• Title/Summary/Keyword: Infantile myofibromatosis

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Infantile Myofibromatosis of the Skull - Case Report - (두개골 유아 근섬유증 - 증례보고 -)

  • Park, Byoung Jun;Koh, Young Cho;Yoo, Heon Yoo;Lee, Chea Heuck;Park, Hyo Il
    • Journal of Korean Neurosurgical Society
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    • v.29 no.3
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    • pp.430-433
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    • 2000
  • Infantile myofibromatosis is a rare and benign myofibroblastic tumor that may occur in either solitary or multicentric form in the soft tissue of infants. A 13-month-old girl presented with a painless firm mass, measuring $2.5{\times}2.5cm$ in the right temporal area. Skull X-ray and CT scan revealed a well enhancing soft tissue tumor with a round skull defect and sclerotic margin. The tumor was totally excised with curettage of the skull defect followed by cranioplasty. Pathology was confirmed to be a solitary infantile myofibromatosis. We report this rare solitary infantile myofibromatosis of the temporal bone with review of the pertinent literature.

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A Case of Infantile Myofibroma in the Pre-auricular Area (전이개에 발생한 유아성 근섬유종 1례)

  • Kim, Deok Su;Jang, Gyu Ho;Kim, Jeong Kyu
    • Korean Journal of Head & Neck Oncology
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    • v.32 no.2
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    • pp.9-13
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    • 2016
  • Infantile myofibromatosis is a rare benign neoplasm which is usually found in males. Most cases of the infantile myofibromatosis are discovered before the age of two years and about half of cases are found at muscle, tendon, and soft tissue of head-neck region. However, it is especially uncommon that infantile myofibroma occurs at the pre-auricular area. In current case, we report a twenty two months old male patient with $2.5{\times}1.5cm$ sized pre-auricular mass at right side. It was surgically removed and histologically showed broad bundle of plump myoid spindle cells with eosinophilic cytoplasm and weakly positive smooth muscle actin expression in myoid cells. In three months of follow up, there was no recurrence.