pattern was not found in the network composed of 3 person's social-link. Therefore, the hypothesis that clique member would have a correlation with smoking was rejected. In reality, the isolate group had a tendency of smoking more frequently. Conclusions: The result of this study suggests that the role of the peer group in smoking is to be considered in the prevention program. More attentions should be paid for the isolate group.

• Pediatric Gastroenterology, Hepatology & Nutrition
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• v.18 no.2
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• pp.138-143
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• 2015

Glycogen storage disease type IX (GSD IX) is caused by a defect in phosphorylase b kinase (PhK) that results from mutations in the PHKA2, PHKB, and PHKG2 genes. Patients usually manifest recurrent ketotic hypoglycemia with growth delay, but some may present simple hepatomegaly. Although GSD IX is one of the most common causes of GSDs, its biochemical and genetic diagnosis has been problematic due to its rarity, phenotypic overlap with other types of GSDs, and genetic heterogeneities. In our report, a 22-month-old boy with GSD IX is described. No other manifestations were evident except for hepatomegaly. His growth and development also have been proceeding normally. Diagnosed was made by histologic examination, an enzyme assay, and genetic testing with known c.3210_3212del (p.Arg1070del) mutation in PHKA2 gene.

• Pediatric Infection and Vaccine
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• v.14 no.2
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• pp.194-198
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• 2007

The PFAPA syndrome is characterized by periodic fever, malaise, aphthous stomatitis, pharyngitis and cervical lymphadenitis without long-term sequelae. It has been known as one of the cause of periodic fever in children. Because there is no specific laboratory findings, the diagnosis of PFAPA syndrome is not only made by exclusion of diseases which are related to the other causes of periodic fever, but also made by a careful history and characteristic clinical manifestations. The dramatic response to the single oral dose of corticosteroid is unique to this syndrome. The PFAPA syndrome tends to be resolved without any long-term adverse sequelae. We have reported a 3 year old boy who was diagnosed as having PFAPA syndrome by episodes of periodic fever for 3 months and by excluding other febrile diseases. He was treated with oral prednisolone and his symptoms had been improved dramatically.

• Journal of the Korean Society of School Health
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• v.23 no.1
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• pp.53-62
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• 2010

Purpose: Adolescent obesity is a growing problem. This study examined the relationships between different types of physical activity and obesity in male and female middle and high school students. Methods: This study used the Korea National Health and Nutrition Examination Survey data of 2007. The study included 282 male and female middle and high school students who completed health survey questionnaires regarding physical activity. Physical activity was measured with vigorous and moderate activity and walking. BMI was used as an obesity indicator. Analyses were done using descriptive statistics, ANOVA, and chi-square test. In addition, multiple logistic regression were conducted to investigate the relationship between physical activity and obesity when adjusting for covariates. SAS/WIN 9.1 was used. Results: Boys spent more days in vigorous and moderate physical activity than girls (p for vigorous activity: <.001, for moderate activity: <.001). There was no significant difference in walking activity between boys and girls and between middle and high school students. Only days spent in vigorous activity was significantly higher in middle school student compared with high school students (p=.013). According to the relationship between physical activity and obesity, moderate physical activity was significantly related to BMI for high school boys (p=.041). However, when adjusting for age, sex, school, parental income, daily caloric intake, physical activity was not significantly related to obesity. Conclusions: The results showed that male and female middle and high school students spent not enough days in doing low moderate and vigorous physical activity. Thus, this strengthens the need to increase physical activity level in these populations. In spite of non-significant relationship between physical activity and obesity from multivariate analysis, increasing moderate physical activity for high school boy could be effective to prevent and manage obesity, since significant difference between moderate activity and obesity in this population.

• Journal of the Korean Home Economics Association
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• v.47 no.9
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• pp.15-26
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• 2009

The main purpose of this study was to speculate how psychological state of adolescent students has changed their school uniform style. For the study, the distinctive characteristics during adolescence stage were theoretically examined. Through the examination, this study found four interests in fashions and school uniforms. For the purpose, this study conducted interviews with grade 2 students in a total of six coeducation secondary schools in Seoul, Gyeongki and Gwangju using a questionnaire. The survey period ranged from December 15 2008 to December 24 2008 and a total of 1196 were used for a final analysis. This study extracted factors as Principal Components Analysis and used Varimax for orthogonal rotation analysis. To measure confidence, it used Cronbach's a test to item internal consistency. For data analysis, it used SPSS WIN 12.0 and for hypothesis analysis, frequency analysis, cross analysis, independent t-test, and one-way ANOVA were conducted. For posterior analysis, it used Sheffe test. The results are as follows: First, the interests in fashion and school uniforms differed depending on their own tastes, but these interests were more influenced by environment around school. Secondly, the boy subjects were more aggressive towards repairs their uniforms than the girls, which suggested that boys had stronger desire to show themselves to others and more satisfaction from repairs their uniforms than the girls. Based on the results, this study concluded as follows: We should pay attention to preventing deformation in original design of school uniforms while expanding options to have variable designs or to change detailed part of design. So, there will be no additional uniform mending expense and financial loss to parents, and students will be more satisfied with their school uniforms.

• Parasites, Hosts and Diseases
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• v.44 no.4 s.140
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• pp.355-360
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• 2006

Cutaneous leishmaniasis (CL), due to Leishmania major, is endemic in different parts of Iran and has long been recognized in most provinces of Iran. This study was conducted to determine the prevalence of childhood leishmaniasis in 3 areas at the southeast of Kashan, A descriptive study was carried out on all children referred to central laboratories during a 3-year period. Initial information including age, sex, sites of ulcer on the body, number of lesions, address, and the place of the disease was obtained. The study gathered 117 children, and the results showed a prevalence of 7.2% in patients with lesions among the population and 4.2% of people displayed lesion and scar. The ages of subjects were from 6 to 15 years (average 9.75 years). The boy: girl ratio was 1.2. All of our patients lived in an endemic area. The face was affected in 47.0% of cases. The encountered forms of leishmaniasis are as follows: papulonodular 27.4%, ulcer 60.7%, sporotrichoid 6%, impetiginous 2.5%, and erysipeloid 3.4%. Treatment with intramuscular meglumine antimoniate 20-30 mg/kg/day was done for 93 patients. Meglumine antimoniate treatment was tolerated with no side effects. All leishmaniasis lesions healed within an average period of 2-14 months. Hyperpigmented scars were formed in 25.6% of the patients, atrophic scars in 4.3%, and hypopigmented scars were in 3.4%, respectively The findings of this study indicate increased prevalence of CL in the villages at the area of Kashan and Aran-Bidgol. The clinical finding patterns belonged to different endemic strains of L. major in Isfahan, which indicates the possible transmission of infection from Isfahan to this area.

• Clinical and Experimental Pediatrics
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• v.54 no.10
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• pp.425-428
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• 2011

Ornithine transcarbamylase (OTC) deficiency is well known as the most common inherited disorder of the urea cycle, and 1 of the most common causes of hyperammonemia in newborns. We experienced a case of a 3-day-old boy with OTC deficiency who appeared healthy in the first 2 days of life but developed lethargy and seizure soon afterwards. His serum ammonia level was measured as > $1,700{\mu}g/dL$ (range, 0 to $45{\mu}g/dL$). Continuous renal replacement therapy (CRRT) in the mode of continuous venovenous hemodiafiltration was immediately applied to correct the raised ammonia level. No seizure occurred after the elevated ammonia level was reduced. Therefore, CRRT should be included as 1 of the treatment modalities for newborns with inborn errors of metabolism, especially hyperammonemia. Here, we report 1 case of successful treatment of hyperammonemia by CRRT in a neonate with OTC deficiency.

• Pediatric Gastroenterology, Hepatology & Nutrition
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• v.13 no.2
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• pp.199-203
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• 2010

Sigmoid volvulus may cause acute or subacute colonic obstruction. Excessive length of the sigmoid colon may be a contributing factor. Typically, the patient develops bilious vomiting and marked gaseous abdominal distension. We report a case of sigmoid volvulus in a 9-year-old boy who presented with recurrent, sudden onset abdominal pain, abdominal distension, and vomiting for 1 year, which was diagnosed by simple abdominal X-ray, barium enema, computed tomography, and colonoscopic examination. Colonoscopic reduction failed and a sigmoid colectomy with primary repair was performed. The intra-operative findings showed that the sigmoid colon was noted to be dilated, and redundant with a lax mesentery. Two clear areas of compression (proximal and distal) were present. After sigmoidectomy, the symptoms resolved. After 5 years of follow-up, he had no new symptoms.