The Korean Journal of Medicine

  • 제99권2호
  • /
  • Pages.116-121
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  • 2024
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  • 1738-9364(pISSN)
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  • 2289-0769(eISSN)
대한내과학회 (The Korean Association of Internal Medicine)
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단백뇨와 경도 신기능장애가 있는 환자에서 진단된 신장에 국한된 결절성 다발성 동맥염 1예: 증례 보고

Polyarteritis Nodosa Confined to the Kidneys in a Patient with Proteinuria and Mild Renal Impairment

  • 서영경 (인제대학교 부산백병원 신장내과) ;
  • 김태희 (인제대학교 부산백병원 신장내과) ;
  • 김영훈 (인제대학교 부산백병원 신장내과) ;
  • 김윤미 (인제대학교 부산백병원 신장내과) ;
  • 허혁 (인제대학교 부산백병원 신장내과) ;
  • 김병우 (인제대학교 부산백병원 신장내과)
  • Young Kyeong Seo (Division of Nephrology, Department of Internal Medicine, Inje University Busan Paik Hospital) ;
  • Taehee Kim (Division of Nephrology, Department of Internal Medicine, Inje University Busan Paik Hospital) ;
  • Yeong Hoon Kim (Division of Nephrology, Department of Internal Medicine, Inje University Busan Paik Hospital) ;
  • Yunmi Kim (Division of Nephrology, Department of Internal Medicine, Inje University Busan Paik Hospital) ;
  • Hyuk Huh (Division of Nephrology, Department of Internal Medicine, Inje University Busan Paik Hospital) ;
  • Byeong Woo Kim (Division of Nephrology, Department of Internal Medicine, Inje University Busan Paik Hospital)
  • 투고 : 2023.10.21
  • 심사 : 2023.11.15
  • 발행 : 2024.04.01
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초록

Polyarteritis nodosa (PAN) is a systemic necrotizing vasculitis predominantly involving medium- or small-sized arteries, typically of the kidneys and other internal organs. Given the rarity of PAN and the variable clinical presentation, diagnosis is challenging and, to date, no definitive diagnostic marker has been identified. A patient diagnosed with immunoglobulin A nephropathy was observed to exhibit deterioration in renal function. To determine whether new structural abnormalities had developed, computed tomography scans of the kidneys, ureters, and bladder were obtained. Both kidneys exhibited multiple cortical defects, and a renal angiogram was performed to determine the cause. Angiography revealed partial obliteration of the left distal renal artery branches and multifocal extensive infarctions in both kidneys, and the patient was diagnosed with renal-limited PAN. Following steroid monotherapy, an improvement in renal function was observed. We believe that this case report may be helpful to physicians who assess and treat patients with suspected renal-limited PAN.

키워드

과제정보

The study was supported by research grants from Inje University.

참고문헌

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