• Journal of Chest Surgery
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• 제28권7호
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• pp.726-730
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• 1995

Congenital cystic adenomatoid malformation[CCAM of the lung is extremely rare. We have experienced an unusual case of congenital cystic adenomatoid malformation. The patient was 20-year-old male and had chest pain for 10 days. On simple chest x-ray and Thoracic CT scan, there was a large cystic mass surrounded with multiloculated round cysts with air fluid level on the right lower lobe of a lung. Right lower lobectomy was performed and the pathologic result was congenital cystic adenomatoid malformation.

• Journal of Chest Surgery
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• 제24권8호
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• pp.819-823
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• 1991

The congenital cystic adenomatoid malformation of the lung is a rare disease, and is one of the most common congenital lung diseases which require prompt surgical intervention. The prognosis depends on its tissue type, prompt diagnosis and surgical intervention. The lesion consists of enlarged, variable sized multiple cyst with overgrowth of terminal bronchioles, like hamartoma. This disease can be associated with other vascular anomalies or other congenital defect especially in type II lesion We recently experienced one case of congenital cystic adenomatoid malformation The patient was 2 months old infant who showed respiratory distress without associated anomaly. After right upper lobe lobectomy, the patient was recovered uneventfully.

• Tuberculosis and Respiratory Diseases
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• 제55권1호
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• pp.107-112
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• 2003

A congenital cystic adenoid malformation of the lung(CCAM) is characterized by an anomalous fetal development of the terminal respiratory structures, resulting in the adenomatoid proliferation of the bronchiolar elements and cystic formation. CCAM has been detected on the fetus, premature babies and stillborn as well as infants and children. An adult presentation of CCAM is extremely rare. When cystic lesions occur with a repeated infection, an evaluation of the cystic lesions requires a differential diagnosis of CCAM, sequestration, a lung abscess, a pneumatocele and a bronchogenic cyst. The definite treatment of CCAM is the surgical removal of the involved lobe. We report a case of a CCAM in a 24-year-old female with a brief review of the relevant literature.

• Journal of Chest Surgery
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• 제49권3호
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• pp.210-213
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• 2016

Congenital cystic adenomatoid malformation is a rare, but well-known disease. It can be managed conservatively in patients without symptoms or require surgical removal when symptomatic. The surgical option of choice is en bloc resection of the affected lesion. We report an experience of life-threatening congenital cystic adenoid malformation in a low-birth-weight (1,590 g) premature neonate who was successfully treated with a lobectomy of the lung.

• Advances in pediatric surgery
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• 제2권2호
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• pp.138-142
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• 1996

Pulmonary sequestration is a complex anomaly involving the pulmonary parenchymal tissue and its vasculature. It presents as a cystic mass of nonfunctional lung tissue without communication with the tracheobronchial system. Usually, it receives blood supply from anomalous systemic vessels. Therefore, preoperative diagnosis of the pulmonary sequestration is difficult, especially when it is located in the abdomen and combined with congenital cystic adenomatoid malformation(CCAM). We encountered such a mass(CCAM type 2) detected prenatally by ultrasonography. It was a kidney bean shaped, pinkish mass straddling the thorax and abdomen on the right side. Because of the sonographic appearance, neuroblastoma was diagnosed preoperatively. The mass was completely extirpated without difficulty.

• Clinical and Experimental Pediatrics
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• 제49권7호
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• pp.796-799
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• 2006

편측성 다낭성 신 이형성증과 폐의 선천성 낭성 선종양 기형은 각각 독립된 질환으로 배아 시기에 발생 과정의 문제로 생긴다고 알려져 있다. 폐의 선천성 낭성 선종양 기형에서 폐 외의 기형으로 신장 기형이 동반될 수 있으나 생존 가능성이 적어 사산아로 출생되는 경우가 많다. 저자들은 위장관염으로 입원한 21개월 남아에서 우연히 편측성 다낭성 신 이형성증을 발견했고, 이 과정에서 폐의 선천성 낭성 선종양 기형도 발견하였기에 보고하는 바이다.

• Journal of Chest Surgery
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• 제13권3호
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• pp.292-297
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• 1980

The congenital cystic adenomatoid malformation of the lung consists of an enlarged, meaty, multicystic lobe with smooth-walled cysts of varying sizes, which can communicate with major bronchi through malformed air passages that usually lacks cartilage. This abnormality is usually symptomatic in infancy with signs of respiratory distress such as tachypnea, substernal retraction and cyanosis. Prompt surgical resection is choice of treatment in life-threatening respiratory distress patients. We recently experienced a case of congenital cystic adenomatoid malformation of the lung in a patient with situs inversus totalis. The patient was 40 days old female who showed severe respiratory difficulty. Emergency left middle lobectomy was undergone successfully. Her postoperative course was uneventful. She was discharged from hospital on the postoperative eighth day in good condition.

• Journal of Chest Surgery
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• 제26권4호
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• pp.320-324
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• 1993

Congenital cystic adenomatoid malformation [CCAM] of the lung is extremely rare. The patient was 10 year old female and had no specipic signs and symptoms except right lower chest pain for 5 days ago before admission.On simple chest X-ray and thoracic CT scan, about 9x8x8cm sized, heterogenous marginal enhanced multiseparated hypodence lesion with air fluid level and gas bubbles in posterior pleural space in right lower chest .The culture result of needle aspiration of cavity was apergillus flavus. Right lower lobectomy was carried out and the result of biopsy was congenital cystic adenomatoid malformation.

• Journal of Chest Surgery
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• 제33권7호
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• pp.594-596
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• 2000

선천성 낭종성 선종양 기형과 외엽형 폐격리증은 아주 드문 질환이다. 본원에서는 4세 된 여자환자에서 좌폐화엽의 선천성 낭종성 선종양 기형을 수술하던 중 우연히 외엽형 폐격리증이 동반된 것을 알고 좌폐하엽 절제술과 외엽형 폐격리증 절제술을 시행하였는데, 외엽형 폐격리증은 흉부대동맥에서 비정상적으로 직접 1개의 동맥으로 유입되고, 늑간정맥을 통하여 기정맥으로 유출되었다. 환자는 수술 후 건강하게 퇴원하였다.

• Journal of Chest Surgery
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• 제28권2호
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• pp.196-200
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• 1995

Congenital Cystic Adenomatoid Malformation [C.C.A.M. is rare, cause acute respiratory distress in the newborn infants. The histologic features are cystic areas and marked proliferation of terminal respiratory structures. On case 1, the patient was 8-month-old male, and suffered from acute respiratory distress and cyanosis. The pulmonary cystic lesion was detected in right lung at birth and has been evaluated since birth. The study for diagnosis were chest x-ray and chest CT. A right upper lobectomy was urgently performed and he was discharged with a satisfactory postoperative course. On case 2, the patient was 20-year-old female, and suffered from cough and sputum for 2 months. The study for diagnosis were chest x-ray, chest CT, and pulmonary angiography. The cystic lesion was detected in left lung and difficult to distinguish from pulmonary sequestration. A left lower lobectomy was performed and she was discharged with a satisfactory postoperative course. We report two cases of C.C.A.M. with differential clinical course.