• Korean Journal of Radiology
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• 제22권10호
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• pp.1690-1696
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• 2021

Objective: To describe the anatomic locations and imaging features of posterior lung herniation in unilateral pulmonary agenesis and aplasia, focusing on radiograph-CT/MRI correlation. Materials and Methods: A total of 10 patients (seven with pulmonary agenesis and three with pulmonary aplasia, male: female = 1:9, mean age 7.3 years, age range from 1 month to 20 years) were included. Chest radiographs (n = 9), CT (n = 9), and MRI (n = 1) were reviewed to assess the type of lung underdevelopment, presence of anterior and posterior lung herniation, bronchus origin, supplying artery, and draining vein of the herniated lung. Results: Pulmonary agenesis/aplasia more commonly affected the left lung (n = 7) than the right lung (n = 3). Anterior lung herniation was observed in nine of the 10 patients. Posterior lung herniation was observed in seven patients with left pulmonary agenesis/aplasia. Two patients showed posterior lung herniation crossing the midline but not beyond the aorta, and five patients showed the posteriorly herniated right lower lobe crossing the midline to extend into the left hemithorax farther beyond the descending thoracic aorta through the space between the esophagus and the aorta. This anatomical configuration resulted in a characteristic radiographic finding of a radiolucent area with a convex lateral border and a vertical medial border in the left lower lung zone, revealing a tongue-like projection on CT and MRI. Conclusion: Posterior lung herniation occurs in unilateral left lung agenesis/aplasia. Approximately 70% of the cases of posterior lung herniation reveal a unique radiolucent tongue-like projection in the left lower lung zone on imaging studies, which is caused by the extension of the posteriorly herniated right lung farther beyond the descending aorta.

• 한국임상수의학회지
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• 제34권4호
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• pp.283-286
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• 2017

A 4-month-old, female Maltese dog was referred with continuous heart murmur. Patent ductus arteriosus was diagnosed via radiography and echocardiography. The patient was untreated because of client's refusal. After 13 months, the dog was referred again with seizure and salivation. Laboratory examination revealed increased liver enzymes, hyperammonemia and decreased total cholesterol and total protein. Microhepatica was identified on abdominal radiography. CT angiography showed a shunt vessel that originated from the portal trunk to the prehepatic caudal vena cava and patent ductus arteriosus connecting proximal descending aorta with the main pulmonary artery. No portal vasculature toward liver is observed after shunt vessel. The patient was diagnosed as concurrent patent ductus arteriosus and congenital extrahepatic portosystemic shunt with suspected portal vein aplasia. In human, cardiac malformations are frequently observed in patients with congenital extrahepatic portosystemic shunt with portal vein aplasia. This report described concurrent patent ductus arteriosus and congenital extrahepatic portosystemic shunt with suspected portal vein aplasia in a dog.

• Childhood Kidney Diseases
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• 제12권1호
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• pp.111-115
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• 2008

저자들은 특별한 가족력이 없으면서 저칼슘혈증, 저인산혈증, 경련, 혈청 알칼리성 인산분해효소의 증가, 1,25-$(OH)_2$ 비타민 D3 농도의 감소, 혈청 부갑상선 호르몬 농도의 증가 및 방사선 소견상 전형적인 구룻병 병소의 소견을 보인 제 1형 비타민 의존성 구룻병 환아에서 일측성 신장 무형성증이 동반되어 있었던 1례를 경험하였기에 문헌고찰과 함께 보고하는 바이다.

• Archives of Plastic Surgery
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• 제33권5호
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• pp.672-675
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• 2006

Purpose: The purpose of this study is to document the surgical methods used in infants with aplasia cutis congenita treated with allogenic dermal matrix and cultured epithelial autografts. Methods: The large defects in both lower legs were replaced with allogenic dermal matrix to avoid the postoperative hypertrophic scar contracture and a full-thickness skin biopsy was taken from right groin area simultaneously. We sent the specimen to a commercial laboratory for culture and obtained cultured epithelial autografts($Holoderm^{(R)}$) after 2 weeks, placed it over the allogenic dermal matrix. Results: The skin-defected area were nearly epithelialized after 2 weeks and there were no significant problem on during 6 months follow-up. Conclusion: The surgical method using allogenic dermal matrix and cultured epithelial autograft provided an excellent coverage of large skin defects of infant with aplasia cutis congenita.

• Journal of Yeungnam Medical Science
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• 제9권2호
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• pp.422-426
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• 1992

저자들은 회귀하고도 사망율이 높은 선천성 피부결손증 1례를 경험하고 국소피판과 피부이식으로써 치료하고 비교적 만족한 결과를 얻었기에 문헌고찰과 함께 보고하는 바이다.

• Journal of Yeungnam Medical Science
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• 제10권2호
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• pp.493-505
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• 1993

저자들은 1예의 선천성 피부결손증을 경험하고 국소피판술과 피부이식으로써 치료하고 술후 발생된 부분적 괴사는 습윤치료로써 자연치유시켜 만족스러운 결과를 얻었고, 4예의 craniosynostosis 환자를 진단하고 modified Marchac's method, Persing's method를 이용하고 교정하였고 CT를 이용한 뇌용적 측정으로 예후를 판정할 수 있었다.

• Journal of Chest Surgery
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• 제50권2호
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• pp.119-122
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• 2017

Pure red cell aplasia (PRCA) and hypogammaglobulinemia are paraneoplastic syndromes that are rarer than myasthenia gravis in patients with thymoma. Good syndrome coexisting with PRCA is an extremely rare pathology. We report the case of a 50-year-old man with thymoma and PRCA associated with Good syndrome who achieved complete PRCA remission after thymectomy and postoperative immunosuppressive therapy, and provide a review of the pertinent literature.

• 대한수의학회지
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• 제57권4호
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• pp.253-255
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• 2017

A 2-year-old, female Pomeranian dog was referred for dyspnea. Thoracic radiographs revealed left-sided mediastinal shift, increased soft tissue opacity in the caudal aspect of left thorax with loss of the left diaphragmatic silhouette, and dorsal elevation of mediastinal structures and heart from the sternum by lung tissue. The left main bronchus was visualized as an air-bronchogram and observed to abruptly discontinue at the level of the 10th rib. Thoracic computed tomography (CT) revealed absence of the left lung parenchyma and left pulmonary vessels with a rudimentary left main bronchus. The case was congenital pulmonary aplasia diagnosed via radiography and CT.

• 대한수의학회지
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• 제59권3호
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• pp.171-173
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• 2019

Two dogs presented with vomiting and head pressing. In both dogs, a large vessel was revealed in computed tomography (CT) angiography, which was found to leave the portal vein (PV) cranial to the splenomesenteric confluence and enter the pre-hepatic caudal vena cava cranial to the right renal vein. The flow of portal blood to the liver was not identified. Based on CT angiography, the dogs were suspected to have congenital PV aplasia with portocaval shunting. Diagnostic imaging of potential malformations for PV continuation should be conducted before attempting shunt closure.

• 한국임상수의학회지
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• 제32권2호
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• pp.196-199
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• 2015

유선종양의 병력이 있는 7년령의 중성화하지 않은 암컷 닥스훈트견과 중성화하지 않은 수컷 요크셔테리어견이 유선종양의 전이평가와 정기 검진을 위해 내원하였다. 두 증례 모두에서 복부 컴퓨터단층촬영 검사가 실시되었으며, 후대정맥 분절 무형성증이 우연히 발견되었다. 닥스훈트견은 복강내의 신후-후대정맥 분절이 결손되었고, 요크셔테리어견은 신전-후대정맥 분절이 신후-후대정맥 분절과 연속되지 않았다. 두 증례 모두에서 장골 정맥의 합류로 형성된 신전-후대정맥 분절이 확장된 홀정맥으로 연속되었다. 개에서 컴퓨터 단층촬영을 이용하여 복강내 혈관 기형을 평가할 때, 우연히 발견될 수 있는 후대정맥 분절 무형성증을 고려해야 한다.