• Journal of Chest Surgery
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• 제27권1호
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• pp.57-59
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• 1994

Ebstein`s anomaly, a rare congenital cardiac anomaly, is characterized by downward displacement of abnormal tricuspid valve. Indication for surgical repair and the optimal surgical approach are still controversy. Recently, we experience a case of Ebstein anomaly, which was treated by atrilized right ventricular plication and annuloplasty. The patient was discharged with good result on 17th post-operative day.

• Journal of Chest Surgery
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• 제25권8호
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• pp.826-831
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• 1992

Ebstein`s anomaly is characterized by a downward displacement of a malformed tricuspid valve, The ideal surgical management of Ebstein`s anomaly is not yet established. Recently we experience one case of Ebstein`s anomaly, which was treated sussessfully by partial artificial annulus formation, and tricuspid valve replacement with St. Jude Medical valve. We have achieved excellent results with mechanical valve replacement and partial artificial annulus formation using wessex pericardial patch. On follow up for 4 years, the patient is well and in functional class I.

• Journal of Chest Surgery
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• 제53권5호
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• pp.243-249
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• 2020

Ebstein anomaly is a rare congenital heart malformation typically involving the tricuspid valve and the right ventricle that has a wide range of anatomical and pathophysiological presentations. Various surgical repair techniques for Ebstein anomaly have been reported because of its near-infinite anatomical variability. Cone repair for Ebstein anomaly can achieve nearly anatomical reconstruction of the tricuspid valve with promising outcomes. In this article, the surgical techniques for cone repair in adult patients with Ebstein anomaly are described in detail, and clinical experiences and technically challenging cases are presented.

• Journal of Chest Surgery
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• 제35권11호
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• pp.817-821
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• 2002

Ebstein기형은 수술적 교정을 위한 여러 가지 변형된 방법들이 소개되고 있지만 수술 후 잔존하는 삼첨판막 역류와 우심부전에 대한 문제는 여전히 남아있다. 본원에서는 심방조동이 동반된 Ebstein기형을 가지고 있는 19세의 남자 환자에 있어서 주름 성형술 없이 간단한 방법으로 삼첨판막 성형술을 시행하였고 양 방향성 상대정맥 -폐동맥 단락술 및 하대정맥 삼첨판 협부의 냉동절제 등을 성공적으로 시행하였기에 문헌고찰과 더불어 증례 보고하는 바이다.

• Journal of Chest Surgery
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• 제13권4호
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• pp.435-441
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• 1980

Ebstein`s anomaly had been amenable to reparative surgery since 1962. However, neither the role of surgery in Ebstein`s anomaly nor the surgical procedure of choice for its correction are clearly defined. Whether or not the atrialized right ventricle, which plays a major role in the functional abnormalities, should be obliterated in all cases remains unsolved. Four cases of Ebstein`s anomaly treated surgically at Seoul National University Hospital were reported. All had closure of the atrial septal defect, obliteration of the atrialized right ventricle by plication, and insertion of a tricuspid bioprosthesis and an epicardial ventricular pacemaker. One patient had a pulmonic valvotomy due to stenotic bicuspid pulmonic valve also. All but one had discharged with a good result.

• Journal of Chest Surgery
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• 제24권9호
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• pp.907-912
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• 1991

Isolated primary tricuspid insufficiency except Ebstein`s anomaly is rare disease. Recently we experienced two cases of isolated primary tricuspid insufficiency and treated successfully with annuloplasty or valve replacement. We could not classify our case as one of the classification of isolated tricuspid insufficiency, because the morphology and microscopic finding did not suggest any similar variety.

• Journal of Chest Surgery
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• 제42권4호
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• pp.509-512
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• 2009

엡스타인 기형은 다양한 형태의 삼첨판막 및 우심실의 이상을 나타내는 선천성 심기형이다. 동반되는 삼첨판막의 역류를 교정하기 위하여 다양한 성형술식들이 사용되고 있으나, 대부분은 전염만을 이용한 단일판막화 술식이다. 저자들은 엡스타인 기형을 가진 31세 여자 환자에게 세개의 판막엽들을 모두 이용하는 cone 재건술로 삼첨판막 성형술을 시행하여 좋은 결과를 얻었기에 보고하는 바이다.

• Journal of Chest Surgery
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• 제29권11호
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• pp.1202-1206
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• 1996

Ebstein기형은 삼첨판, 우심실 및 우심방의 특징적인 변형를 보이는 희귀한 선천성 심질환으로, 삼첨판의 후판막첨과 중격판막첨이 우심실로 나선형의 변형을 보이는 것이 특징적이다. 본 교실에서는 1988년 1월 1일부터 1995년 12월 31일까지 7년간 11명의 환자를 경험하였으며 평균연령은 29.6$\pm$11.1세, 성비는 남자 5명 여자 6명이었고, 주증상으로는 운동시 호흡곤란이었다. 모든례에서 삼첨판의 전형적인 변형을 보였으며 동반된 심기형으로는 개방성 난원창, 심방중격결손, 심실중격결손이 있었다. 9명은 Danielson씨 삼첨판성형술과 주름성형술을 시행하고 2명은 삼첨판막치환술과 주름성형술을 시행하였으며 동반된 심기형을 교정하였다. 수술후 5명의 환자에서 저심박출증, 부정맥, 창상감염 등의 합병증이 발생하였으며 수술사망례는 없었다. 술후 평균 33.3개월의 추적관찰 결과 모든 환자에서 술전보다 양호한 심기능을 보였다.

• Korean Circulation Journal
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• 제54권2호
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• pp.78-90
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• 2024

Background and Objective: We aimed to investigate long-term clinical and echocardiographic outcomes, including tricuspid valve durability, annular growth, and left ventricular reverse remodeling, after modified cone reconstruction in patients with Ebstein's anomaly. Methods: This was a retrospective analysis of all pediatric patients who underwent modified cone reconstruction for Ebstein's anomaly at a single tertiary center between January 2005 and June 2021. Results: A total of 14 pediatric patients underwent modified cone reconstruction for Ebstein's anomaly; the median age was 5.8 years (range, 0.01-16.6). There were three patients (21.4%) with Carpentier type B, ten patients with Carpentier type C (71.4%), and one patient with Carpentier type D (7.1%). There was no early or late mortality, arrhythmia, or readmission for heart failure at a 10-year follow-up. There were no cases of more than mild tricuspid stenosis or more than moderate tricuspid regurgitation during the study period, except for one patient with severe tricuspid regurgitation who underwent reoperation. The z value for tricuspid valve annular size significantly decreased immediately after the operation (2.46 vs. -1.15, p<0.001). However, from 1 year to 7 years after surgery, the z values were maintained between -1 and +1. Left ventricular end-systolic volume, end-diastolic volume, and stroke volume increased after surgery and remained elevated until seven years postoperatively. Conclusions: Ebstein's anomaly in children can be repaired by modified cone reconstruction with low mortality and morbidity, good tricuspid valve durability, and annular growth relative to somatic growth.

• Journal of Chest Surgery
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• 제18권3호
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• pp.391-397
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• 1985

Ebstein`s anomaly is a rare congenital cardiac malformation and characterized by downward displacement of an abnormal tricuspid valve cusps. But until now, the ideal surgical correction is still controversial. We present a case of Ebstein`s anomaly experienced lately. The patient was 13 year old girl with the complaints of dyspnea on exertion, fatigability and cyanosis. Echocardiography revealed downward displacement of septal leaflet of tricuspid valve and atrialized right ventricle. Cardiac catheterization and cineangiography revealed ASD and large right atrium. During operation, the atrialized right ventricle was plicated and tricuspid annuloplasty was done. And the two secundum type ASD`s were closed by direct suture closure. The patient`s postoperative course was uneventful and discharged on the 24th postoperative days.