• Journal of Genetic Medicine
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• v.21 no.1
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• pp.14-21
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• 2024

Infantile nystagmus syndrome (INS) refers to congenital forms of nystagmus that are present at birth or during infancy. This syndrome may be caused by afferent visual system disorders or abnormal development of the ocular motor system. INS is a genetically heterogeneous disorder for which there are more than 100 causative genes. Since applying clinical tests for the differential diagnosis of INS can be challenging in early infancy and children, genetic testings such as next-generation sequencing are becoming more important for achieving accurate diagnoses. An improved understanding of the molecular mechanisms of INS may also lead to the development of gene-based therapies for INS. These advantages of genetic testing have the potential to change the diagnostic paradigm of patients with INS. However, the diagnostic pathway based on genetic testing still has several limitations in terms of the therapeutic effect and methodology. This review summarizes genetic and clinical features of INS, and discusses the promise and pitfalls of genetic testing in INS.

• Journal of the Korean Society for Nondestructive Testing
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• v.21 no.5
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• pp.556-560
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• 2001

Remote field eddy current testing (RFECT) with through-wall transmission characteristic is being applied to pipes ranging from small tubes of heat exchanger to natural gas supply pipelines. Cast iron pipes with nominal diameter of 100mm are used primarily as the waterline pipes. The leakage of water occurs due to defects in the pipes caused by vibration of automobiles and corrosion. But, the use of direct inspection methods such as insertion of inspection equipment inside the pipelines has been limited due to its lack of economical efficiency. Economical development of inspection equipments is possible since RFECT method can be easily employed for system integration and quantitative evaluation of both inside and outside defects. In this study, the development of underground pipeline inspection system was tarried out by using RFECT method in consideration of the characteristics of waterline network. This paper specifically describes the design and production of RFECT pipeline inspection pig using centralizer mechanism, development of remote field eddy current signal acquisition and processing software, and review of RFECT system operation procedures.

• Journal of the Korean Society for Nondestructive Testing
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• v.29 no.2
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• pp.137-144
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• 2009

In this paper, the signal analysis of eddy current array probe was performed to analyze the electromagnetic characteristics with the variation of FBH(flat bottomed hole) defects size on steam generator tube in NPP(nuclear power plants) using the electromagnetic finite element method. To obtain the electromagnetic characteristic of probes, the governing equation was derived from Maxwell's equations, and the individual problem was analyzed by using the 3-dimensional finite element method. For the simulation FBH defects were used. The depth of FBH defects were 20%, 40%, 60%, 80% and 100% of steam generator(SG) tube thickness, and it was assumed that the defects were located on the tube outside. And the operation frequencies of 100 kHz, 300 kHz and 400 kHz were used. Material of specimen was Inconel 600 which is usually used for SG tubes in NPP. The signal difference could be observed according to the size variation of depth of FBH defects and operation frequencies. The results in this paper can be helpful when the ECT(eddy current testing) signals from EC array probe are evaluated and analyzed.

• Analytical Science and Technology
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• v.25 no.2
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• pp.102-113
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• 2012

Our study researched on unification of KS I ISO standard harmonized with ISO and Official Test Method enacted by Korean Ministry of Environment-drinking water and indoor air quality. We reviewed KS methods related to drinking water and indoor air quality for about 23,000 KS methods. KS methods related environmental field are classified as KS I, total 635 methods and 583 KS I methods were harmonized with ISO. For Environmental Standard methods for drinking water, 100 methods were reviewed according to 232 KS methods related to ISO/ TC 147 "Water Quality". Environmental Standard methods for indoor air quality were reviewed according to 95 KS standard methods related to ISO/TC 146 "Air Quality". By reviews and comparison tests for unifiable ES for drinking water and indoor air quality with KS methods harmonized with ISO, it was evaluated that for 100 ES methods for drinking water, 23 ES methods were unification complete, 29 ES methods were unification possible, 12 ES methods were unification impossible, no corresponding methods were found in KS I ISO for 36 ES methods and for 17 ES methods for indoor air quality,1 ES methods were unification complete, 3 ES methods were unification possible, 3 ES methods were impossible, no corresponding methods were found in KS I ISO for 10 ES methods.

• Journal of the Korea Organic Resources Recycling Association
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• v.25 no.1
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• pp.47-55
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• 2017

The technology for hydrothermal reaction of organic waste is one of the promising process to improve energy efficiency of biomass waste recycling system since moisture contents of treated biomass could be reduced at 40% or less than by dehydration processes. For these reasons, many parts of the world are interested in hydrothermal reaction of organic waste. In this paper, drying performances were evaluated with and without hydrothermal reaction of organic wastes which are sewage sludge and food wastes. For the hydrothermal reaction, organic wastes were treated at $200^{\circ}C$ for 1hr. Drying time of treated organic waste by hydrothermal reaction was reduced. In case of food waste drying at $100^{\circ}C$, drying time of treated wasted was reduced more 52.9% than non-treated. Hence, drying performances of sewage sludge and food wastes should be improved by hydrothermal reaction. Drying rates of treated wastes were considerably increased at preheat period of drying characteristic curve as followings; at $80^{\circ}C$ sludge as 148%, $100^{\circ}C$ sewage sludge as 151%, $80^{\circ}C$ food waste as 209%, $100^{\circ}C$ food waste as 366%. It means the surface area of treated wastes could be increased with destruction of cell membrane by hydrothermal reaction. However, the designer and operator of drying process should be careful, since enhanced drying rate cause the extension the decreasing drying period.

• Journal of Bio-Environment Control
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• v.22 no.2
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• pp.162-166
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• 2013

The objective of this study was to investigate the influence of fertilization levels by soil testing on plant growth and fruit quality of musk melon in greenhouse cultivation. Leaf area and fruit weight were severely affected by fertilization level. Leaf areas were significantly reduced by 54.1% and 24.5% at 0 and 50% fertilization level compared to the 100% fertilization level, respectively. Fruit weights were reduced by 38.2% and 19.9% at 0 and 50% fertilization level compared to the 100% fertilization level, respectively. However, soluble solids and sucrose contents were increased by 1.8% and 23.3% at 50% fertilization level compared to the 100% fertilization level, respectively. These results suggest that reduction of 50% fertilization level by soil testing seem to be effective methods to reduce salt accumulation in the soil as well as increasing of fruit quality such as soluble solids and sucrose contents.

• Journal of the Korean Society for Nondestructive Testing
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• v.18 no.1
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• pp.42-45
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• 1998

원유 또는 가스 생산을 위해 해상에 설치되는 플랜트 해양설비는 크게 jacket과 module로 나눌 수 있다. Jacket은 module을 지지하기 위한 구조물로써 jacket 본체와 pile로 구성되어 있으며, 미국용접학회(AWS)의 규정에 의해 대부분의 맞대기 완전용접 이음부(full penetration butt welds)에 대해 100% 방사선투과검사를 실시하게 되어 있다. 그러나 지금까지 방사선투과검사를 실시해 온 경험으로 미루어 볼 때 방사성에 대한 안전성, 생산공정의 영향(검사지연) 등 방사선투과검사는 많은 문제점을 가지고 있었다. 이에 대한 문제점을 해소하고, 국내의 비파괴검사 기술 향상을 위해 자동 초음파탐상 system을 개발, 방사선투과검사를 자동 초음파탐상검사로 대체하여 적용한 사례를 간략하게 기술하였다. 또한, 적용 확대를 위해 개방중인 system을 소개하고 아울러 자동 초음파탐상기술에 대한 앞으로의 방향을 제시하였다.

• Journal of Electrical Engineering and Technology
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• v.7 no.5
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• pp.778-783
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• 2012

The synthetic short-circuit making test to adequately stress the circuit breaker has been specified as the mandatory test duty in the IEC 62271-100. The purpose of this test is to give the maximum pre-arcing energy during making operation. And this requires the making operation with symmetrical short-circuit current that is established when the breakdown between contact gap occurs near the crest of the applied voltage. Also, if the interrupting chamber of circuit breakers is designed as the type of common enclosure or the operation is made by the gang operated mechanism that three-phase contacts are operated by one common mechanism, three-phase synthetic making test is basically required. Therefore, several testing laboratories have developed and proposed their own test circuits to properly evaluate the breaker performance. With these technical backgrounds, we have developed the new alternative three-phase making circuit.

• Journal of Korean Society for Atmospheric Environment
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• v.16 no.1
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• pp.69-77
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• 2000

This paper summerizes the results of the first proficiency testing program for achieving the analytical quality assurance of anions and metal ions in air borne particles in Korea. This program covered the chemical testing of anions(Cl-, NO3-, SO42-) and metals(Fe, Pb, Zn) in qeueous solution. The exercies was conducted by the Measurement & Analysis Committee of Korean Society for Atmospheric Environment(KOSAE). Pilot lab. was Division of Chemical Metrology and Materais Evaluation in Korea Research Institute of Standards and Science(KRISS). A total of 11 laboratories participated in the program. Two samples of 100mL in low density polyehylene bottles were supplied to participating laboratories. The proficiency testing results were interpreted by two graphical methods, Youden polt and x-Charts(control chart).

• International Journal of Internet, Broadcasting and Communication
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• v.8 no.4
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• pp.11-18
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• 2016

Due to open source policy, Android systems are exposed to a variety of security problems. In particular, app reuse attacks are detrimental threat to the Android system security. This is because attacker can create core malign components and quickly generate a bunch of malicious apps by reusing these components. Hence, it is very imperative to discern whether Android apps contain reused components. To meet this need, we propose an Android app reuse analysis technique based on the Sequential Hypothesis Testing. This technique quickly makes a decision with a few number of samples whether a set of Android apps is made through app reuse. We performed experimental study with 6 malicious app groups, 1 google and 1 third-party app group such that each group consists of 100 Android apps. Experimental results demonstrate that our proposed analysis technique efficiently judges Android app groups with reused components.