Journal of Cerebrovascular and Endovascular Neurosurgery

  • 제26권3호
  • /
  • Pages.324-330
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  • 2024
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  • 2234-8565(pISSN)
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  • 2287-3139(eISSN)
대한뇌혈관외과학회 (Korean Society of Cerebravascular Surgeons)
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Primary Angiitis of Central Nervous System related intracranial aneurysm with spontaneous occlusion after immunomodulatory treatment

  • Seby John (Department of Neurology and Neurointerventional Surgery, Neurological Institute (NI), Cleveland Clinic Abu Dhabi (CCAD)) ;
  • Muhammad Khan (Department of Biomedical Engineering, Khalifa University) ;
  • Praveen Kesav (Department of Neurology, Neurological Institute (NI), Cleveland Clinic Abu Dhabi (CCAD)) ;
  • Divya Raj (Department of Neurology, Neurological Institute (NI), Cleveland Clinic Abu Dhabi (CCAD)) ;
  • Syed Irteza Hussain (Department of Neurology and Neurointerventional Surgery, Neurological Institute (NI), Cleveland Clinic Abu Dhabi (CCAD))
  • 투고 : 2023.04.14
  • 심사 : 2024.01.02
  • 발행 : 2024.09.30
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초록

Primary Angiitis of the Central Nervous System (PACNS) is an uncommon disease with kaleidoscopic clinical manifestations. Ischemic strokes are commoner than their hemorrhagic counterpart. Intracranial pseudoaneurysms are rarely reported in PACNS cohorts. We hereby describe the case of a 39-year-old female, who presented for evaluation of acute onset of left middle cerebral artery (MCA) ischemic stroke, with cerebral angiogram showing multifocal stenosis and irregularities in intracranial blood vessels with an aneurysm arising from the lenticulostriate branch of the left MCA M1 segment. A diagnosis of probable PACNS was made and patient initiated on immunomodulatory treatment with corticosteroids. 12 weeks follow up neuroimaging studies revealed resolution of the previously described intracranial aneurysm, thereby postulating the possibility of a pseudoaneurysm related to the underlying angiitis.

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참고문헌

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