• Title/Summary/Keyword: Congenital atresia

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Congenital Esophgeal Anomaly -6 Cases- (선천성 식도 폐쇄증 -치험 6례-)

  • 최진호
    • Journal of Chest Surgery
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    • v.28 no.6
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    • pp.637-639
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    • 1995
  • Congenital esophageal anomaly with or without tracheoesophageal fistula was rare congenital disease.We experienced 6 cases of congenital esophageal atresia, with tracheoesophageal fistula [5 cases and one esophageal atresia without fistula, were treated in the Department of Thoracic and Cardiovascular Surgery, Kangnam Sacred Heart Hospital, Hallym university, from May, 1992 to July, 1994. The type of four cases were upper blind pouch and lower tracheo or broncho esophageal fistula and one case H-type fistula with no esophageal atresia, and the one case was esophageal atresia without fistula. We performed modified Haight`s method, one case was primary closure with feeding gastrostomy and stomach interposition. Three were died due to respiratory failure on 7 and 9th postoperative days.Three were recovered uneventfully.

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Congenital Esophageal Atresia: Report of Four Cases (선천성 식도폐쇄증 4례 보고)

  • 노준량
    • Journal of Chest Surgery
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    • v.5 no.2
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    • pp.153-158
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    • 1972
  • The esophageal atresia with tracheoesophageal fistula occurs approximately once in 3, 000 live births. In Korea, about 20 cases were reported with five successful surgical corrections. The atresia characteristically occurs at the level of, or just cephalad to, the carina and is associated with a tracheoesophageal fistula. In about 90% of the cases, the upper esophagus ends in a blind pouch, and the lower esophageal segment communicates with the trachea through the membranous posterior wall just above the carina. Many of the Infants with esophageal atresia have other congenital anomalies. The most common of these are congenital cardiac anomalies, imperforate anus, genitourinary malformations, and intestinal atresia. Recently we experienced four cases of esophageal atresia, of which three were Gross type C and one was type A. Two of them were treated by primary repair, and one [type A] was taken cervical esophagostomy and gastrostomy. The another was refused surgery.

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Suryical Treatment of Congenital Esophayeal Atresia without Tracheoesophageal Fistula -A Case Report of Staged Operation- (기관 식도루가 없는 선천성 식도 폐쇄)

  • 김영대
    • Journal of Chest Surgery
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    • v.27 no.12
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    • pp.1052-1055
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    • 1994
  • Congenital esophageal atresia without tracheoesophageal fistula which called isolated esophageal atresia is a very rare entity and the neonate classified as category C by Waterston`s classification has high mortality rate. We experienced a case of isolated esophageal atresia. This patient was a male with 1,750gm in body weight and had been suffered from bilateral pneumonia. The patient was managed with staged operation. Feeding gastrostomy was made as the first intervention and delayed primary anastomosis was performed 3 months later. The postoperative course was uneventful and he was discharged on the 22nd postoperative day.

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Congenital bronchoesophageal fistula without esophageal atresia in adults-report of 5 cases- (성인에서 발생된 선천성 식도기관지루 수술 치험: 5례 보고)

  • 김주현
    • Journal of Chest Surgery
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    • v.16 no.3
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    • pp.381-385
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    • 1983
  • Congenital bronchoesophageal fistula without esophageal atresia is very rare and often has an insidious clinical course that occasionally persists into adult life. Here are presented five cases of congenital bronchoesophageal fistula without esophageal atresia in adults treated successfully in the Seoul National University Hospital. The patients included two women and three men in the range of 16 and 45 years old. [mean age: 32 years old] Three of five cases could be diagnosed preoperatively by esophagogram and bronchogram but two of them could only be found in operative field. Cineesophagogram is recommended, on review of the literature, to be the most rewarding diagnostic procedure.

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Congenital Esophgo-bronchial Fistula without Esophageal Atresia in the Adult -A Case Report- (성인의 선천성 식도 기관지루 -수술치험 1례 보고-)

  • Kim, Byeong-Rin;O, Tae-Yun;Jang, Un-Ha
    • Journal of Chest Surgery
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    • v.28 no.4
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    • pp.431-436
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    • 1995
  • Congenital esophago-bronchial fistula without atresia is very rare and usually demonstrate more insidious clinical effects, and patients may reach adult life before the diagnosis. We had been experienced a typical case of esophago-bronchial fistula without atresia and document the case. A 42-year-old women was admitted to our hospital due to frequent choking symptom and attacks of pneumonia, and patient status was in chronic pulmonary infection status such as most probably bronchiectatic state of right middle & lower lobe including significant destructive changes. We had confirmed esophago-bronchial fistula without atresia with esophagoscopy, esophagogram, and chest CT, and performed esophago-bronchial fistulectomy and right middle & lower lobectomy. Its belongs to type II of Braimbridge`s classification for congenital esophago-bronchial fistula. Postoperation course was smooth and uneventful.

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A Clinical Study of Congenital Intestinal Atresia and Stenosis (선천성 장폐쇄 및 협착에 대한 임상적 고찰)

  • Kim, Sang-Woo;Jung, Poong-Man
    • Advances in pediatric surgery
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    • v.3 no.2
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    • pp.117-125
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    • 1997
  • Seventy neonates with congenital intestinal atresia and stenosis who were treated at pediatric surgical service. Hanyang University Hospital from September 1979 to December 1996 were analyzed retrospectively. The lesion occurred in 27 cases at the duodenum, in 26 cases at the jeiunum, in 13 cases at the ileum and in 2 cases at the pylorus and colon each. There were 10 multiple atresias and 7 apple-peel anomaly cases. The atresia predominated over the stenosis by the ratio of 4 : 1. Male to female ratio was 1.3 : 1. The average gestational age was 38 weeks, and the average birth weight was 2,754 grams. Though 22.9 % were borne prematurely and 34.3 % had low birth weight, 92.3 % of them had a weight appropriate for gestational age. Polyhydramnios(40 %) was more frequently observed in duodenal and jeiunal atresia while microcolon in ileal atresia(58.3 %). Weight loss and electrolyte imbalance occurred more frequently in the duodenal stenosis cases because of delayed diagnosis. Twenty(55.6 %) of 37 jeiunoileal atresia cases had evidence of intrauterine vascular accident : 4 intrauterine intussusception, 3 intrauterine volvulus and 3 strangulated intestine in gastroschisis, and 10 cases of intrauterine peritonitis. There were one or more associated anomalies in 45 patients (64.3 %). Preoperatively proximal loop volvulus developed in 3 cases and proximal loop perforation in 5 cases and one case each of distal loop perforation, duodenal perforation and midgut volvulus occurred in the jeiunoileal atresia. Overall mortality rate was 20 %.

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A Case of Congenital Laryngeal Atresia with Single Umbilical Artery Who Required a Tracheotomy (기관절개술을 받았던 단일 제대동맥이 동반된 선천성 후두폐쇄증 1례)

  • Wi, Ho Sung;Baek, Hey Sung;Oh, Jae Won;Yum, Myung-Kul;Kim, Yong Joo;Moon, Soo Jee;Tae, Kyung;Kim, Chang-Ryul
    • Clinical and Experimental Pediatrics
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    • v.48 no.5
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    • pp.557-560
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    • 2005
  • Congenital laryngeal atresia is a rare cause of airway obstruction that is almost always lethal within a few minutes after birth. Therefore congenital laryngeal atresia should be diagnosed in the prenatal period. If not, it should be considered in newborn infant with life-threatening symptoms at birth such as cyanosis and dyspnea that need emergent procedures like a tracheotomy. We report a case of congenital laryngeal atresia with single umbilical artery diagnosed in a one-day-old neonate who required a tracheotomy and ventilator care after intubation failure.

A Case of Coronary Sinus Atresia with a Total Anomalous Cardiac Venous Drainage to the Left Atrium without Persistent Left Superior Vena Cava: Imaging Findings on Cardiac CT (지속성 좌상대정맥을 없이, 좌심방으로 연결되는 전관상정맥환류이상과 동반된 관상정맥동 입구폐쇄 1예: 심장전산화단층촬영 소견)

  • Sang Hun Baek;Eun-Ju Kang;Ki-Nam Lee
    • Journal of the Korean Society of Radiology
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    • v.82 no.4
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    • pp.982-987
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    • 2021
  • The coronary sinus (CS) is the venous drainage system of the heart. CS ostium atresia is a rarely seen cardiac malformation. Congenital atresia of the CS is usually found together with persistent left superior vena cava (LSVC) and other cardiac malformations. However, isolated congenital atresia of the CS is very rare. We present a rare case of isolated congenital atresia of the CS connecting the left atrium and coronary veins without persistent LSVC in a 58-year-old female.

Surgical treatent of esophageal atresia with tracheo-esophageal fistula (기관 식도루를 동반한 선천성 식도 폐쇄증의 외과적 치료)

  • 김동원
    • Journal of Chest Surgery
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    • v.27 no.7
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    • pp.603-609
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    • 1994
  • Esophageal atresia is a rare congenital anomaly and it usually associated with tracheo-esophgeal fistula and other congenital anomalies. The first report of esophageal atresia with tracheo-esophageal fistula was done by Thomas Gibson in 1696. In 1941, Haight performed the first successful primary anastomosis for esophageal atresia. These accomplishments opened the gateway for clinical studies that have resulted in reinforcements and improvement in the care of infants born with this anomaly. From January 1986 to April 1994, 14 cases of esophgeal atresia with tracheo-esophgeal fistula were diagnosed in Kyung Hee Uinv. Hospital. There were 9 male and 5 female infants. 12 infants were Gross classification type C and 2 infants were type A. The average body weight was 2.7$\pm$0.4kg and Waterson Category A contained 4 infants, B contained 3 infants and C contained 7 infants. Among these infants, 9 infants were underwent anastomosis procedures. We performed retropleural approach in 6 infants, transpleural approach in 2 infants and 1 infant was performed colon interposition through substernal space.By the method of anastomosis, end-to-side anastomosis was performed in 5 infants, end-to-end anastomosis in 3 infants and esophagocologastrostomy in 1 infant.The former 8 infants were Gross classification type C and the latter was type A. Among the type C infants, 6 infants were anastomosed with one layer interrupted suture and 2 infants with 2 layer interrupted suture. Post- operative death was in 1 infant and 8 infants were discharged with good result and have been in good condition.

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