• Tuberculosis and Respiratory Diseases
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• 제66권1호
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• pp.58-61
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• 2009

기관지 Dieulafoy 질환은 기관지 점막 하부에 위치하는 일종의 동맥기형으로서, 일반적인 방사선적 및 기관지 내시경 검사에서 원인 불명의 대량 객혈 환자에서 감별 진단에 고려되어야 할 질환이다. 기관지 동맥 조영술이 진단에 도움이 될 수 있으며, 객혈의 조절을 위해 우선적으로 시도될 수 있지만, 반복적인 대량 객혈의 위험으로 외과적 절제술이 가장 효과적인 치료 방법이다. 저자들은 대량객혈로 내원하여 외과적 절제술 후 기관지 Dieulafoy 질환으로 확진된 환자 1예를 경험하였기에 문헌 고찰과 함께 보고하는 바이다.

• Pediatric Gastroenterology, Hepatology & Nutrition
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• 제2권1호
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• pp.80-84
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• 1999

Dieulafoy's disease, a vascular anomaly mainly in the upper stomach, is a rare but potentially life-threatening cause of upper gastrointestinal bleeding. Pathogenesis is still controversial, but the most accepted theory is that a persistent caliber vessel in the submucosa is exposed by a small mucosal erosion leading to massive bleeding. The bleeding site is usually within 6 cm of the esophagogastric junction in the cardia or fundus of the stomach. The treatment of choice is therapeutic endoscopy or surgery. The age of patients reported is mainly between 50 and 70 years, and patients of pediatric age are extremely rare. We are reporting a 5-year-old male patient who had Dieulafoy's disease which was diagnosed by emergency upper gastrointestinal endoscopy. Endoscopic finding was a nodular lesion with an adherent clot on the lessor curvature of the stomach 2 cm below the esophagogastric junction. Epinephrine and $Beriplast^{(R)}$ was injected in the lesion. On the second day after endoscopic sclerotherapy, the patient had recurred massive hematemesis and accompanying shock. So we performed gastrotomy and ligation. After the operation, he showed an improved general condition and was discharged at the 12th hospital day.